Details for: ABCD1

Gene ID: 215

Symbol: ABCD1

Ensembl ID: ENSG00000101986

Description: ATP binding cassette subfamily D member 1

Associated with

Other Information

Genular Protein ID: 3541784732

Symbol: ABCD1_HUMAN

Name: N/A

UniProtKB Accession Codes:

Database IDs:

Citations:

PubMed ID: 8441467

Title: Putative X-linked adrenoleukodystrophy gene shares unexpected homology with ABC transporters.

PubMed ID: 8441467

DOI: 10.1038/361726a0

PubMed ID: 15772651

Title: The DNA sequence of the human X chromosome.

PubMed ID: 15772651

DOI: 10.1038/nature03440

PubMed ID: 15489334

Title: The status, quality, and expansion of the NIH full-length cDNA project: the Mammalian Gene Collection (MGC).

PubMed ID: 15489334

DOI: 10.1101/gr.2596504

PubMed ID: 10551832

Title: Homo- and heterodimerization of peroxisomal ATP-binding cassette half-transporters.

PubMed ID: 10551832

DOI: 10.1074/jbc.274.46.32738

PubMed ID: 11248239

Title: Characterization and functional analysis of the nucleotide binding fold in human peroxisomal ATP binding cassette transporters.

PubMed ID: 11248239

DOI: 10.1016/s0014-5793(01)02235-9

PubMed ID: 10777694

Title: Human adrenoleukodystrophy protein and related peroxisomal ABC transporters interact with the peroxisomal assembly protein PEX19p.

PubMed ID: 10777694

DOI: 10.1006/bbrc.2000.2572

PubMed ID: 10704444

Title: PEX19 binds multiple peroxisomal membrane proteins, is predominantly cytoplasmic, and is required for peroxisome membrane synthesis.

PubMed ID: 10704444

DOI: 10.1083/jcb.148.5.931

PubMed ID: 16213491

Title: X-linked adrenoleukodystrophy mice demonstrate abnormalities in cholesterol metabolism.

PubMed ID: 16213491

DOI: 10.1016/j.febslet.2005.09.014

PubMed ID: 15781447

Title: Function of the PEX19-binding site of human adrenoleukodystrophy protein as targeting motif in man and yeast. PMP targeting is evolutionarily conserved.

PubMed ID: 15781447

DOI: 10.1074/jbc.m501750200

PubMed ID: 15682271

Title: Probing substrate-induced conformational alterations in adrenoleukodystrophy protein by proteolysis.

PubMed ID: 15682271

DOI: 10.1007/s10038-004-0226-4

PubMed ID: 16946495

Title: ATP-binding and -hydrolysis activities of ALDP (ABCD1) and ALDRP (ABCD2), human peroxisomal ABC proteins, overexpressed in Sf21 cells.

PubMed ID: 16946495

DOI: 10.1248/bpb.29.1836

PubMed ID: 17609205

Title: Live cell FRET microscopy: homo- and heterodimerization of two human peroxisomal ABC transporters, the adrenoleukodystrophy protein (ALDP, ABCD1) and PMP70 (ABCD3).

PubMed ID: 17609205

DOI: 10.1074/jbc.m702122200

PubMed ID: 18757502

Title: The human peroxisomal ABC half transporter ALDP functions as a homodimer and accepts acyl-CoA esters.

PubMed ID: 18757502

DOI: 10.1096/fj.08-110866

PubMed ID: 21145416

Title: Differential substrate specificities of human ABCD1 and ABCD2 in peroxisomal fatty acid beta-oxidation.

PubMed ID: 21145416

DOI: 10.1016/j.bbalip.2010.11.010

PubMed ID: 23671276

Title: Impaired very long-chain acyl-CoA beta-oxidation in human X-linked adrenoleukodystrophy fibroblasts is a direct consequence of ABCD1 transporter dysfunction.

PubMed ID: 23671276

DOI: 10.1074/jbc.m112.445445

PubMed ID: 18691976

Title: Kinase-selective enrichment enables quantitative phosphoproteomics of the kinome across the cell cycle.

PubMed ID: 18691976

DOI: 10.1016/j.molcel.2008.07.007

PubMed ID: 18669648

Title: A quantitative atlas of mitotic phosphorylation.

PubMed ID: 18669648

DOI: 10.1073/pnas.0805139105

PubMed ID: 21269460

Title: Initial characterization of the human central proteome.

PubMed ID: 21269460

DOI: 10.1186/1752-0509-5-17

PubMed ID: 24275569

Title: An enzyme assisted RP-RPLC approach for in-depth analysis of human liver phosphoproteome.

PubMed ID: 24275569

DOI: 10.1016/j.jprot.2013.11.014

PubMed ID: 25944712

Title: N-terminome analysis of the human mitochondrial proteome.

PubMed ID: 25944712

DOI: 10.1002/pmic.201400617

PubMed ID: 29397936

Title: Characterization of human ATP-binding cassette protein subfamily D reconstituted into proteoliposomes.

