Details for: COL17A1

Gene ID: 1308

Symbol: COL17A1

Ensembl ID: ENSG00000065618

Description: collagen type XVII alpha 1 chain

Associated with

Other Information

Genular Protein ID: 3163795455

Symbol: COHA1_HUMAN

Name: Collagen alpha-1(XVII) chain

UniProtKB Accession Codes:

Database IDs:

Citations:

PubMed ID: 1324962

Title: Cloning and primary structural analysis of the bullous pemphigoid autoantigen, BP180.

PubMed ID: 1324962

DOI: 10.1111/1523-1747.ep12616580

PubMed ID: 9012408

Title: Cloning of the human type XVII collagen gene (COL17A1), and detection of novel mutations in generalized atrophic benign epidermolysis bullosa.

PubMed ID: 9012408

PubMed ID: 15164054

Title: The DNA sequence and comparative analysis of human chromosome 10.

PubMed ID: 15164054

DOI: 10.1038/nature02462

PubMed ID: 15489334

Title: The status, quality, and expansion of the NIH full-length cDNA project: the Mammalian Gene Collection (MGC).

PubMed ID: 15489334

DOI: 10.1101/gr.2596504

PubMed ID: 1748679

Title: Genomic organization of collagenous domains and chromosomal assignment of human 180-kDa bullous pemphigoid antigen-2, a novel collagen of stratified squamous epithelium.

PubMed ID: 1748679

DOI: 10.1016/s0021-9258(18)54393-3

PubMed ID: 14675210

Title: The 97-kDa (LABD97) and 120-kDa (LAD-1) fragments of bullous pemphigoid antigen 180/type XVII collagen have different N-termini.

PubMed ID: 14675210

DOI: 10.1046/j.1523-1747.2003.12607.x

PubMed ID: 9506436

Title: The 97 kDa linear IgA bullous disease antigen is identical to a portion of the extracellular domain of the 180 kDa bullous pemphigoid antigen, BPAg2.

PubMed ID: 9506436

DOI: 10.1046/j.1523-1747.1998.00129.x

PubMed ID: 8618013

Title: LAD-1, the linear IgA bullous dermatosis autoantigen, is a novel 120-kDa anchoring filament protein synthesized by epidermal cells.

PubMed ID: 8618013

DOI: 10.1111/1523-1747.ep12345782

PubMed ID: 8618014

Title: 97-kDa linear IgA bullous dermatosis (LAD) antigen localizes to the lamina lucida of the epidermal basement membrane.

PubMed ID: 8618014

DOI: 10.1111/1523-1747.ep12345793

PubMed ID: 9748270

Title: Two forms of collagen XVII in keratinocytes. A full-length transmembrane protein and a soluble ectodomain.

PubMed ID: 9748270

DOI: 10.1074/jbc.273.40.25937

PubMed ID: 10637308

Title: The N terminus of the transmembrane protein BP180 interacts with the N-terminal domain of BP230, thereby mediating keratin cytoskeleton anchorage to the cell surface at the site of the hemidesmosome.

PubMed ID: 10637308

DOI: 10.1091/mbc.11.1.277

PubMed ID: 12356719

Title: Transmembrane collagen XVII, an epithelial adhesion protein, is shed from the cell surface by ADAMs.

PubMed ID: 12356719

DOI: 10.1093/emboj/cdf532

PubMed ID: 12482924

Title: Analysis of the interactions between BP180, BP230, plectin and the integrin alpha6beta4 important for hemidesmosome assembly.

PubMed ID: 12482924

DOI: 10.1242/jcs.00241

PubMed ID: 17545155

Title: Extracellular phosphorylation of collagen XVII by ecto-casein kinase 2 inhibits ectodomain shedding.

PubMed ID: 17545155

DOI: 10.1074/jbc.m701937200

PubMed ID: 21269460

Title: Initial characterization of the human central proteome.

PubMed ID: 21269460

DOI: 10.1186/1752-0509-5-17

PubMed ID: 25676728

Title: Mutations in collagen, type XVII, alpha 1 (COL17A1) cause epithelial recurrent erosion dystrophy (ERED).

PubMed ID: 25676728

DOI: 10.1002/humu.22764

PubMed ID: 8669466

Title: Compound heterozygosity for a dominant glycine substitution and a recessive internal duplication mutation in the type XVII collagen gene results in junctional epidermolysis bullosa and abnormal dentition.

PubMed ID: 8669466

PubMed ID: 9199555

Title: Three novel homozygous point mutations and a new polymorphism in the COL17A1 gene: relation to biological and clinical phenotypes of junctional epidermolysis bullosa.

PubMed ID: 9199555

DOI: 10.1086/515463

PubMed ID: 10652291

Title: Collagen XVII is destabilized by a glycine substitution mutation in the cell adhesion domain Col15.

