Details for: ATP7A

Gene ID: 538

Symbol: ATP7A

Ensembl ID: ENSG00000165240

Description: ATPase copper transporting alpha

Associated with

Other Information

Genular Protein ID: 715975783

Symbol: ATP7A_HUMAN

Name: Copper-transporting ATPase 1

UniProtKB Accession Codes:

Database IDs:

Citations:

PubMed ID: 8490659

Title: Isolation of a candidate gene for Menkes disease and evidence that it encodes a copper-transporting ATPase.

PubMed ID: 8490659

DOI: 10.1038/ng0193-7

PubMed ID: 7607665

Title: Characterization of the exon structure of the Menkes disease gene using vectorette PCR.

PubMed ID: 7607665

DOI: 10.1016/0888-7543(95)80160-n

PubMed ID: 9693104

Title: Multiple transcripts coding for the menkes gene: evidence for alternative splicing of Menkes mRNA.

PubMed ID: 9693104

DOI: 10.1042/bj3340071

PubMed ID: 10079814

Title: Multiple forms of the Menkes Cu-ATPase.

PubMed ID: 10079814

DOI: 10.1007/978-1-4615-4859-1_4

PubMed ID: 15772651

Title: The DNA sequence of the human X chromosome.

PubMed ID: 15772651

DOI: 10.1038/nature03440

PubMed ID: 7490081

Title: Molecular structure of the Menkes disease gene (ATP7A).

PubMed ID: 7490081

DOI: 10.1006/geno.1995.1175

PubMed ID: 8490646

Title: Isolation of a candidate gene for Menkes disease that encodes a potential heavy metal binding protein.

PubMed ID: 8490646

DOI: 10.1038/ng0193-14

PubMed ID: 8490647

Title: Isolation of a partial candidate gene for Menkes disease by positional cloning.

PubMed ID: 8490647

DOI: 10.1038/ng0193-20

PubMed ID: 11214319

Title: Molecular phylogenetics and the origins of placental mammals.

PubMed ID: 11214319

DOI: 10.1038/35054550

PubMed ID: 9467005

Title: Constitutive skipping of alternatively spliced exon 10 in the ATP7A gene abolishes Golgi localization of the menkes protein and produces the occipital horn syndrome.

PubMed ID: 9467005

DOI: 10.1093/hmg/7.3.465

PubMed ID: 10970802

Title: Evidence for a Menkes-like protein with a nuclear targeting sequence.

PubMed ID: 10970802

DOI: 10.1042/bj3500855

PubMed ID: 9147644

Title: Immunocytochemical localization of the Menkes copper transport protein (ATP7A) to the trans-Golgi network.

PubMed ID: 9147644

DOI: 10.1093/hmg/6.3.409

PubMed ID: 10484781

Title: The Menkes protein (ATP7A; MNK) cycles via the plasma membrane both in basal and elevated extracellular copper using a C-terminal di-leucine endocytic signal.

PubMed ID: 10484781

DOI: 10.1093/hmg/8.11.2107

PubMed ID: 10419525

Title: Functional analysis of the N-terminal CXXC metal-binding motifs in the human Menkes copper-transporting P-type ATPase expressed in cultured mammalian cells.

PubMed ID: 10419525

DOI: 10.1074/jbc.274.31.22008

PubMed ID: 11092760

Title: The Menkes copper transporter is required for the activation of tyrosinase.

PubMed ID: 11092760

DOI: 10.1093/hmg/9.19.2845

PubMed ID: 16051599

Title: A single PDZ domain protein interacts with the Menkes copper ATPase, ATP7A. A new protein implicated in copper homeostasis.

PubMed ID: 16051599

DOI: 10.1074/jbc.m505889200

PubMed ID: 16371425

Title: Essential role for the Menkes ATPase in activation of extracellular superoxide dismutase: implication for vascular oxidative stress.

