Details for: ACADVL

Gene ID: 37

Gene Type:  Protein-coding  - A gene that serves as a template for producing a messenger RNA (mRNA) molecule, which is then translated into a functional protein.

Symbol: ACADVL

Ensembl ID: ENSG00000072778

Description: acyl-CoA dehydrogenase very long chain

Cell Significance Landscape

Associated with

Significant Cells

Cell Significance Index (CSI) scores for the chosen context(s)

  • M cell of gut CL0000682
    CSI 65.58
    rCSI 69.68%
    PRS 21.71
  • colon epithelial cell CL0011108
    CSI 55.36
    rCSI 57.99%
    PRS 11.39
  • stem cell CL0000034
    CSI 54.81
    rCSI 52.85%
    PRS 8.35
  • multi-ciliated epithelial cell CL0005012
    CSI 53.08
    rCSI 52.98%
    PRS 10.46
  • transit amplifying cell of colon CL0009011
    CSI 49.88
    rCSI 58.58%
    PRS 14.42
  • placental villous trophoblast CL2000060
    CSI 42.43
    rCSI 65.56%
    PRS 11.46
  • intestinal epithelial cell CL0002563
    CSI 40.46
    rCSI 42.28%
    PRS 12.87
  • enterocyte CL0000584
    CSI 36.62
    rCSI 59.05%
    PRS 19.55
  • pancreatic acinar cell CL0002064
    CSI 32.24
    rCSI 42.84%
    PRS 13.37
  • colonocyte CL1000347
    CSI 31.28
    rCSI 44.84%
    PRS 16.78
  • pancreatic ductal cell CL0002079
    CSI 30.85
    rCSI 60%
    PRS 12.49
  • intrahepatic cholangiocyte CL0002538
    CSI 29.15
    rCSI 69.96%
    PRS 22.32
  • pancreatic A cell CL0000171
    CSI 28.55
    rCSI 29.91%
    PRS 13.05
  • extravillous trophoblast CL0008036
    CSI 23.56
    rCSI 29.14%
    PRS 10.73
  • mucous neck cell CL0000651
    CSI 22.63
    rCSI 32.62%
    PRS 19.72
  • syncytiotrophoblast cell CL0000525
    CSI 22.48
    rCSI 64.77%
    PRS 23.78
  • colon goblet cell CL0009039
    CSI 21.44
    rCSI 50.96%
    PRS 18.44
  • deuterosomal cell CL4033044
    CSI 20.81
    rCSI 70.35%
    PRS 20.56
  • foveolar cell of stomach CL0002179
    CSI 20.6
    rCSI 43.86%
    PRS 19.75
  • epithelial cell of lung CL0000082
    CSI 20.04
    rCSI 16.61%
    PRS 11.54
  • intestine goblet cell CL0019031
    CSI 18.58
    rCSI 16.49%
    PRS 12.25
  • centrilobular region hepatocyte CL0019029
    CSI 17.07
    rCSI 44.53%
    PRS 19.67
  • midzonal region hepatocyte CL0019028
    CSI 16.68
    rCSI 39.15%
    PRS 18.68
  • microcirculation associated smooth muscle cell CL0008035
    CSI 16.07
    rCSI 46.54%
    PRS 13.84
  • respiratory suprabasal cell CL4033048
    CSI 15.5
    rCSI 19.87%
    PRS 14.13
  • ionocyte CL0005006
    CSI 14.9
    rCSI 15.97%
    PRS 11.25
  • tracheal goblet cell CL1000329
    CSI 13.66
    rCSI 29.82%
    PRS 24.69
  • plasmablast CL0000980
    CSI 13.47
    rCSI 10.59%
    PRS 14.52
  • paneth cell of epithelium of small intestine CL1000343
    CSI 12.84
    rCSI 35.98%
    PRS 18.91
  • BEST4+ enteroycte CL4030026
    CSI 12.35
    rCSI 15.36%
    PRS 12.92
  • intestinal crypt stem cell of small intestine CL0009017
    CSI 12.27
    rCSI 33.07%
    PRS 15.76
  • transit amplifying cell CL0009010
    CSI 12.23
    rCSI 18.71%
    PRS 19.89
  • luminal epithelial cell of mammary gland CL0002326
    CSI 12.05
    rCSI 21.89%
    PRS 18.71
  • pancreatic PP cell CL0002275
    CSI 11.53
    rCSI 45.91%
    PRS 21.48
  • goblet cell CL0000160
    CSI 11.24
    rCSI 10.62%
    PRS 12.78
  • keratinocyte CL0000312
    CSI 11.19
    rCSI 9.38%
    PRS 14.66
  • kidney epithelial cell CL0002518
    CSI 10.86
    rCSI 20.74%
    PRS 28.9
  • pancreatic D cell CL0000173
    CSI 10.44
    rCSI 10.27%
    PRS 13.27
  • bronchial goblet cell CL1000312
    CSI 10.26
    rCSI 41%
    PRS 26.84
  • tracheobronchial serous cell CL0019001
    CSI 10.09
    rCSI 43.58%
    PRS 23.42
  • enterocyte of epithelium of large intestine CL0002071
    CSI 9.63
    rCSI 50.6%
    PRS 21.86
  • pancreatic epsilon cell CL0005019
    CSI 9.43
    rCSI 43.98%
    PRS 29.13
  • transit amplifying cell of small intestine CL0009012
    CSI 9.25
    rCSI 40.63%
    PRS 22.8
  • enteroendocrine cell of colon CL0009042
    CSI 9.17
    rCSI 43%
    PRS 32.81
  • pancreatic stellate cell CL0002410
    CSI 9.04
    rCSI 52.61%
    PRS 18.39
  • epithelial cell of lower respiratory tract CL0002632
    CSI 8.88
    rCSI 6.89%
    PRS 11.65
  • fallopian tube secretory epithelial cell CL4030006
