Details for: COL7A1

Gene ID: 1294

Symbol: COL7A1

Ensembl ID: ENSG00000114270

Description: collagen type VII alpha 1 chain

Associated with

Other Information

Genular Protein ID: 367924138

Symbol: CO7A1_HUMAN

Name: Collagen alpha-1(VII) chain

UniProtKB Accession Codes:

Database IDs:

Citations:

PubMed ID: 8088784

Title: Structural organization of the human type VII collagen gene (COL7A1), composed of more exons than any previously characterized gene.

PubMed ID: 8088784

DOI: 10.1006/geno.1994.1239

PubMed ID: 8051117

Title: Cloning of human type VII collagen. Complete primary sequence of the alpha 1(VII) chain and identification of intragenic polymorphisms.

PubMed ID: 8051117

DOI: 10.1016/s0021-9258(17)31984-1

PubMed ID: 1307247

Title: The large non-collagenous domain (NC-1) of type VII collagen is amino-terminal and chimeric. Homology to cartilage matrix protein, the type III domains of fibronectin and the A domains of von Willebrand factor.

PubMed ID: 1307247

DOI: 10.1093/hmg/1.7.475

PubMed ID: 1567409

Title: Molecular cloning and characterization of type VII collagen cDNA.

PubMed ID: 1567409

DOI: 10.1016/s0006-291x(05)80283-9

PubMed ID: 1469284

Title: Noncollagenous (NC1) domain of collagen VII resembles multidomain adhesion proteins involved in tissue-specific organization of extracellular matrix.

PubMed ID: 1469284

DOI: 10.1111/1523-1747.ep12614080

PubMed ID: 1871109

Title: Human type VII collagen: cDNA cloning and chromosomal mapping of the gene.

PubMed ID: 1871109

DOI: 10.1073/pnas.88.16.6931

PubMed ID: 8499916

Title: The carboxyl-terminal half of type VII collagen, including the non-collagenous NC-2 domain and intron/exon organization of the corresponding region of the COL7A1 gene.

PubMed ID: 8499916

DOI: 10.1093/hmg/2.3.273

PubMed ID: 2537292

Title: Cleavage of type VII collagen by interstitial collagenase and type IV collagenase (gelatinase) derived from human skin.

PubMed ID: 2537292

DOI: 10.1016/s0021-9258(19)84924-4

PubMed ID: 19269366

Title: TANGO1 facilitates cargo loading at endoplasmic reticulum exit sites.

PubMed ID: 19269366

DOI: 10.1016/j.cell.2008.12.025

PubMed ID: 9375848

Title: Molecular basis of dystrophic epidermolysis bullosa: mutations in the type VII collagen gene (COL7A1).

PubMed ID: 9375848

DOI: 10.1002/(sici)1098-1004(1997)10:5<338::aid-humu2>3.0.co;2-b

PubMed ID: 21269460

Title: Initial characterization of the human central proteome.

PubMed ID: 21269460

DOI: 10.1186/1752-0509-5-17

PubMed ID: 2653224

Title: Epidermolysis bullosa simplex superficialis. A new variant of epidermolysis bullosa characterized by subcorneal skin cleavage mimicking peeling skin syndrome.

PubMed ID: 2653224

DOI: 10.1001/archderm.125.5.633

PubMed ID: 8513326

Title: A missense mutation in type VII collagen in two affected siblings with recessive dystrophic epidermolysis bullosa.

PubMed ID: 8513326

DOI: 10.1038/ng0593-62

PubMed ID: 8170945

Title: Dominant dystrophic epidermolysis bullosa: identification of a Gly-->Ser substitution in the triple-helical domain of type VII collagen.

PubMed ID: 8170945

DOI: 10.1073/pnas.91.9.3549

PubMed ID: 8541842

Title: Pretibial epidermolysis bullosa: genetic linkage to COL7A1 and identification of a glycine-to-cysteine substitution in the triple-helical domain of type VII collagen.

PubMed ID: 8541842

DOI: 10.1093/hmg/4.9.1579

PubMed ID: 7861014

Title: A glycine-to-arginine substitution in the triple-helical domain of type VII collagen in a family with dominant dystrophic epidermolysis bullosa.

PubMed ID: 7861014

DOI: 10.1111/1523-1747.ep12666033

PubMed ID: 8644729

Title: Glycine substitutions in the triple-helical region of type VII collagen result in a spectrum of dystrophic epidermolysis bullosa phenotypes and patterns of inheritance.

PubMed ID: 8644729

PubMed ID: 8592061

Title: Molecular basis of recessive dystrophic epidermolysis bullosa: genotype/phenotype correlation in a case of moderate clinical severity.