PubMed ID: 16371425

DOI: 10.1096/fj.05-4564fje

PubMed ID: 19690332

Title: Quantitative phosphoproteomic analysis of T cell receptor signaling reveals system-wide modulation of protein-protein interactions.

PubMed ID: 19690332

DOI: 10.1126/scisignal.2000007

PubMed ID: 20068231

Title: Quantitative phosphoproteomics reveals widespread full phosphorylation site occupancy during mitosis.

PubMed ID: 20068231

DOI: 10.1126/scisignal.2000475

PubMed ID: 21667063

Title: The copper-transporting capacity of ATP7A mutants associated with Menkes disease is ameliorated by COMMD1 as a result of improved protein expression.

PubMed ID: 21667063

DOI: 10.1007/s00018-011-0743-1

PubMed ID: 23186163

Title: Toward a comprehensive characterization of a human cancer cell phosphoproteome.

PubMed ID: 23186163

DOI: 10.1021/pr300630k

PubMed ID: 24275569

Title: An enzyme assisted RP-RPLC approach for in-depth analysis of human liver phosphoproteome.

PubMed ID: 24275569

DOI: 10.1016/j.jprot.2013.11.014

PubMed ID: 9437429

Title: Solution structure of the fourth metal-binding domain from the Menkes copper-transporting ATPase.

PubMed ID: 9437429

DOI: 10.1038/nsb0198-47

PubMed ID: 19453293

Title: Copper(I)-mediated protein-protein interactions result from suboptimal interaction surfaces.

PubMed ID: 19453293

DOI: 10.1042/bj20090422

PubMed ID: 19917612

Title: The binding mode of ATP revealed by the solution structure of the N-domain of human ATP7A.

PubMed ID: 19917612

DOI: 10.1074/jbc.m109.054262

PubMed ID: 31283225

Title: Mechanistic and Structural Basis for Inhibition of Copper Trafficking by Platinum Anticancer Drugs.

PubMed ID: 31283225

DOI: 10.1021/jacs.9b05550

PubMed ID: 10079817

Title: Mutation spectrum of ATP7A, the gene defective in Menkes disease.

PubMed ID: 10079817

DOI: 10.1007/978-1-4615-4859-1_7

PubMed ID: 7977350

Title: Diverse mutations in patients with Menkes disease often lead to exon skipping.

PubMed ID: 7977350

PubMed ID: 8981948

Title: Identification of point mutations in 41 unrelated patients affected with Menkes disease.

PubMed ID: 8981948

PubMed ID: 9246006

Title: A C2055T transition in exon 8 of the ATP7A gene is associated with exon skipping in an occipital horn syndrome family.

PubMed ID: 9246006

DOI: 10.1016/s0002-9297(07)64297-9

PubMed ID: 10401004

Title: Defective copper-induced trafficking and localization of the Menkes protein in patients with mild and copper-treated classical Menkes disease.

PubMed ID: 10401004

DOI: 10.1093/hmg/8.8.1547

PubMed ID: 10319589

Title: Identification of three novel mutations in the MNK gene in three unrelated Japanese patients with classical Menkes disease.

PubMed ID: 10319589

DOI: 10.1007/s100380050144

PubMed ID: 11431706

Title: A novel frameshift mutation in exon 23 of ATP7A (MNK) results in occipital horn syndrome and not in Menkes disease.

PubMed ID: 11431706

DOI: 10.1086/321290

PubMed ID: 11241493

Title: ATP7A gene mutations in 16 patients with Menkes disease and a patient with occipital horn syndrome.

PubMed ID: 11241493

DOI: 10.1002/1096-8628(2001)9999:9999<::aid-ajmg1167>3.0.co;2-r

PubMed ID: 11350187

Title: Identification of four novel mutations in classical Menkes disease and successful prenatal DNA diagnosis.