    CSI 8.7
    rCSI 8.37%
    PRS 12.66
  • type EC enteroendocrine cell CL0000577
    CSI 8.62
    rCSI 30.58%
    PRS 20.07
  • elicited macrophage CL0000861
    CSI 8.58
    rCSI 7.88%
    PRS 13.96
  • intestinal crypt stem cell of colon CL0009043
    CSI 8.19
    rCSI 61.5%
    PRS 22.54
  • club cell CL0000158
    CSI 7.27
    rCSI 10.65%
    PRS 14.3
  • renal principal cell CL0005009
    CSI 6.76
    rCSI 17.55%
    PRS 16.41
  • blood vessel smooth muscle cell CL0019018
    CSI 6.66
    rCSI 54.2%
    PRS 12.65
  • Hofbauer cell CL3000001
    CSI 6.56
    rCSI 12.39%
    PRS 15.18
  • P/D1 enteroendocrine cell CL0002268
    CSI 6.48
    rCSI 35.27%
    PRS 30.21
  • granulocyte monocyte progenitor cell CL0000557
    CSI 6.33
    rCSI 5.48%
    PRS 13.62
  • plasma cell CL0000786
    CSI 6.24
    rCSI 8.18%
    PRS 51.89
  • double negative thymocyte CL0002489
    CSI 6.16
    rCSI 4.28%
    PRS 14.32
  • respiratory goblet cell CL0002370
    CSI 5.75
    rCSI 62.55%
    PRS 23.64
  • hepatocyte CL0000182
    CSI 5.71
    rCSI 10.22%
    PRS 11.39
  • podocyte CL0000653
    CSI 5.62
    rCSI 24.99%
    PRS 12.05
  • activated type II NK T cell CL0000931
    CSI 5.57
    rCSI 6.27%
    PRS 19.58
  • endothelial cell of periportal hepatic sinusoid CL0019021
    CSI 5.33
    rCSI 24.43%
    PRS 34.21
  • sst GABAergic cortical interneuron CL4023017
    CSI 5.23
    rCSI 6.74%
    PRS 7.48
  • basal cell of epithelium of trachea CL1000348
    CSI 5.22
    rCSI 36.86%
    PRS 37.58
  • epithelial cell CL0000066
    CSI 5.14
    rCSI 7.9%
    PRS 17.47
  • cholangiocyte CL1000488
    CSI 5.01
    rCSI 30.04%
    PRS 19.23
  • myofibroblast cell CL0000186
    CSI 4.97
    rCSI 6.89%
    PRS 17.63
  • kidney distal convoluted tubule epithelial cell CL1000849
    CSI 4.96
    rCSI 52.51%
    PRS 17.23
  • pvalb GABAergic cortical interneuron CL4023018
    CSI 4.95
    rCSI 6.15%
    PRS 6.63
  • kidney loop of Henle thick ascending limb epithelial cell CL1001106
    CSI 4.94
    rCSI 42.67%
    PRS 22.23
  • fibroblast of lung CL0002553
    CSI 4.86
    rCSI 4.52%
    PRS 12.27
  • cardiac muscle cell CL0000746
    CSI 4.84
    rCSI 6.95%
    PRS 9.56
  • secretory cell CL0000151
    CSI 4.8
    rCSI 5%
    PRS 12.56
  • unswitched memory B cell CL0000970
    CSI 4.77
    rCSI 4.01%
    PRS 19.7
  • type B pancreatic cell CL0000169
    CSI 4.74
    rCSI 10.49%
    PRS 11.35
  • effector CD8-positive, alpha-beta T cell CL0001050
    CSI 4.68
    rCSI 3.56%
    PRS 15.99
  • alveolar type 1 fibroblast cell CL4028004
    CSI 4.65
    rCSI 5.1%
    PRS 13.98
  • inflammatory macrophage CL0000863
    CSI 4.65
    rCSI 7.94%
    PRS 24.65
  • paneth cell of colon CL0009009
    CSI 4.62
    rCSI 45.4%
    PRS 34.76
  • paneth cell CL0000510
    CSI 4.59
    rCSI 6.78%
    PRS 19.25
  • lung goblet cell CL1000143
    CSI 4.54
    rCSI 50.73%
    PRS 40
  • mature alpha-beta T cell CL0000791
    CSI 4.51
    rCSI 16.31%
    PRS 20.98
  • periportal region hepatocyte CL0019026
    CSI 4.46
    rCSI 17.34%
    PRS 17.19
  • basal cell of prostate epithelium CL0002341
    CSI 4.44
    rCSI 12.84%
    PRS 27.21
  • skin fibroblast CL0002620
    CSI 4.42
    rCSI 3.81%
    PRS 19.84
  • enteroendocrine cell CL0000164
    CSI 4.29
    rCSI 5.86%
    PRS 13.56
  • bronchus fibroblast of lung CL2000093
    CSI 4.28
    rCSI 3.48%
    PRS 12.94
  • alveolar adventitial fibroblast CL4028006
    CSI 4.11
    rCSI 6.49%
    PRS 12.23
  • hematopoietic precursor cell CL0008001
    CSI 4.03
    rCSI 4.15%
    PRS 19.92
  • common dendritic progenitor CL0001029
    CSI 4
    rCSI 5.02%
    PRS 15.57
  • peptic cell CL0000155
    CSI 3.97
    rCSI 39.07%
    PRS 36
  • brush cell of tracheobronchial tree CL0002075
    CSI 3.97
    rCSI 11.78%
    PRS 18.15
  • adventitial cell CL0002503
    CSI 3.95
    rCSI 9.43%
    PRS 19.07
  • acinar cell CL0000622
    CSI 3.91
    rCSI 5.74%
    PRS 16.03
  • ciliated cell CL0000064
    CSI 3.81
    rCSI 6.18%
    PRS 12.47
  • precursor B cell CL0000817
    CSI 3.8
    rCSI 3.32%
    PRS 16.2
  • kidney loop of Henle thin ascending limb epithelial cell CL1001107
    CSI 3.75
    rCSI 9.7%
    PRS 11.4
  • IgA plasma cell CL0000987
