Details for: ASPA

Gene ID: 443

Symbol: ASPA

Ensembl ID: ENSG00000108381

Description: aspartoacylase

Associated with

Other Information

Genular Protein ID: 1147104961

Symbol: ACY2_HUMAN

Name: Aminoacylase-2

UniProtKB Accession Codes:

Database IDs:

Citations:

PubMed ID: 8252036

Title: Cloning of the human aspartoacylase cDNA and a common missense mutation in Canavan disease.

PubMed ID: 8252036

DOI: 10.1038/ng1093-118

PubMed ID: 15489334

Title: The status, quality, and expansion of the NIH full-length cDNA project: the Mammalian Gene Collection (MGC).

PubMed ID: 15489334

DOI: 10.1101/gr.2596504

PubMed ID: 12706335

Title: Purification and preliminary characterization of brain aspartoacylase.

PubMed ID: 12706335

DOI: 10.1016/s0003-9861(03)00055-9

PubMed ID: 17027983

Title: Identification of the zinc binding ligands and the catalytic residue in human aspartoacylase, an enzyme involved in Canavan disease.

PubMed ID: 17027983

DOI: 10.1016/j.febslet.2006.09.056

PubMed ID: 18293939

Title: Examination of the mechanism of human brain aspartoacylase through the binding of an intermediate analogue.

PubMed ID: 18293939

DOI: 10.1021/bi702400x

PubMed ID: 17194761

Title: Structure of aspartoacylase, the brain enzyme impaired in Canavan disease.

PubMed ID: 17194761

DOI: 10.1073/pnas.0607817104

PubMed ID: 8023850

Title: Canavan disease: mutations among Jewish and non-Jewish patients.

PubMed ID: 8023850

PubMed ID: 7668285

Title: The molecular basis of canavan (aspartoacylase deficiency) disease in European non-Jewish patients.

PubMed ID: 7668285

PubMed ID: 7599639

Title: Novel (Cys152 > Arg) missense mutation in an Arab patient with Canavan disease.

PubMed ID: 7599639

DOI: 10.1002/humu.1380050313

PubMed ID: 8659549

Title: Identification and expression of eight novel mutations among non-Jewish patients with Canavan disease.

PubMed ID: 8659549

PubMed ID: 9452117

Title: Missense mutation (I143T) in a Japanese patient with Canavan disease.

PubMed ID: 9452117

DOI: 10.1002/humu.1380110196

PubMed ID: 10564886

Title: Novel missense mutation (Y231C) in a Turkish patient with Canavan disease.

PubMed ID: 10564886

DOI: 10.1002/(sici)1096-8628(19991126)87:3<273::aid-ajmg17>3.0.co;2-o

PubMed ID: 10407784

Title: The spectrum of mutations of the aspartoacylase gene in Canavan disease in non-Jewish patients.

PubMed ID: 10407784

DOI: 10.1023/a:1005512524957

PubMed ID: 10909858

Title: Mutation detection in the aspartoacylase gene in 17 patients with Canavan disease: four new mutations in the non-Jewish population.

PubMed ID: 10909858

DOI: 10.1038/sj.ejhg.5200477

PubMed ID: 12638939

Title: Identification and characterization of novel mutations of the aspartoacylase gene in non-Jewish patients with Canavan disease.

PubMed ID: 12638939

DOI: 10.1023/a:1022091223498

PubMed ID: 12205125

Title: Two novel aspartoacylase gene (ASPA) missense mutations specific to Norwegian and Swedish patients with Canavan disease.

PubMed ID: 12205125

DOI: 10.1136/jmg.39.9.e55

PubMed ID: 24036223

Title: New T530C mutation in the aspartoacylase gene caused Canavan disease with no correlation between severity and N-acetylaspartate excretion.

PubMed ID: 24036223

DOI: 10.1016/j.clinbiochem.2013.09.004

PubMed ID: 28101991

Title: Clinically distinct phenotypes of Canavan disease correlate with residual aspartoacylase enzyme activity.

PubMed ID: 28101991

DOI: 10.1002/humu.23181

Sequence Information:

  • Length: 313
  • Mass: 35735
  • Checksum: 33C0B9B07839E7F5
  • Sequence:
  • MTSCHIAEEH IQKVAIFGGT HGNELTGVFL VKHWLENGAE IQRTGLEVKP FITNPRAVKK 
    CTRYIDCDLN RIFDLENLGK KMSEDLPYEV RRAQEINHLF GPKDSEDSYD IIFDLHNTTS 
    NMGCTLILED SRNNFLIQMF HYIKTSLAPL PCYVYLIEHP SLKYATTRSI AKYPVGIEVG 
    PQPQGVLRAD ILDQMRKMIK HALDFIHHFN EGKEFPPCAI EVYKIIEKVD YPRDENGEIA 
    AIIHPNLQDQ DWKPLHPGDP MFLTLDGKTI PLGGDCTVYP VFVNEAAYYE KKEAFAKTTK 
    LTLNAKSIRC CLH

Database document:

This is a preview of the gene's schema. Only a few entries are kept for 'singleCellExpressions,' 'mRNAExpressions,' and other large data arrays for visualization purposes. You can zoom in with the mouse wheel for a closer view, and the text will adjust automatically if necessary. For the full schema, download it here.