PubMed ID: 29397936

DOI: 10.1016/j.bbrc.2018.01.153

PubMed ID: 33500543

Title: Acyl-CoA thioesterase activity of peroxisomal ABC protein ABCD1 is required for the transport of very long-chain acyl-CoA into peroxisomes.

PubMed ID: 33500543

DOI: 10.1038/s41598-021-81949-3

PubMed ID: 7904210

Title: Abnormal messenger RNA expression and a missense mutation in patients with X-linked adrenoleukodystrophy.

PubMed ID: 7904210

DOI: 10.1093/hmg/2.11.1949

PubMed ID: 7849723

Title: Missense mutations are frequent in the gene for X-chromosomal adrenoleukodystrophy (ALD).

PubMed ID: 7849723

DOI: 10.1093/hmg/3.10.1903

PubMed ID: 8040304

Title: Identification of mutations in the putative ATP-binding domain of the adrenoleukodystrophy gene.

PubMed ID: 8040304

DOI: 10.1172/jci117363

PubMed ID: 7825602

Title: Spectrum of mutations in the gene encoding the adrenoleukodystrophy protein.

PubMed ID: 7825602

PubMed ID: 7717396

Title: Mutations in the gene for X-linked adrenoleukodystrophy in patients with different clinical phenotypes.

PubMed ID: 7717396

PubMed ID: 7668254

Title: Altered expression of ALDP in X-linked adrenoleukodystrophy.

PubMed ID: 7668254

PubMed ID: 7860075

Title: De novo missense mutation Y174S in exon 1 of the adrenoleukodystrophy (ALD) gene.

PubMed ID: 7860075

DOI: 10.1007/bf00209412

PubMed ID: 7581394

Title: Mutational analysis of patients with X-linked adrenoleukodystrophy.

PubMed ID: 7581394

DOI: 10.1002/humu.1380060203

PubMed ID: 7561948

Title: Molecular analysis of X-linked adrenoleukodystrophy patients.

PubMed ID: 7561948

DOI: 10.1016/0022-510x(95)00047-6

PubMed ID: 8651290

Title: Mutational and protein analysis of patients and heterozygous women with X-linked adrenoleukodystrophy.

PubMed ID: 8651290

PubMed ID: 8566952

Title: Identification of mutations in the ALD-gene of 20 families with adrenoleukodystrophy/adrenomyeloneuropathy.

PubMed ID: 8566952

DOI: 10.1007/bf02265264

PubMed ID: 9452087

Title: First missense mutation (W679R) in exon 10 of the adrenoleukodystrophy gene in siblings with adrenomyeloneuropathy.

PubMed ID: 9452087

DOI: 10.1002/humu.1380110166

PubMed ID: 9584268

Title: A novel mutation found in an adrenoleukodystrophy patient who underwent bone marrow transplantation.

PubMed ID: 9584268

DOI: 10.1023/a:1005399810735

PubMed ID: 9553942

Title: Clinical and genetic aspects of X-linked adrenoleukodystrophy.

PubMed ID: 9553942

DOI: 10.1055/s-2007-973526

PubMed ID: 10190819

Title: Mutational analysis and genotype-phenotype correlation of 29 unrelated Japanese patients with X-linked adrenoleukodystrophy.

PubMed ID: 10190819

DOI: 10.1001/archneur.56.3.295

PubMed ID: 10480364

Title: X-linked adrenomyeloneuropathy associated with 14 novel ALD-gene mutations: no correlation between type of mutation and age of onset.

PubMed ID: 10480364

DOI: 10.1007/s004399900090

PubMed ID: 10369742

Title: Two novel missense mutations causing adrenoleukodystrophy in Italian patients.

PubMed ID: 10369742

DOI: 10.1006/mcpr.1999.0232

PubMed ID: 10227685

Title: X-linked adrenoleukodystrophy: genes, mutations, and phenotypes.

PubMed ID: 10227685

DOI: 10.1023/a:1022535930009

PubMed ID: 10737980

Title: Determination of 30 X-linked adrenoleukodystrophy mutations, including 15 not previously described.

PubMed ID: 10737980

DOI: 10.1002/(sici)1098-1004(200004)15:4<348::aid-humu7>3.0.co;2-n

PubMed ID: 10980539

Title: Detection of mutations in the ALD gene (ABCD1) in seven Italian families: description of four novel mutations.

PubMed ID: 10980539

DOI: 10.1002/1098-1004(200009)16:3<271::aid-humu15>3.0.co;2-d

PubMed ID: 11810273

Title: Characterisation of two mutations in the ABCD1 gene leading to low levels of normal ALDP.

PubMed ID: 11810273

DOI: 10.1007/s00439-001-0632-z

PubMed ID: 11438993

Title: Eight novel ABCD1 gene mutations and three polymorphisms in patients with X-linked adrenoleukodystrophy: the first polymorphism causing an amino acid exchange.