    CSI 3.72
    rCSI 3.81%
    PRS 22.7
  • interstitial cell of Cajal CL0002088
    CSI 3.61
    rCSI 4.6%
    PRS 14.21
  • CD8-positive, alpha-beta cytotoxic T cell CL0000794
    CSI -12.3
    rCSI -14.7%
    PRS 21.2%
  • retinal blood vessel endothelial cell CL0002585
    CSI -5.8
    rCSI -9.2%
    PRS 13.4%
  • L2/3-6 intratelencephalic projecting glutamatergic neuron CL4023040
    CSI -4.9
    rCSI -12.0%
    PRS 7.0%
  • sncg GABAergic cortical interneuron CL4023015
    CSI -2.2
    rCSI -3.5%
    PRS 7.9%
  • L6b glutamatergic cortical neuron CL4023038
    CSI -1.4
    rCSI -4.4%
    PRS 7.7%
  • double-positive, alpha-beta thymocyte CL0000809
    CSI -0.9
    rCSI -0.9%
    PRS 17.5%
  • lung neuroendocrine cell CL1000223
    CSI -0.9
    rCSI -1.3%
    PRS 14.1%
  • effector CD4-positive, alpha-beta T cell CL0001044
    CSI -0.5
    rCSI -1.4%
    PRS 17.7%
  • cardiac neuron CL0010022
    CSI -0.5
    rCSI -1.5%
    PRS 8.7%
  • chandelier pvalb GABAergic cortical interneuron CL4023036
    CSI -0.1
    rCSI -0.3%
    PRS 8.2%
  • conjunctival epithelial cell CL1000432
    CSI -0.1
    rCSI -0.1%
    PRS 12.3%
  • mesenchymal stem cell CL0000134
    CSI 0.0
    rCSI 0.1%
    PRS 22.1%
  • lymphoid lineage restricted progenitor cell CL0000838
    CSI 0.1
    rCSI 0.3%
    PRS 20.1%
  • erythroblast CL0000765
    CSI 0.1
    rCSI 0.3%
    PRS 20.2%
  • Merkel cell CL0000242
    CSI 0.1
    rCSI 3.3%
    PRS 69.6%
  • collagen secreting cell CL0000667
    CSI 0.2
    rCSI 0.9%
    PRS 44.3%
  • prostate gland microvascular endothelial cell CL2000059
    CSI 0.2
    rCSI 3.7%
    PRS 41.4%
  • fibroblast of cardiac tissue CL0002548
    CSI 0.2
    rCSI 0.8%
    PRS 8.1%
  • vasa recta descending limb cell CL1001285
    CSI 0.2
    rCSI 1.4%
    PRS 48.5%
  • cytotoxic T cell CL0000910
    CSI 0.2
    rCSI 1.1%
    PRS 17.9%
  • dopaminergic neuron CL0000700
    CSI 0.2
    rCSI 1.1%
    PRS 4.8%
  • mature B cell CL0000785
    CSI 0.2
    rCSI 0.2%
    PRS 15.1%
  • mesodermal cell CL0000222
    CSI 0.2
    rCSI 0.3%
    PRS 12.1%
  • OFF-bipolar cell CL0000750
    CSI 0.2
    rCSI 0.3%
    PRS 20.1%
  • fast muscle cell CL0000190
    CSI 0.2
    rCSI 0.9%
    PRS 30.1%
  • pre-conventional dendritic cell CL0002010
    CSI 0.2
    rCSI 2.9%
    PRS 39.6%
  • hair follicular keratinocyte CL2000092
    CSI 0.2
    rCSI 4.0%
    PRS 47.8%
  • forebrain radial glial cell CL0013000
    CSI 0.2
    rCSI 0.8%
    PRS 18.0%
  • retinal cone cell CL0000573
    CSI 0.3
    rCSI 0.4%
    PRS 9.4%
  • VIP GABAergic cortical interneuron CL4023016
    CSI 0.3
    rCSI 0.3%
    PRS 7.0%
  • kidney connecting tubule principal cell CL4030018
    CSI 0.3
    rCSI 2.1%
    PRS 65.7%
  • myeloid lineage restricted progenitor cell CL0000839
    CSI 0.3
    rCSI 1.6%
    PRS 24.0%
  • class switched memory B cell CL0000972
    CSI 0.3
    rCSI 0.3%
    PRS 20.5%
  • corticothalamic-projecting glutamatergic cortical neuron CL4023013
    CSI 0.3
    rCSI 2.0%
    PRS 7.5%
  • CD14-positive, CD16-negative classical monocyte CL0002057
    CSI 0.3
    rCSI 2.1%
    PRS 27.3%
  • effector memory CD8-positive, alpha-beta T cell, terminally differentiated CL0001062
    CSI 0.4
    rCSI 1.8%
    PRS 15.9%
  • renal interstitial pericyte CL1001318
    CSI 0.4
    rCSI 1.0%
    PRS 11.5%
  • lung microvascular endothelial cell CL2000016
    CSI 0.4
    rCSI 7.5%
    PRS 38.4%
  • CD8-positive, alpha-beta thymocyte CL0000811
    CSI 0.4
    rCSI 0.6%
    PRS 29.6%
  • stromal cell of ovary CL0002132
    CSI 0.4
    rCSI 1.1%
    PRS 20.2%
  • primitive red blood cell CL0002355
    CSI 0.4
    rCSI 2.3%
    PRS 22.9%
  • enteroendocrine cell of small intestine CL0009006
    CSI 0.4
    rCSI 0.9%
    PRS 18.8%
  • thymocyte CL0000893
    CSI 0.4
    rCSI 1.5%
    PRS 38.0%
  • peripheral nervous system neuron CL2000032
    CSI 0.4
    rCSI 0.6%
    PRS 10.9%
  • intermediate monocyte CL0002393
    CSI 0.4
    rCSI 0.7%
    PRS 12.1%
  • colon macrophage CL0009038
    CSI 0.4
    rCSI 2.0%
    PRS 25.4%
  • serous secreting cell CL0000313
    CSI 0.4
    rCSI 2.3%
    PRS 48.8%
  • basophil mast progenitor cell CL0002028
    CSI 0.5
    rCSI 2.5%
    PRS 44.1%
  • myeloid dendritic cell, human CL0001057