PubMed ID: 10652291

DOI: 10.1074/jbc.275.5.3093

PubMed ID: 10951237

Title: Hemizygosity for a glycine substitution in collagen XVII: unfolding and degradation of the ectodomain.

PubMed ID: 10951237

DOI: 10.1046/j.1523-1747.2000.00049.x

PubMed ID: 11912005

Title: A novel homozygous point mutation in the COL17A1 gene in a Chinese family with generalized atrophic benign epidermolysis bullosa.

PubMed ID: 11912005

DOI: 10.1016/s0923-1811(01)00163-3

Sequence Information:

  • Length: 1497
  • Mass: 150419
  • Checksum: E01027005F3AE843
  • Sequence:
  • MDVTKKNKRD GTEVTERIVT ETVTTRLTSL PPKGGTSNGY AKTASLGGGS RLEKQSLTHG 
    SSGYINSTGS TRGHASTSSY RRAHSPASTL PNSPGSTFER KTHVTRHAYE GSSSGNSSPE 
    YPRKEFASSS TRGRSQTRES EIRVRLQSAS PSTRWTELDD VKRLLKGSRS ASVSPTRNSS 
    NTLPIPKKGT VETKIVTASS QSVSGTYDAT ILDANLPSHV WSSTLPAGSS MGTYHNNMTT 
    QSSSLLNTNA YSAGSVFGVP NNMASCSPTL HPGLSTSSSV FGMQNNLAPS LTTLSHGTTT 
    TSTAYGVKKN MPQSPAAVNT GVSTSAACTT SVQSDDLLHK DCKFLILEKD NTPAKKEMEL 
    LIMTKDSGKV FTASPASIAA TSFSEDTLKK EKQAAYNADS GLKAEANGDL KTVSTKGKTT 
    TADIHSYGSS GGGGSGGGGG VGGAGGGPWG PAPAWCPCGS CCSWWKWLLG LLLTWLLLLG 
    LLFGLIALAE EVRKLKARVD ELERIRRSIL PYGDSMDRIE KDRLQGMAPA AGADLDKIGL 
    HSDSQEELWM FVRKKLMMEQ ENGNLRGSPG PKGDMGSPGP KGDRGFPGTP GIPGPLGHPG 
    PQGPKGQKGS VGDPGMEGPM GQRGREGPMG PRGEAGPPGS GEKGERGAAG EPGPHGPPGV 
    PGSVGPKGSS GSPGPQGPPG PVGLQGLRGE VGLPGVKGDK GPMGPPGPKG DQGEKGPRGL 
    TGEPGMRGLP GAVGEPGAKG AMGPAGPDGH QGPRGEQGLT GMPGIRGPPG PSGDPGKPGL 
    TGPQGPQGLP GTPGRPGIKG EPGAPGKIVT SEGSSMLTVP GPPGPPGAMG PPGPPGAPGP 
    AGPAGLPGHQ EVLNLQGPPG PPGPRGPPGP SIPGPPGPRG PPGEGLPGPP GPPGSFLSNS 
    ETFLSGPPGP PGPPGPKGDQ GPPGPRGHQG EQGLPGFSTS GSSSFGLNLQ GPPGPPGPQG 
    PKGDKGDPGV PGALGIPSGP SEGGSSSTMY VSGPPGPPGP PGPPGSISSS GQEIQQYISE 
    YMQSDSIRSY LSGVQGPPGP PGPPGPVTTI TGETFDYSEL ASHVVSYLRT SGYGVSLFSS 
    SISSEDILAV LQRDDVRQYL RQYLMGPRGP PGPPGASGDG SLLSLDYAEL SSRILSYMSS 
    SGISIGLPGP PGPPGLPGTS YEELLSLLRG SEFRGIVGPP GPPGPPGIPG NVWSSISVED 
    LSSYLHTAGL SFIPGPPGPP GPPGPRGPPG VSGALATYAA ENSDSFRSEL ISYLTSPDVR 
    SFIVGPPGPP GPQGPPGDSR LLSTDASHSR GSSSSSHSSS VRRGSSYSSS MSTGGGGAGS 
    LGAGGAFGEA AGDRGPYGTD IGPGGGYGAA AEGGMYAGNG GLLGADFAGD LDYNELAVRV 
    SESMQRQGLL QGMAYTVQGP PGQPGPQGPP GISKVFSAYS NVTADLMDFF QTYGAIQGPP 
    GQKGEMGTPG PKGDRGPAGP PGHPGPPGPR GHKGEKGDKG DQVYAGRRRR RSIAVKP

Database document:

This is a preview of the gene's schema. Only a few entries are kept for 'singleCellExpressions,' 'mRNAExpressions,' and other large data arrays for visualization purposes. You can zoom in with the mouse wheel for a closer view, and the text will adjust automatically if necessary. For the full schema, download it here.