PubMed ID: 11438993

DOI: 10.1002/humu.1149

PubMed ID: 11748843

Title: ABCD1 mutations and the X-linked adrenoleukodystrophy mutation database: role in diagnosis and clinical correlations.

PubMed ID: 11748843

DOI: 10.1002/humu.1227

PubMed ID: 11992258

Title: Contiguous deletion of the X-linked adrenoleukodystrophy gene (ABCD1) and DXS1357E: a novel neonatal phenotype similar to peroxisomal biogenesis disorders.

PubMed ID: 11992258

DOI: 10.1086/340849

PubMed ID: 15643618

Title: Identification of seven novel mutations in ABCD1 by a DHPLC-based assay in Italian patients with X-linked adrenoleukodystrophy.

PubMed ID: 15643618

DOI: 10.1002/humu.9303

PubMed ID: 34337821

Title:

PubMed ID: 34337821

DOI: 10.1002/humu.24093

PubMed ID: 21889498

Title: Molecular analysis of ABCD1 gene in Indian patients with X-linked adrenoleukodystrophy.

PubMed ID: 21889498

DOI: 10.1016/j.cca.2011.08.026

PubMed ID: 21700483

Title: X-linked adrenoleukodystrophy: ABCD1 de novo mutations and mosaicism.

PubMed ID: 21700483

DOI: 10.1016/j.ymgme.2011.05.016

PubMed ID: 20661612

Title: Identification of novel SNPs of ABCD1, ABCD2, ABCD3, and ABCD4 genes in patients with X-linked adrenoleukodystrophy (ALD) based on comprehensive resequencing and association studies with ALD phenotypes.

PubMed ID: 20661612

DOI: 10.1007/s10048-010-0253-6

PubMed ID: 21966424

Title: Genomic profiling identifies novel mutations and SNPs in ABCD1 gene: a molecular, biochemical and clinical analysis of X-ALD cases in India.

PubMed ID: 21966424

DOI: 10.1371/journal.pone.0025094

PubMed ID: 23651979

Title: Molecular characterization of X-linked adrenoleukodystrophy in a Tunisian family: identification of a novel missense mutation in the ABCD1 gene.

PubMed ID: 23651979

DOI: 10.1159/000346680

PubMed ID: 26686776

Title: Phenotypic variability in a Tunisian family with X-linked adrenoleukodystrophy caused by the p.Gln316Pro novel mutation.

PubMed ID: 26686776

DOI: 10.1016/j.cca.2015.12.014

PubMed ID: 28456143

Title: A first case of adrenomyeloneuropathy with mutation Y174S of the adrenoleukodystrophy gene.

PubMed ID: 28456143

Sequence Information:

  • Length: 745
  • Mass: 82937
  • Checksum: 82F90905F71FFDC8
  • Sequence:
  • MPVLSRPRPW RGNTLKRTAV LLALAAYGAH KVYPLVRQCL APARGLQAPA GEPTQEASGV 
    AAAKAGMNRV FLQRLLWLLR LLFPRVLCRE TGLLALHSAA LVSRTFLSVY VARLDGRLAR 
    CIVRKDPRAF GWQLLQWLLI ALPATFVNSA IRYLEGQLAL SFRSRLVAHA YRLYFSQQTY 
    YRVSNMDGRL RNPDQSLTED VVAFAASVAH LYSNLTKPLL DVAVTSYTLL RAARSRGAGT 
    AWPSAIAGLV VFLTANVLRA FSPKFGELVA EEARRKGELR YMHSRVVANS EEIAFYGGHE 
    VELALLQRSY QDLASQINLI LLERLWYVML EQFLMKYVWS ASGLLMVAVP IITATGYSES 
    DAEAVKKAAL EKKEEELVSE RTEAFTIARN LLTAAADAIE RIMSSYKEVT ELAGYTARVH 
    EMFQVFEDVQ RCHFKRPREL EDAQAGSGTI GRSGVRVEGP LKIRGQVVDV EQGIICENIP 
    IVTPSGEVVV ASLNIRVEEG MHLLITGPNG CGKSSLFRIL GGLWPTYGGV LYKPPPQRMF 
    YIPQRPYMSV GSLRDQVIYP DSVEDMQRKG YSEQDLEAIL DVVHLHHILQ REGGWEAMCD 
    WKDVLSGGEK QRIGMARMFY HRPKYALLDE CTSAVSIDVE GKIFQAAKDA GIALLSITHR 
    PSLWKYHTHL LQFDGEGGWK FEKLDSAARL SLTEEKQRLE QQLAGIPKMQ RRLQELCQIL 
    GEAVAPAHVP APSPQGPGGL QGAST

Database document:

This is a preview of the gene's schema. Only a few entries are kept for 'singleCellExpressions,' 'mRNAExpressions,' and other large data arrays for visualization purposes. You can zoom in with the mouse wheel for a closer view, and the text will adjust automatically if necessary. For the full schema, download it here.