    CSI 0.5
    rCSI 2.7%
    PRS 38.4%
  • retinal bipolar neuron CL0000748
    CSI 0.5
    rCSI 0.9%
    PRS 8.8%
  • macula densa epithelial cell CL1000850
    CSI 0.5
    rCSI 7.1%
    PRS 62.7%
  • metallothionein-positive alveolar macrophage CL4033042
    CSI 0.5
    rCSI 5.5%
    PRS 47.2%
  • parietal epithelial cell CL1000452
    CSI 0.5
    rCSI 1.4%
    PRS 10.5%
  • lung secretory cell CL1000272
    CSI 0.5
    rCSI 1.3%
    PRS 11.3%
  • endothelial cell of placenta CL0009092
    CSI 0.5
    rCSI 2.6%
    PRS 16.6%
  • vasa recta ascending limb cell CL1001131
    CSI 0.5
    rCSI 2.5%
    PRS 44.2%
  • activated CD8-positive, alpha-beta T cell, human CL0001049
    CSI 0.6
    rCSI 1.0%
    PRS 24.4%
  • corneal epithelial cell CL0000575
    CSI 0.6
    rCSI 1.6%
    PRS 22.1%
  • L5 extratelencephalic projecting glutamatergic cortical neuron CL4023041
    CSI 0.6
    rCSI 2.0%
    PRS 6.6%
  • effector memory CD8-positive, alpha-beta T cell CL0000913
    CSI 0.6
    rCSI 0.5%
    PRS 18.5%
  • smooth muscle cell of the pulmonary artery CL0002591
    CSI 0.6
    rCSI 4.4%
    PRS 44.6%
  • cell of skeletal muscle CL0000188
    CSI 0.6
    rCSI 6.8%
    PRS 59.8%
  • common lymphoid progenitor CL0000051
    CSI 0.7
    rCSI 0.9%
    PRS 23.3%
  • tracheobronchial smooth muscle cell CL0019019
    CSI 0.7
    rCSI 1.2%
    PRS 16.1%
  • dendritic cell, human CL0001056
    CSI 0.7
    rCSI 1.0%
    PRS 14.3%
  • megakaryocyte progenitor cell CL0000553
    CSI 0.7
    rCSI 12.4%
    PRS 34.9%
  • helper T cell CL0000912
    CSI 0.7
    rCSI 1.0%
    PRS 17.1%
  • neuroendocrine cell CL0000165
    CSI 0.7
    rCSI 2.8%
    PRS 25.1%
  • retinal ganglion cell CL0000740
    CSI 0.7
    rCSI 1.6%
    PRS 8.8%
  • megakaryocyte CL0000556
    CSI 0.8
    rCSI 3.3%
    PRS 22.0%
  • eosinophil CL0000771
    CSI 0.8
    rCSI 5.2%
    PRS 31.7%
  • hematopoietic multipotent progenitor cell CL0000837
    CSI 0.8
    rCSI 1.9%
    PRS 19.4%
  • choroid plexus epithelial cell CL0000706
    CSI 0.8
    rCSI 1.3%
    PRS 9.4%
  • CD4-positive, alpha-beta cytotoxic T cell CL0000934
    CSI 0.8
    rCSI 1.2%
    PRS 25.2%
  • Bergmann glial cell CL0000644
    CSI 0.8
    rCSI 1.2%
    PRS 12.5%
  • mature T cell CL0002419
    CSI 0.9
    rCSI 0.7%
    PRS 17.6%
  • small intestine goblet cell CL1000495
    CSI 0.9
    rCSI 1.9%
    PRS 16.3%
  • platelet CL0000233
    CSI 0.9
    rCSI 3.6%
    PRS 26.3%
  • endocardial cell CL0002350
    CSI 0.9
    rCSI 4.2%
    PRS 15.8%
  • adipocyte CL0000136
    CSI 0.9
    rCSI 1.2%
    PRS 12.4%
  • neural progenitor cell CL0011020
    CSI 0.9
    rCSI 4.1%
    PRS 11.9%
  • promyelocyte CL0000836
    CSI 1.0
    rCSI 1.4%
    PRS 17.0%
  • astrocyte of the cerebral cortex CL0002605
    CSI 1.0
    rCSI 2.1%
    PRS 7.5%
  • retina horizontal cell CL0000745
    CSI 1.0
    rCSI 1.5%
    PRS 11.4%
  • alternatively activated macrophage CL0000890
    CSI 1.0
    rCSI 1.2%
    PRS 18.7%
  • vein endothelial cell of respiratory system CL4033008
    CSI 1.0
    rCSI 6.9%
    PRS 24.0%
  • pulmonary alveolar type 1 cell CL0002062
    CSI 1.0
    rCSI 5.9%
    PRS 16.3%
  • cerebellar granule cell CL0001031
    CSI 1.0
    rCSI 1.5%
    PRS 11.2%
  • myoepithelial cell CL0000185
    CSI 1.1
    rCSI 2.7%
    PRS 15.2%
  • glioblast CL0000030
    CSI 1.1
    rCSI 1.7%
    PRS 10.5%
  • CD4-positive helper T cell CL0000492
    CSI 1.1
    rCSI 0.8%
    PRS 16.9%
  • CD14-low, CD16-positive monocyte CL0002396
    CSI 1.1
    rCSI 0.8%
    PRS 11.1%
  • serous secreting cell of bronchus submucosal gland CL4033005
    CSI 1.1
    rCSI 6.2%
    PRS 45.6%
  • mononuclear phagocyte CL0000113
    CSI 1.1
    rCSI 2.4%
    PRS 13.5%
  • kidney interstitial alternatively activated macrophage CL1000695
    CSI 1.1
    rCSI 2.9%
    PRS 11.3%
  • tendon cell CL0000388
    CSI 1.1
    rCSI 2.9%
    PRS 33.2%
  • immature B cell CL0000816
    CSI 1.1
    rCSI 0.8%
    PRS 18.1%
  • kidney loop of Henle thin descending limb epithelial cell CL1001111
    CSI 1.1
    rCSI 1.6%
    PRS 11.4%
  • kidney connecting tubule epithelial cell CL1000768
    CSI 1.1
    rCSI 2.9%
    PRS 9.3%
  • T-helper 17 cell CL0000899
    CSI 1.2
    rCSI 0.9%
    PRS 21.5%

