Details for: AQP2

Gene ID: 359

Symbol: AQP2

Ensembl ID: ENSG00000167580

Description: aquaporin 2

Associated with

Other Information

Genular Protein ID: 3087139650

Symbol: AQP2_HUMAN

Name: Aquaporin-2

UniProtKB Accession Codes:

Database IDs:

Citations:

PubMed ID: 8140421

Title: Requirement of human renal water channel aquaporin-2 for vasopressin-dependent concentration of urine.

PubMed ID: 8140421

DOI: 10.1126/science.8140421

PubMed ID: 7522228

Title: Isolation of human aquaporin-CD gene.

PubMed ID: 7522228

DOI: 10.1016/s0021-9258(17)31537-5

PubMed ID: 7524315

Title: Patients with autosomal nephrogenic diabetes insipidus homozygous for mutations in the aquaporin 2 water-channel gene.

PubMed ID: 7524315

PubMed ID: 7510718

Title: Cloning, characterization, and chromosomal mapping of human aquaporin of collecting duct.

PubMed ID: 7510718

DOI: 10.1172/jci117079

PubMed ID: 11929850

Title: Heteroligomerization of an aquaporin-2 mutant with wild-type aquaporin-2 and their misrouting to late endosomes/lysosomes explains dominant nephrogenic diabetes insipidus.

PubMed ID: 11929850

DOI: 10.1093/hmg/11.7.779

PubMed ID: 15489334

Title: The status, quality, and expansion of the NIH full-length cDNA project: the Mammalian Gene Collection (MGC).

PubMed ID: 15489334

DOI: 10.1101/gr.2596504

PubMed ID: 12194985

Title: The role of putative phosphorylation sites in the targeting and shuttling of the aquaporin-2 water channel.

PubMed ID: 12194985

DOI: 10.1074/jbc.m207525200

PubMed ID: 32176498

Title: Micropeptide MIAC Inhibits HNSCC Progression by Interacting with Aquaporin 2.

PubMed ID: 32176498

DOI: 10.1021/jacs.0c00706

PubMed ID: 36117171

Title: Micropeptide MIAC inhibits the tumor progression by interacting with AQP2 and inhibiting EREG/EGFR signaling in renal cell carcinoma.

PubMed ID: 36117171

DOI: 10.1186/s12943-022-01654-1

PubMed ID: 24733887

Title: X-ray structure of human aquaporin 2 and its implications for nephrogenic diabetes insipidus and trafficking.

PubMed ID: 24733887

DOI: 10.1073/pnas.1321406111

PubMed ID: 8882880

Title: Two novel mutations in the aquaporin-2 and the vasopressin V2 receptor genes in patients with congenital nephrogenic diabetes insipidus.

PubMed ID: 8882880

DOI: 10.1007/s004390050264

PubMed ID: 9302264

Title: Identification and characterization of aquaporin-2 water channel mutations causing nephrogenic diabetes insipidus with partial vasopressin response.

PubMed ID: 9302264

DOI: 10.1093/hmg/6.11.1865

PubMed ID: 9048343

Title: New mutations in the AQP2 gene in nephrogenic diabetes insipidus resulting in functional but misrouted water channels.

PubMed ID: 9048343

DOI: 10.1681/asn.v82242

PubMed ID: 9402087

Title: Mutations in the vasopressin V2 receptor and aquaporin-2 genes in 12 families with congenital nephrogenic diabetes insipidus.

PubMed ID: 9402087

DOI: 10.1681/asn.v8121855

PubMed ID: 9550615

Title: Aquaporin-2, a vasopressin-sensitive water channel, and nephrogenic diabetes insipidus.

PubMed ID: 9550615

DOI: 10.2169/internalmedicine.37.215

PubMed ID: 9649557

Title: An aquaporin-2 water channel mutant which causes autosomal dominant nephrogenic diabetes insipidus is retained in the Golgi complex.

PubMed ID: 9649557

DOI: 10.1172/jci2605

PubMed ID: 9745427

Title: Novel mutations in aquaporin-2 gene in female siblings with nephrogenic diabetes insipidus: evidence of disrupted water channel function.

PubMed ID: 9745427

DOI: 10.1210/jcem.83.9.5074

PubMed ID: 12191971

Title: Cell-biologic and functional analyses of five new Aquaporin-2 missense mutations that cause recessive nephrogenic diabetes insipidus.

PubMed ID: 12191971

DOI: 10.1097/01.asn.0000027355.41663.14

PubMed ID: 12050236

Title: Two novel aquaporin-2 mutations responsible for congenital nephrogenic diabetes insipidus in Chinese families.

PubMed ID: 12050236

DOI: 10.1210/jcem.87.6.8617

PubMed ID: 15509592

Title: A novel mechanism in recessive nephrogenic diabetes insipidus: wild-type aquaporin-2 rescues the apical membrane expression of intracellularly retained AQP2-P262L.

PubMed ID: 15509592

DOI: 10.1093/hmg/ddh339

PubMed ID: 16120822

Title: Lack of arginine vasopressin-induced phosphorylation of aquaporin-2 mutant AQP2-R254L explains dominant nephrogenic diabetes insipidus.

PubMed ID: 16120822

DOI: 10.1681/asn.2005010104

PubMed ID: 16361827

Title: Two novel mutations in the aquaporin 2 gene in a girl with congenital nephrogenic diabetes insipidus.

PubMed ID: 16361827

DOI: 10.3346/jkms.2005.20.6.1076

PubMed ID: 16845277

Title: Novel mutations underlying nephrogenic diabetes insipidus in Arab families.

PubMed ID: 16845277

DOI: 10.1097/01.gim.0000223554.46981.7a

PubMed ID: 19585583

Title: p.R254Q mutation in the aquaporin-2 water channel causing dominant nephrogenic diabetes insipidus is due to a lack of arginine vasopressin-induced phosphorylation.

PubMed ID: 19585583

DOI: 10.1002/humu.21082

PubMed ID: 19701945

Title: Repulsion between Lys258 and upstream arginines explains the missorting of the AQP2 mutant p.Glu258Lys in nephrogenic diabetes insipidus.

PubMed ID: 19701945

DOI: 10.1002/humu.21068

PubMed ID: 24944815

Title: Congenital nephrogenic diabetes insipidus with a novel mutation in the aquaporin 2 gene.

PubMed ID: 24944815

DOI: 10.3892/br.2014.283

Sequence Information:

  • Length: 271
  • Mass: 28837
  • Checksum: C2DDE2AF4DDD192A
  • Sequence:
  • MWELRSIAFS RAVFAEFLAT LLFVFFGLGS ALNWPQALPS VLQIAMAFGL GIGTLVQALG 
    HISGAHINPA VTVACLVGCH VSVLRAAFYV AAQLLGAVAG AALLHEITPA DIRGDLAVNA 
    LSNSTTAGQA VTVELFLTLQ LVLCIFASTD ERRGENPGTP ALSIGFSVAL GHLLGIHYTG 
    CSMNPARSLA PAVVTGKFDD HWVFWIGPLV GAILGSLLYN YVLFPPAKSL SERLAVLKGL 
    EPDTDWEERE VRRRQSVELH SPQSLPRGTK A

Database document:

This is a preview of the gene's schema. Only a few entries are kept for 'singleCellExpressions,' 'mRNAExpressions,' and other large data arrays for visualization purposes. You can zoom in with the mouse wheel for a closer view, and the text will adjust automatically if necessary. For the full schema, download it here.