PubMed ID: 8592061

DOI: 10.1111/1523-1747.ep12329600

PubMed ID: 8618018

Title: Influence of the second COL7A1 mutation in determining the phenotypic severity of recessive dystrophic epidermolysis bullosa.

PubMed ID: 8618018

DOI: 10.1111/1523-1747.ep12345814

PubMed ID: 8757758

Title: Clinicopathological correlations of compound heterozygous COL7A1 mutations in recessive dystrophic epidermolysis bullosa.

PubMed ID: 8757758

DOI: 10.1111/1523-1747.ep12329570

PubMed ID: 9326325

Title: Characterization of 18 new mutations in COL7A1 in recessive dystrophic epidermolysis bullosa provides evidence for distinct molecular mechanisms underlying defective anchoring fibril formation.

PubMed ID: 9326325

DOI: 10.1086/515495

PubMed ID: 9444387

Title: Identification of a glycine substitution and a splice site mutation in the type VII collagen gene in a proband with mitis recessive dystrophic epidermolysis bullosa.

PubMed ID: 9444387

DOI: 10.1007/s004030050253

PubMed ID: 9215684

Title: Modulation of disease severity of dystrophic epidermolysis bullosa by a splice site mutation in combination with a missense mutation in the COL7A1 gene.

PubMed ID: 9215684

DOI: 10.1093/hmg/6.7.1125

PubMed ID: 9008239

Title: Glycine substitution mutations in the type VII collagen gene (COL7A1) in dystrophic epidermolysis bullosa: implications for genetic counseling.

PubMed ID: 9008239

DOI: 10.1111/1523-1747.ep12335324

PubMed ID: 9668111

Title: Some, but not all, glycine substitution mutations in COL7A1 result in intracellular accumulation of collagen VII, loss of anchoring fibrils, and skin blistering.

PubMed ID: 9668111

DOI: 10.1074/jbc.273.30.19228

PubMed ID: 9740253

Title: Novel COL7A1 mutations in dystrophic forms of epidermolysis bullosa.

PubMed ID: 9740253

DOI: 10.1046/j.1523-1747.1998.00326.x

PubMed ID: 9804332

Title: Compound heterozygosity for a recessive glycine substitution and a splice site mutation in the COL7A1 gene causes an unusually mild form of localized recessive dystrophic epidermolysis bullosa.

PubMed ID: 9804332

DOI: 10.1046/j.1523-1747.1998.00397.x

PubMed ID: 9856843

Title: Novel and de novo glycine substitution mutations in the type VII collagen gene (COL7A1) in dystrophic epidermolysis bullosa: implications for genetic counseling.

PubMed ID: 9856843

DOI: 10.1046/j.1523-1747.1998.00422.x

PubMed ID: 9856844

Title: Transient bullous dermolysis of the newborn associated with compound heterozygosity for recessive and dominant COL7A1 mutations.

PubMed ID: 9856844

DOI: 10.1046/j.1523-1747.1998.00394.x

PubMed ID: 10232406

Title: Diagnostic dilemma of 'sporadic' cases of dystrophic epidermolysis bullosa: a new dominant or mitis recessive mutation?

PubMed ID: 10232406

DOI: 10.1111/j.1600-0625.1999.tb00362.x

PubMed ID: 10232407

Title: Identification of a de novo glycine substitution in the type VII collagen gene in a proband with mild dystrophic epidermolysis bullosa.

PubMed ID: 10232407

DOI: 10.1111/j.1600-0625.1999.tb00363.x

PubMed ID: 10232408

Title: Squamous cell carcinoma in a family with dominant dystrophic epidermolysis bullosa: a molecular genetic study.

PubMed ID: 10232408

DOI: 10.1111/j.1600-0625.1999.tb00364.x

PubMed ID: 10084325

Title: Clustering of COL7A1 mutations in exon 73: implications for mutation analysis in dystrophic epidermolysis bullosa.

PubMed ID: 10084325

DOI: 10.1046/j.1523-1747.1999.00518.x

PubMed ID: 10233777

Title: Dominant dystrophic epidermolysis bullosa (Pasini) caused by a novel glycine substitution mutation in the type VII collagen gene (COL7A1).

PubMed ID: 10233777

DOI: 10.1046/j.1523-1747.1999.00568.x

PubMed ID: 10383749

Title: Allelic heterogeneity of dominant and recessive COL7A1 mutations underlying epidermolysis bullosa pruriginosa.