PubMed ID: 11350187

DOI: 10.1006/mgme.2001.3169

PubMed ID: 15981243

Title: Identification and analysis of 21 novel disease-causing amino acid substitutions in the conserved part of ATP7A.

PubMed ID: 15981243

DOI: 10.1002/humu.20190

PubMed ID: 17108763

Title: Functional copper transport explains neurologic sparing in occipital horn syndrome.

PubMed ID: 17108763

DOI: 10.1097/01.gim.0000245578.94312.1e

PubMed ID: 20170900

Title: Missense mutations in the copper transporter gene ATP7A cause X-linked distal hereditary motor neuropathy.

PubMed ID: 20170900

DOI: 10.1016/j.ajhg.2010.01.027

PubMed ID: 22992316

Title: The T1048I mutation in ATP7A gene causes an unusual Menkes disease presentation.

PubMed ID: 22992316

DOI: 10.1186/1471-2431-12-150

PubMed ID: 28389643

Title: Characterization of ATP7A missense mutants suggests a correlation between intracellular trafficking and severity of Menkes disease.

PubMed ID: 28389643

DOI: 10.1038/s41598-017-00618-6

Sequence Information:

  • Length: 1500
  • Mass: 163373
  • Checksum: A54F17EA08FDACDB
  • Sequence:
  • MDPSMGVNSV TISVEGMTCN SCVWTIEQQI GKVNGVHHIK VSLEEKNATI IYDPKLQTPK 
    TLQEAIDDMG FDAVIHNPDP LPVLTDTLFL TVTASLTLPW DHIQSTLLKT KGVTDIKIYP 
    QKRTVAVTII PSIVNANQIK ELVPELSLDT GTLEKKSGAC EDHSMAQAGE VVLKMKVEGM 
    TCHSCTSTIE GKIGKLQGVQ RIKVSLDNQE ATIVYQPHLI SVEEMKKQIE AMGFPAFVKK 
    QPKYLKLGAI DVERLKNTPV KSSEGSQQRS PSYTNDSTAT FIIDGMHCKS CVSNIESTLS 
    ALQYVSSIVV SLENRSAIVK YNASSVTPES LRKAIEAVSP GLYRVSITSE VESTSNSPSS 
    SSLQKIPLNV VSQPLTQETV INIDGMTCNS CVQSIEGVIS KKPGVKSIRV SLANSNGTVE 
    YDPLLTSPET LRGAIEDMGF DATLSDTNEP LVVIAQPSSE MPLLTSTNEF YTKGMTPVQD 
    KEEGKNSSKC YIQVTGMTCA SCVANIERNL RREEGIYSIL VALMAGKAEV RYNPAVIQPP 
    MIAEFIRELG FGATVIENAD EGDGVLELVV RGMTCASCVH KIESSLTKHR GILYCSVALA 
    TNKAHIKYDP EIIGPRDIIH TIESLGFEAS LVKKDRSASH LDHKREIRQW RRSFLVSLFF 
    CIPVMGLMIY MMVMDHHFAT LHHNQNMSKE EMINLHSSMF LERQILPGLS VMNLLSFLLC 
    VPVQFFGGWY FYIQAYKALK HKTANMDVLI VLATTIAFAY SLIILLVAMY ERAKVNPITF 
    FDTPPMLFVF IALGRWLEHI AKGKTSEALA KLISLQATEA TIVTLDSDNI LLSEEQVDVE 
    LVQRGDIIKV VPGGKFPVDG RVIEGHSMVD ESLITGEAMP VAKKPGSTVI AGSINQNGSL 
    LICATHVGAD TTLSQIVKLV EEAQTSKAPI QQFADKLSGY FVPFIVFVSI ATLLVWIVIG 
    FLNFEIVETY FPGYNRSISR TETIIRFAFQ ASITVLCIAC PCSLGLATPT AVMVGTGVGA 
    QNGILIKGGE PLEMAHKVKV VVFDKTGTIT HGTPVVNQVK VLTESNRISH HKILAIVGTA 
    ESNSEHPLGT AITKYCKQEL DTETLGTCID FQVVPGCGIS CKVTNIEGLL HKNNWNIEDN 
    NIKNASLVQI DASNEQSSTS SSMIIDAQIS NALNAQQYKV LIGNREWMIR NGLVINNDVN 
    DFMTEHERKG RTAVLVAVDD ELCGLIAIAD TVKPEAELAI HILKSMGLEV VLMTGDNSKT 
    ARSIASQVGI TKVFAEVLPS HKVAKVKQLQ EEGKRVAMVG DGINDSPALA MANVGIAIGT 
    GTDVAIEAAD VVLIRNDLLD VVASIDLSRK TVKRIRINFV FALIYNLVGI PIAAGVFMPI 
    GLVLQPWMGS AAMAASSVSV VLSSLFLKLY RKPTYESYEL PARSQIGQKS PSEISVHVGI 
    DDTSRNSPKL GLLDRIVNYS RASINSLLSD KRSLNSVVTS EPDKHSLLVG DFREDDDTAL