Cell ID: Standard Cell Ontology term used for mapping and comparing cells across experiments. Ensures consistency in analyzing cellular functions across tissues.
Fold Change: Represents the ratio of the current Cell Significance Index to the Cell Significance Index Threshold, indicating how much the gene expression has changed compared to a baseline.
Cell Significance Index: Reflects how strongly a gene is expressed in this specific cell.

Cell ID: Standard Cell Ontology term used for mapping and comparing cells across experiments. Ensures consistency in analyzing cellular functions across tissues.
Fold Change: Represents the ratio of the current Cell Significance Index to the Cell Significance Index Threshold, indicating how much the gene expression has changed compared to a baseline.
Cell Significance Index: Reflects how strongly a gene is expressed in this cell type. Calculated using techniques like effect size estimation and bootstrapping for reliability.

Cell ID: Standard Cell Ontology term used for mapping and comparing cells across experiments. Ensures consistency in analyzing cellular functions across tissues.
Fold Change: Represents the ratio of the current Cell Significance Index to the Cell Significance Index Threshold, indicating how much the gene expression has changed compared to a baseline.
Cell Significance Index: Reflects how strongly a gene is expressed in this cell type. Calculated using techniques like effect size estimation and bootstrapping for reliability.
Network Configuration

Explore relationships of the current gene. Select an Interaction Source: 'ONTOLOGY' for shared pathways (GO/Reactome) or 'STRING' for protein-protein interactions. Further refine by selecting context genes and comparing Cell Significance Index (CSI) scores between baseline and target cell types and their specific contexts.

