Details for: AGA

Gene ID: 175

Symbol: AGA

Ensembl ID: ENSG00000038002

Description: aspartylglucosaminidase

Associated with

Other Information

Genular Protein ID: 2633922562

Symbol: ASPG_HUMAN

Name: N(4)-(beta-N-acetylglucosaminyl)-L-asparaginase

UniProtKB Accession Codes:

Database IDs:

Citations:

PubMed ID: 2401370

Title: Cloning and sequence analysis of a cDNA for human glycosylasparaginase. A single gene encodes the subunits of this lysosomal amidase.

PubMed ID: 2401370

DOI: 10.1016/0014-5793(90)81211-6

PubMed ID: 2265705

Title:

PubMed ID: 2265705

DOI: 10.1016/0014-5793(90)80551-s

PubMed ID: 1703489

Title: Aspartylglucosaminuria: cDNA encoding human aspartylglucosaminidase and the missense mutation causing the disease.

PubMed ID: 1703489

DOI: 10.1002/j.1460-2075.1991.tb07920.x

PubMed ID: 1840528

Title: Genomic structure of human lysosomal glycosylasparaginase.

PubMed ID: 1840528

DOI: 10.1016/0014-5793(91)81027-6

PubMed ID: 1904874

Title: Characterization of the mutation responsible for aspartylglucosaminuria in three Finnish patients. Amino acid substitution Cys163-->Ser abolishes the activity of lysosomal glycosylasparaginase and its conversion into subunits.

PubMed ID: 1904874

DOI: 10.1016/s0021-9258(18)99071-x

PubMed ID: 2011603

Title: Aspartylglycosaminuria in the Finnish population: identification of two point mutations in the heavy chain of glycoasparaginase.

PubMed ID: 2011603

DOI: 10.1073/pnas.88.7.2941

PubMed ID: 14702039

Title: Complete sequencing and characterization of 21,243 full-length human cDNAs.

PubMed ID: 14702039

DOI: 10.1038/ng1285

PubMed ID: 15815621

Title: Generation and annotation of the DNA sequences of human chromosomes 2 and 4.

PubMed ID: 15815621

DOI: 10.1038/nature03466

PubMed ID: 15489334

Title: The status, quality, and expansion of the NIH full-length cDNA project: the Mammalian Gene Collection (MGC).

PubMed ID: 15489334

DOI: 10.1101/gr.2596504

PubMed ID: 1281977

Title: Purification and structure of human liver aspartylglucosaminidase.

PubMed ID: 1281977

DOI: 10.1042/bj2881005

PubMed ID: 21269460

Title: Initial characterization of the human central proteome.

PubMed ID: 21269460

DOI: 10.1186/1752-0509-5-17

PubMed ID: 24275569

Title: An enzyme assisted RP-RPLC approach for in-depth analysis of human liver phosphoproteome.

PubMed ID: 24275569

DOI: 10.1016/j.jprot.2013.11.014

PubMed ID: 25944712

Title: N-terminome analysis of the human mitochondrial proteome.

PubMed ID: 25944712

DOI: 10.1002/pmic.201400617

PubMed ID: 8846222

Title: Three-dimensional structure of human lysosomal aspartylglucosaminidase.

PubMed ID: 8846222

DOI: 10.1038/nsb1295-1102

PubMed ID: 1301945

Title: Mutations causing aspartylglucosaminuria (AGU): a lysosomal accumulation disease.

PubMed ID: 1301945

DOI: 10.1002/humu.1380010503

PubMed ID: 8776587

Title: Ser72-->Pro active-site disease mutation in human lysosomal aspartylglucosaminidase: abnormal intracellular processing and evidence for extracellular activation.

PubMed ID: 8776587

DOI: 10.1093/hmg/5.6.737

PubMed ID: 9137882

Title: Two novel mutations in a Canadian family with aspartylglucosaminuria and early outcome post bone marrow transplantation.

PubMed ID: 9137882

DOI: 10.1111/j.1399-0004.1997.tb02448.x

PubMed ID: 11309371

Title: Molecular pathogenesis of a disease: structural consequences of aspartylglucosaminuria mutations.

PubMed ID: 11309371

DOI: 10.1093/hmg/10.9.983

Sequence Information:

  • Length: 346
  • Mass: 37208
  • Checksum: 766F1690B5B62FFA
  • Sequence:
  • MARKSNLPVL LVPFLLCQAL VRCSSPLPLV VNTWPFKNAT EAAWRALASG GSALDAVESG 
    CAMCEREQCD GSVGFGGSPD ELGETTLDAM IMDGTTMDVG AVGDLRRIKN AIGVARKVLE 
    HTTHTLLVGE SATTFAQSMG FINEDLSTTA SQALHSDWLA RNCQPNYWRN VIPDPSKYCG 
    PYKPPGILKQ DIPIHKETED DRGHDTIGMV VIHKTGHIAA GTSTNGIKFK IHGRVGDSPI 
    PGAGAYADDT AGAAAATGNG DILMRFLPSY QAVEYMRRGE DPTIACQKVI SRIQKHFPEF 
    FGAVICANVT GSYGAACNKL STFTQFSFMV YNSEKNQPTE EKVDCI

Database document:

This is a preview of the gene's schema. Only a few entries are kept for 'singleCellExpressions,' 'mRNAExpressions,' and other large data arrays for visualization purposes. You can zoom in with the mouse wheel for a closer view, and the text will adjust automatically if necessary. For the full schema, download it here.