PubMed ID: 10383749

DOI: 10.1046/j.1523-1747.1999.00614.x

PubMed ID: 10469344

Title: Compound heterozygosity for silent and dominant glycine substitution mutations in COL7A1 leads to a marked transient intracytoplasmic retention of procollagen VII and a moderately severe dystrophic epidermolysis bullosa phenotype.

PubMed ID: 10469344

DOI: 10.1046/j.1523-1747.1999.00713.x

PubMed ID: 10504458

Title: Comparative mutation detection screening of the type VII collagen gene (COL7A1) using the protein truncation test, fluorescent chemical cleavage of mismatch, and conformation sensitive gel electrophoresis.

PubMed ID: 10504458

DOI: 10.1046/j.1523-1747.1999.00732.x

PubMed ID: 10836608

Title: A de novo glycine substitution mutation in the collagenous domain of COL7A1 in dominant dystrophic epidermolysis bullosa.

PubMed ID: 10836608

DOI: 10.1007/s004030050472

PubMed ID: 11142768

Title: Glycine substitution mutations by different amino acids in the same codon of COL7A1 lead to heterogeneous clinical phenotypes of dominant dystrophic epidermolysis bullosa.

PubMed ID: 11142768

DOI: 10.1007/s004030000162

PubMed ID: 10620140

Title: Combination of novel premature termination codon and glycine substitution mutations in COL7A1 leads to moderately severe recessive dystrophic epidermolysis bullosa.

PubMed ID: 10620140

DOI: 10.1046/j.1523-1747.2000.00848.x

PubMed ID: 11167698

Title: Generalized dystrophic epidermolysis bullosa: identification of a novel, homozygous glycine substitution, G2031S, in exon 73 of COL7A1 in monozygous triplets.

PubMed ID: 11167698

DOI: 10.1046/j.1365-2133.2001.03966.x

PubMed ID: 11843659

Title: Toenail dystrophy with COL7A1 glycine substitution mutations segregates as an autosomal dominant trait in 2 families with dystrophic epidermolysis bullosa.

PubMed ID: 11843659

DOI: 10.1001/archderm.138.2.269

PubMed ID: 11874498

Title: EB simplex superficialis resulting from a mutation in the type VII collagen gene.

PubMed ID: 11874498

DOI: 10.1046/j.0022-202x.2001.01702.x

PubMed ID: 12787275

Title: Dystrophic epidermolysis bullosa inversa with COL7A1 mutations and absence of GDA-J/F3 protein.

PubMed ID: 12787275

DOI: 10.1046/j.1525-1470.2003.20312.x

PubMed ID: 16959974

Title: The consensus coding sequences of human breast and colorectal cancers.

PubMed ID: 16959974

DOI: 10.1126/science.1133427

PubMed ID: 20108428

Title: Novel human pathological mutations. Gene symbol: COL7A1. Disease: Epidermolysis bullosa dystrophica.

PubMed ID: 20108428

PubMed ID: 20598510

Title: Analysis of the COL7A1 gene in Czech patients with dystrophic epidermolysis bullosa reveals novel and recurrent mutations.

PubMed ID: 20598510

DOI: 10.1016/j.jdermsci.2010.05.007

Sequence Information:

  • Length: 2944
  • Mass: 295220
  • Checksum: 96D8BF6D0FD387DB
  • Sequence:
  • MTLRLLVAAL CAGILAEAPR VRAQHRERVT CTRLYAADIV FLLDGSSSIG RSNFREVRSF 
    LEGLVLPFSG AASAQGVRFA TVQYSDDPRT EFGLDALGSG GDVIRAIREL SYKGGNTRTG 
    AAILHVADHV FLPQLARPGV PKVCILITDG KSQDLVDTAA QRLKGQGVKL FAVGIKNADP 
    EELKRVASQP TSDFFFFVND FSILRTLLPL VSRRVCTTAG GVPVTRPPDD STSAPRDLVL 
    SEPSSQSLRV QWTAASGPVT GYKVQYTPLT GLGQPLPSER QEVNVPAGET SVRLRGLRPL 
    TEYQVTVIAL YANSIGEAVS GTARTTALEG PELTIQNTTA HSLLVAWRSV PGATGYRVTW 
    RVLSGGPTQQ QELGPGQGSV LLRDLEPGTD YEVTVSTLFG RSVGPATSLM ARTDASVEQT 
    LRPVILGPTS ILLSWNLVPE ARGYRLEWRR ETGLEPPQKV VLPSDVTRYQ LDGLQPGTEY 
    RLTLYTLLEG HEVATPATVV PTGPELPVSP VTDLQATELP GQRVRVSWSP VPGATQYRII 
    VRSTQGVERT LVLPGSQTAF DLDDVQAGLS YTVRVSARVG PREGSASVLT VRREPETPLA 
    VPGLRVVVSD ATRVRVAWGP VPGASGFRIS WSTGSGPESS QTLPPDSTAT DITGLQPGTT 
    YQVAVSVLRG REEGPAAVIV ARTDPLGPVR TVHVTQASSS SVTITWTRVP GATGYRVSWH 
    SAHGPEKSQL VSGEATVAEL DGLEPDTEYT VHVRAHVAGV DGPPASVVVR TAPEPVGRVS 
    RLQILNASSD VLRITWVGVT GATAYRLAWG RSEGGPMRHQ ILPGNTDSAE IRGLEGGVSY 
    SVRVTALVGD REGTPVSIVV TTPPEAPPAL GTLHVVQRGE HSLRLRWEPV PRAQGFLLHW 
    QPEGGQEQSR VLGPELSSYH LDGLEPATQY RVRLSVLGPA GEGPSAEVTA RTESPRVPSI 
    ELRVVDTSID SVTLAWTPVS RASSYILSWR PLRGPGQEVP GSPQTLPGIS SSQRVTGLEP 
    GVSYIFSLTP VLDGVRGPEA SVTQTPVCPR GLADVVFLPH ATQDNAHRAE ATRRVLERLV 
    LALGPLGPQA VQVGLLSYSH RPSPLFPLNG SHDLGIILQR IRDMPYMDPS GNNLGTAVVT 
    AHRYMLAPDA PGRRQHVPGV MVLLVDEPLR GDIFSPIREA QASGLNVVML GMAGADPEQL 
    RRLAPGMDSV QTFFAVDDGP SLDQAVSGLA TALCQASFTT QPRPEPCPVY CPKGQKGEPG 
    EMGLRGQVGP PGDPGLPGRT GAPGPQGPPG SATAKGERGF PGADGRPGSP GRAGNPGTPG 
    APGLKGSPGL PGPRGDPGER GPRGPKGEPG APGQVIGGEG PGLPGRKGDP GPSGPPGPRG 
    PLGDPGPRGP PGLPGTAMKG DKGDRGERGP PGPGEGGIAP GEPGLPGLPG SPGPQGPVGP 
    PGKKGEKGDS EDGAPGLPGQ PGSPGEQGPR GPPGAIGPKG DRGFPGPLGE AGEKGERGPP 
    GPAGSRGLPG VAGRPGAKGP EGPPGPTGRQ GEKGEPGRPG DPAVVGPAVA GPKGEKGDVG 
    PAGPRGATGV QGERGPPGLV LPGDPGPKGD PGDRGPIGLT GRAGPPGDSG PPGEKGDPGR 
    PGPPGPVGPR GRDGEVGEKG DEGPPGDPGL PGKAGERGLR GAPGVRGPVG EKGDQGDPGE 
    DGRNGSPGSS GPKGDRGEPG PPGPPGRLVD TGPGAREKGE PGDRGQEGPR GPKGDPGLPG 
    APGERGIEGF RGPPGPQGDP GVRGPAGEKG DRGPPGLDGR SGLDGKPGAA GPSGPNGAAG 
    KAGDPGRDGL PGLRGEQGLP GPSGPPGLPG KPGEDGKPGL NGKNGEPGDP GEDGRKGEKG 
    DSGASGREGR DGPKGERGAP GILGPQGPPG LPGPVGPPGQ GFPGVPGGTG PKGDRGETGS 
    KGEQGLPGER GLRGEPGSVP NVDRLLETAG IKASALREIV ETWDESSGSF LPVPERRRGP 
    KGDSGEQGPP GKEGPIGFPG ERGLKGDRGD PGPQGPPGLA LGERGPPGPS GLAGEPGKPG 
    IPGLPGRAGG VGEAGRPGER GERGEKGERG EQGRDGPPGL PGTPGPPGPP GPKVSVDEPG 
    PGLSGEQGPP GLKGAKGEPG SNGDQGPKGD RGVPGIKGDR GEPGPRGQDG NPGLPGERGM 
    AGPEGKPGLQ GPRGPPGPVG GHGDPGPPGA PGLAGPAGPQ GPSGLKGEPG ETGPPGRGLT 
    GPTGAVGLPG PPGPSGLVGP QGSPGLPGQV GETGKPGAPG RDGASGKDGD RGSPGVPGSP 
    GLPGPVGPKG EPGPTGAPGQ AVVGLPGAKG EKGAPGGLAG DLVGEPGAKG DRGLPGPRGE 
    KGEAGRAGEP GDPGEDGQKG APGPKGFKGD PGVGVPGSPG PPGPPGVKGD LGLPGLPGAP 
    GVVGFPGQTG PRGEMGQPGP SGERGLAGPP GREGIPGPLG PPGPPGSVGP PGASGLKGDK 
    GDPGVGLPGP RGERGEPGIR GEDGRPGQEG PRGLTGPPGS RGERGEKGDV GSAGLKGDKG 
    DSAVILGPPG PRGAKGDMGE RGPRGLDGDK GPRGDNGDPG DKGSKGEPGD KGSAGLPGLR 
    GLLGPQGQPG AAGIPGDPGS PGKDGVPGIR GEKGDVGFMG PRGLKGERGV KGACGLDGEK 
    GDKGEAGPPG RPGLAGHKGE MGEPGVPGQS GAPGKEGLIG PKGDRGFDGQ PGPKGDQGEK 
    GERGTPGIGG FPGPSGNDGS AGPPGPPGSV GPRGPEGLQG QKGERGPPGE RVVGAPGVPG 
    APGERGEQGR PGPAGPRGEK GEAALTEDDI RGFVRQEMSQ HCACQGQFIA SGSRPLPSYA 
    ADTAGSQLHA VPVLRVSHAE EEERVPPEDD EYSEYSEYSV EEYQDPEAPW DSDDPCSLPL 
    DEGSCTAYTL RWYHRAVTGS TEACHPFVYG GCGGNANRFG TREACERRCP PRVVQSQGTG 
    TAQD