Comma-separated if multiple.
Comma-separated if multiple.

Legend:
  • Query Gene
  • Node Color (Target Cell CSI, relative to current network):
    • Very High
    • High
    • Medium
    • Low
    • Very Low
    • CSI N/A
  • Node Size: Proportional to Target Cell CSI magnitude
  • STRING PPI Edge
  • Shared Pathway Edge (ONTOLOGY)

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Other Information

This section provides additional information about the gene, including a description generated by an AI language model and details about associated proteins.

## Summary [ACADVL](/details-gene/37), or Acyl-CoA Dehydrogenase Very Long Chain, is a protein-coding gene located on human chromosome 17p13.1. It encodes a critical mitochondrial enzyme that catalyzes the initial step of the beta-oxidation of very-long-chain fatty acids. This function positions [ACADVL](/details-gene/37) as a key player in cellular energy metabolism, particularly in tissues with high energy demands. Its expression is most significant in various epithelial cells, especially those of the gastrointestinal tract, such as [M cell of gut](/details-cell/CL0000682) and [colon epithelial cell](/details-cell/CL0011108), as well as in placental trophoblasts. Clinically, mutations in the [ACADVL](/details-gene/37) gene are associated with Very Long-Chain Acyl-CoA Dehydrogenase (VLCAD) deficiency ([201475](https://omim.org/entry/201475)), a serious inborn error of metabolism [Link](https://pubmed.ncbi.nlm.nih.gov/9973285/). ## Cellular Roles and Expression Landscape The **Overall** expression profile of [ACADVL](/details-gene/37) highlights its specialized role in metabolically active tissues. It exhibits the highest significance in epithelial cells lining the gut, including [M cell of gut](/details-cell/CL0000682), [colon epithelial cell](/details-cell/CL0011108), [transit amplifying cell of colon](/details-cell/CL0009011), and [enterocyte](/details-cell/CL0000584). This pattern suggests a crucial function in providing energy for the high-turnover environment of the intestinal epithelium, which is responsible for nutrient absorption and barrier maintenance. High significance is also observed in other high-demand cell types such as [stem cell](/details-cell/CL0000034), [placental villous trophoblast](/details-cell/CL2000060), and various pancreatic cells ([pancreatic acinar cell](/details-cell/CL0002064), [pancreatic ductal cell](/details-cell/CL0002079)). The pronounced expression in placental tissue underscores its likely importance in supporting fetal development through efficient energy production. Conversely, [ACADVL](/details-gene/37) shows very low to negative significance in hematopoietic and neural lineages. Notably, its expression is significantly low in immune cells like [CD8-positive, alpha-beta cytotoxic T cell](/details-cell/CL0000794) and various neuronal subtypes, including [L2/3-6 intratelencephalic projecting glutamatergic neuron](/details-cell/CL4023040). This restricted expression pattern indicates that [ACADVL](/details-gene/37) is not a ubiquitous housekeeping gene for fatty acid metabolism but is instead tailored to the specific energetic requirements of absorptive and secretory epithelial tissues. ## Pathways and Molecular Function Functionally, [ACADVL](/details-gene/37) is annotated with [very-long-chain fatty acyl-coa dehydrogenase activity](/details-gene/GO:0017099) and [acyl-coa dehydrogenase activity](/details-gene/GO:0003995), consistent with its central role in the biological process of [fatty acid beta-oxidation using acyl-coa dehydrogenase](/details-gene/GO:0033539). Its protein product is localized primarily to the [mitochondrial inner membrane](/details-gene/GO:0005743) and [mitochondrial matrix](/details-gene/GO:0005759), the site of fatty acid oxidation. The gene's activity is integral to several key Reactome pathways, most prominently [mitochondrial fatty acid beta-oxidation](/details-gene/R-HSA-77289) and the broader [metabolism of lipids](/details-gene/R-HSA-556833). This is consistent with its high expression in enterocytes and colonocytes, which rely on fatty acid oxidation for energy. Beyond core metabolism, [ACADVL](/details-gene/37) is also implicated in pathways related to cellular stress, such as the [unfolded protein response (upr)](/details-gene/R-HSA-381119) and [cellular responses to stress](/details-gene/R-HSA-2262752). This connection may reflect a role in managing metabolic stress in cells undergoing high rates of lipid processing. ## Research Directions Given the well-established role of [ACADVL](/details-gene/37) in inherited metabolic disease, future research can explore its function in complex diseases affecting high-expression tissues. ### Proposed Hypotheses: 1. **Hypothesis 1:** Due to its high expression in gut epithelial cells and its role in energy production, [ACADVL](/details-gene/37) may be essential for maintaining intestinal barrier integrity. Reduced [ACADVL](/details-gene/37) activity, whether through genetic variation or environmental stressors, could impair energy supply to colonocytes, leading to a compromised epithelial barrier and contributing to the pathophysiology of inflammatory bowel disease (IBD). 2. **Hypothesis 2:** The significant expression of [ACADVL](/details-gene/37) in placental trophoblasts suggests it is critical for placental bioenergetics. Insufficient [ACADVL](/details-gene/37)-mediated fatty acid oxidation may contribute to placental dysfunction, potentially linking it to pregnancy complications such as pre-eclampsia or intrauterine growth restriction (IUGR). ### Key Experiment: To test the role of [ACADVL](/details-gene/37) in gut barrier function (Hypothesis 1), one could utilize a conditional knockout mouse model where [ACADVL](/details-gene/37) is specifically deleted in intestinal epithelial cells. These mice, along with wild-type controls, could be subjected to a dextran sulfate sodium (DSS)-induced colitis model. The experimental readout would involve assessing disease severity (weight loss, colon length), histological damage, and direct measurement of barrier permeability using an in vivo FITC-dextran assay. Furthermore, isolated colonocytes from these mice could be analyzed for ATP levels and oxygen consumption rates to directly measure the metabolic defect. ### Therapeutic Potential: As a therapeutic target, [ACADVL](/details-gene/37) is primarily relevant in the context of its deficiency. The therapeutic goal is therefore **activation** or restoration of function, not inhibition. For patients with VLCAD deficiency ([201475](https://omim.org/entry/201475)), current management involves dietary modification, but this is not always sufficient. Gene therapy aimed at delivering a functional copy of the [ACADVL](/details-gene/37) gene to affected tissues like the liver and muscle represents a potential long-term curative strategy. Furthermore, if a role in conditions like IBD is substantiated, developing small-molecule activators of [ACADVL](/details-gene/37) could offer a novel therapeutic approach to bolster epithelial metabolism and enhance gut barrier function.