Genular Protein ID: 3897435048

Symbol: B4DRW0_HUMAN

Name: N/A

UniProtKB Accession Codes:

Database IDs:

Sequence Information:

  • Length: 488
  • Mass: 52494
  • Checksum: 372107CF0324AE75
  • Sequence:
  • MVGTGVGAQN GILIKGGEPL EMAHKVKVVV FDKTGTITHG TPVVNQVKVL TESNRISHHK 
    ILAIVGTAES NSEHPLGTAI TKYCKQELDT ETLGTCIDFQ VVPGCGISCK VTNIEGLLHK 
    NNWNIEDNNI KNASLVQIDA SNEQSSTSSS MIIDAQISNA LNAQQYKVLI GNREWMIRNG 
    LVINNDVNDF MTEHERKGRT AVLVAVDDEL CGLIAIADTV KPEAELAIHI LKSMGLEVVL 
    MTGDNSKTAR SIASQVGITK VFAEVLPSHK VAKVKQLQEE GKRVAMVGDG INDSPALAMA 
    NVGIAIGTGT DVAIEAADVV LIRNDLLDVV ASIDLSRKTV KRIRINFVFA LIYNLVGIPI 
    AAGVFMPIGL VLQPWMGSAA MAASSVSVVL SSLFLKLYRK PTYESYELPA RSQIGQKSPS 
    EISVHVGIDD TSRNSPKLGL LDRIVNYSRA SINSLLSDKR SLNSVVTSEP DKHSLLVGDF 
    REDDDTAL

Genular Protein ID: 1221986320

Symbol: Q762B6_HUMAN

Name: N/A

UniProtKB Accession Codes:

Database IDs:

Sequence Information:

  • Length: 274
  • Mass: 30124
  • Checksum: 1233AE33CD302122
  • Sequence:
  • MDPSMGVNSV TISVEGMTCN SCVWTIEQQI GKVNGVHHIK VSLEEKNATI IYDPKLQTPK 
    TLQEAIDDMG FDAVIHNPDP LPVLTDTLFL TVTASLTLPW DHIQSTLLKT KGVTDIKIYP 
    QKRTVAVTII PSIVNANQIK ELVPELSLDT GTLEKKSGAC EDHSMAQAGE VVLKMKVEGM 
    TCHSCTSTIE GKIGKLQGVQ RIKVSLDNQE ATIVYQPHLI SVEEMKKQIE AMGFPAFVKK 
    QPKYLKLGAI DVERLKNTPV KSSEGSQQRS PSYQ

Database document:

This is a preview of the gene's schema. Only a few entries are kept for 'singleCellExpressions,' 'mRNAExpressions,' and other large data arrays for visualization purposes. You can zoom in with the mouse wheel for a closer view, and the text will adjust automatically if necessary. For the full schema, download it here.