Genular Protein ID: 2617458229

Symbol: Q59F16_HUMAN

Name: N/A

UniProtKB Accession Codes:

Database IDs:

Sequence Information:

  • Length: 1027
  • Mass: 96806
  • Checksum: 59F1A5256985A6D3
  • Sequence:
  • GLPGRKGDPG PSGPPGPRGP LGDPGPRGPP GLPGTAMKGD KGDRGERGPP GPGEGGIAPG 
    EPGLPGLPGS PGPQGPVGPP GKKGEKGDSE DGAPGLPGQP GSPGEQGPRG PPGAIGPKGD 
    RGFPGPLGEA GEKGERGPPG PAGSRGLPGV AGRPGAKGPE GPPGPTGRQG EKGEPGRPGD 
    PAVVGPAVAG PKGEKGDVGP AGPRGATGVQ GERGPPGLVL PGDPGPKGDP GDRGPIGLTG 
    RAGPPGDSGP PGEKGDPGRP GPPGPVGPRG RDGEVGEKGD EGPPGDPGLP GKAGERGLRG 
    APGVRGPVGE KGDQGDPGED GRNGSPGSSG PKGDRGEPGP PGPPGRLVDT GPGAREKGEP 
    GDRGQEGPRG PKGDPGLPGA PGERGIEGFR GPPGPQGDPG VRGPAGEKGD RGPPGLDGRS 
    GLDGKPGAAG PSGPNGAAGK AGDPGRDGLP GLRGEQGLPG PSGPPGLPGK PGEDGKPGLN 
    GKNGEPGDPG EDGRKGEKGD SGASGREGRD GPKGERGAPG ILGPQGPPGL PGPVGPPGQG 
    FPGVPGGTGP KGDRGETGSK GEQGLPGERG LRGEPGSVPN VDRLLETAGI KASALREIVE 
    TWDESSGSFL PVPERRRGPK GDSGEQGPPG KEGPIGFPGE RGLKGDRGDP GPQGPPGLAL 
    GERGPPGPSG LAGEPGKPGI PGLPGRAGGV GEAGRPGERG ERGEKGERGE QGRDGPPGLP 
    GTPGPPGPPG PKVSVDEPGP GLSGEQGPPG LKGAKGEPGS NGDQGPKGDR GVPGIKGDRG 
    EPGPRGQDGN PGLPGERGMA GPEGKPGLQG PRGPPGPVGG HGDPGPPGAP GLAGPAGPQG 
    PSGLKGEPGE TGPPGRGLTG PTGAVGLPGP PGPSGLVGPQ GSPGLPGQVG ETGKPGAPGR 
    DGASGKDGDR GSPGVPGSPG LPGPVGPKGE PGPTGAPGQA VVGLPGAKGE KGAPGGLAGD 
    LVGEPGAKGD RGLPGPRGEK GEAGRAGEPG DPGEDVSPGP RQGRAWPEEC DGGHKGPLLG 
    RGTCLSP

Database document:

This is a preview of the gene's schema. Only a few entries are kept for 'singleCellExpressions,' 'mRNAExpressions,' and other large data arrays for visualization purposes. You can zoom in with the mouse wheel for a closer view, and the text will adjust automatically if necessary. For the full schema, download it here.