Genular Protein ID: 1016093399

Symbol: ACADV_HUMAN

Name: N/A

UniProtKB Accession Codes:

Database IDs:

Citations:

PubMed ID: 7668252

Title: Cloning of human very-long-chain acyl-coenzyme A dehydrogenase and molecular characterization of its deficiency in two patients.

PubMed ID: 7668252

PubMed ID: 8845838

Title: Cloning and characterization of human very-long-chain acyl-CoA dehydrogenase cDNA, chromosomal assignment of the gene and identification in four patients of nine different mutations within the VLCAD gene.

PubMed ID: 8845838

DOI: 10.1093/hmg/5.4.461

PubMed ID: 8554625

Title: Genomic DNA organization of human mitochondrial very-long-chain acyl-CoA dehydrogenase and mutation analysis.

PubMed ID: 8554625

DOI: 10.1006/bbrc.1995.2867

PubMed ID: 14702039

Title: Complete sequencing and characterization of 21,243 full-length human cDNAs.

PubMed ID: 14702039

DOI: 10.1038/ng1285

PubMed ID: 16625196

Title: DNA sequence of human chromosome 17 and analysis of rearrangement in the human lineage.

PubMed ID: 16625196

DOI: 10.1038/nature04689

PubMed ID: 15489334

Title: The status, quality, and expansion of the NIH full-length cDNA project: the Mammalian Gene Collection (MGC).

PubMed ID: 15489334

DOI: 10.1101/gr.2596504

PubMed ID: 7769092

Title: Purification of human very-long-chain acyl-coenzyme A dehydrogenase and characterization of its deficiency in seven patients.

PubMed ID: 7769092

DOI: 10.1172/jci117947

PubMed ID: 9461620

Title: Catalytic and FAD-binding residues of mitochondrial very long chain acyl-coenzyme A dehydrogenase.

PubMed ID: 9461620

DOI: 10.1074/jbc.273.7.4227

PubMed ID: 9973285

Title: Clear correlation of genotype with disease phenotype in very-long-chain acyl-CoA dehydrogenase deficiency.

PubMed ID: 9973285

DOI: 10.1086/302261

PubMed ID: 17374501

Title: Expression and characterization of mutations in human very long-chain acyl-CoA dehydrogenase using a prokaryotic system.

PubMed ID: 17374501

DOI: 10.1016/j.ymgme.2007.01.013

PubMed ID: 19608861

Title: Lysine acetylation targets protein complexes and co-regulates major cellular functions.

PubMed ID: 19608861

DOI: 10.1126/science.1175371

PubMed ID: 21269460

Title: Initial characterization of the human central proteome.

PubMed ID: 21269460

DOI: 10.1186/1752-0509-5-17

PubMed ID: 21237683

Title: Identification and characterization of new long chain acyl-CoA dehydrogenases.

PubMed ID: 21237683

DOI: 10.1016/j.ymgme.2010.12.005

PubMed ID: 23186163

Title: Toward a comprehensive characterization of a human cancer cell phosphoproteome.

PubMed ID: 23186163

DOI: 10.1021/pr300630k

PubMed ID: 24275569

Title: An enzyme assisted RP-RPLC approach for in-depth analysis of human liver phosphoproteome.

PubMed ID: 24275569

DOI: 10.1016/j.jprot.2013.11.014

PubMed ID: 25944712

Title: N-terminome analysis of the human mitochondrial proteome.

PubMed ID: 25944712

DOI: 10.1002/pmic.201400617

PubMed ID: 18227065

Title: Structural basis for substrate fatty acyl chain specificity: crystal structure of human very-long-chain acyl-CoA dehydrogenase.

PubMed ID: 18227065

DOI: 10.1074/jbc.m709135200

PubMed ID: 8554073

Title: Mutation analysis of very-long-chain acyl-coenzyme A dehydrogenase (VLCAD) deficiency: identification and characterization of mutant VLCAD cDNAs from four patients.

PubMed ID: 8554073

PubMed ID: 9546340

Title: Very long chain acyl-coenzyme A dehydrogenase deficiency with adult onset.

PubMed ID: 9546340

DOI: 10.1002/ana.410430422

PubMed ID: 9839948

Title: Relationship between structure and substrate-chain-length specificity of mitochondrial very-long-chain acyl-coenzyme A dehydrogenase.

PubMed ID: 9839948

DOI: 10.1046/j.1432-1327.1998.2570592.x

PubMed ID: 9599005

Title: Very-long-chain acyl-CoA dehydrogenase subunit assembles to the dimer form on mitochondrial inner membrane.

PubMed ID: 9599005

DOI: 10.1016/s0014-5793(98)00343-3

PubMed ID: 10077518

Title: Molecular heterogeneity in very-long-chain acyl-CoA dehydrogenase deficiency causing pediatric cardiomyopathy and sudden death.

PubMed ID: 10077518

DOI: 10.1161/01.cir.99.10.1337

Sequence Information:

  • Length: 655
  • Mass: 70390
  • Checksum: A5594D1EA7911D19
  • Sequence:
  • MQAARMAASL GRQLLRLGGG SSRLTALLGQ PRPGPARRPY AGGAAQLALD KSDSHPSDAL 
    TRKKPAKAES KSFAVGMFKG QLTTDQVFPY PSVLNEEQTQ FLKELVEPVS RFFEEVNDPA 
    KNDALEMVEE TTWQGLKELG AFGLQVPSEL GGVGLCNTQY ARLVEIVGMH DLGVGITLGA 
    HQSIGFKGIL LFGTKAQKEK YLPKLASGET VAAFCLTEPS SGSDAASIRT SAVPSPCGKY 
    YTLNGSKLWI SNGGLADIFT VFAKTPVTDP ATGAVKEKIT AFVVERGFGG ITHGPPEKKM 
    GIKASNTAEV FFDGVRVPSE NVLGEVGSGF KVAMHILNNG RFGMAAALAG TMRGIIAKAV 
    DHATNRTQFG EKIHNFGLIQ EKLARMVMLQ YVTESMAYMV SANMDQGATD FQIEAAISKI 
    FGSEAAWKVT DECIQIMGGM GFMKEPGVER VLRDLRIFRI FEGTNDILRL FVALQGCMDK 
    GKELSGLGSA LKNPFGNAGL LLGEAGKQLR RRAGLGSGLS LSGLVHPELS RSGELAVRAL 
    EQFATVVEAK LIKHKKGIVN EQFLLQRLAD GAIDLYAMVV VLSRASRSLS EGHPTAQHEK 
    MLCDTWCIEA AARIREGMAA LQSDPWQQEL YRNFKSISKA LVERGGVVTS NPLGF

Genular Protein ID: 1807849729

Symbol: B3KPA6_HUMAN

Name: N/A

UniProtKB Accession Codes:

Database IDs:

Citations:

PubMed ID: 11181995

Title: The sequence of the human genome.

PubMed ID: 11181995

DOI: 10.1126/science.1058040

PubMed ID: 14702039

Title: Complete sequencing and characterization of 21,243 full-length human cDNAs.

PubMed ID: 14702039

DOI: 10.1038/ng1285

Sequence Information:

  • Length: 579
  • Mass: 62582
  • Checksum: F354E18C74751AE8
  • Sequence:
  • MFKGQLTTDQ VFPYPSVLNE EQTQFLKELV EPVSRFFEEV NDPAKNDALE MVEETTWQGL 
    KELGAFGLQV PSELGGVGLC NTQYARLVEI VGMHDLGVGI TLGAHQSIGF KGILLFGTKA 
    QKEKYLPKLA SGETVAAFCL TEPSSGSDAA SIRTSAVPSP CGKYYTLNGS KLWISNGGLA 
    DIFTVFAKTP VTDPATGAVK EKITAFVVER GFGGITHGPP EKKMGIKASN TAEVFFDGVR 
    VPSENVLGEV GSGFKVAMHI LNNGRFGMAA ALAGTMRGII AKAVDHATNR TQFGEKIHNF 
    GLIQEKLARM VMLQYVTESM AYMVSANMDQ GATDFQIEAA ISKIFGSEAA WKVTDECIQI 
    MGGMGFMKEP GVERVLRDLR IFRIFEGTND ILRLFVALQG CMDKGKELSG LGSALKNPFG 
    NAGLLLGEAG KQLRRRAGLG SGLSLSGLVH PELSRSGELA VRALEQFATV VEAKLIKHKK 
    GIVNEQFLLQ RLADGAIDLY AMVVVLSRAS RSLSEGHPTA QHEKMLCDTW CIEAAARIRE 
    GMAALQSDPW QQELYRNFKS ISKALVERGG VVTSNPLGF