Details for: APTX

Gene ID: 54840

Symbol: APTX

Ensembl ID: ENSG00000137074

Description: aprataxin

Associated with

Other Information

Genular Protein ID: 302307883

Symbol: APTX_HUMAN

Name: Aprataxin

UniProtKB Accession Codes:

Database IDs:

Citations:

PubMed ID: 15276230

Title: Novel splice variants increase molecular diversity of aprataxin, the gene responsible for early-onset ataxia with ocular motor apraxia and hypoalbuminemia.

PubMed ID: 15276230

DOI: 10.1016/j.neulet.2004.05.034

PubMed ID: 14702039

Title: Complete sequencing and characterization of 21,243 full-length human cDNAs.

PubMed ID: 14702039

DOI: 10.1038/ng1285

PubMed ID: 17974005

Title: The full-ORF clone resource of the German cDNA consortium.

PubMed ID: 17974005

DOI: 10.1186/1471-2164-8-399

PubMed ID: 15164053

Title: DNA sequence and analysis of human chromosome 9.

PubMed ID: 15164053

DOI: 10.1038/nature02465

PubMed ID: 15489334

Title: The status, quality, and expansion of the NIH full-length cDNA project: the Mammalian Gene Collection (MGC).

PubMed ID: 15489334

DOI: 10.1101/gr.2596504

PubMed ID: 11586299

Title: Early-onset ataxia with ocular motor apraxia and hypoalbuminemia is caused by mutations in a new HIT superfamily gene.

PubMed ID: 11586299

DOI: 10.1038/ng1001-184

PubMed ID: 11586300

Title: The gene mutated in ataxia-ocular apraxia 1 encodes the new HIT/Zn-finger protein aprataxin.

PubMed ID: 11586300

DOI: 10.1038/ng1001-189

PubMed ID: 14755728

Title: Aprataxin, the causative protein for EAOH is a nuclear protein with a potential role as a DNA repair protein.

PubMed ID: 14755728

DOI: 10.1002/ana.10808

PubMed ID: 15380105

Title: The ataxia-oculomotor apraxia 1 gene product has a role distinct from ATM and interacts with the DNA strand break repair proteins XRCC1 and XRCC4.

PubMed ID: 15380105

DOI: 10.1016/j.dnarep.2004.06.017

PubMed ID: 15044383

Title: Aprataxin, a novel protein that protects against genotoxic stress.

PubMed ID: 15044383

DOI: 10.1093/hmg/ddh122

PubMed ID: 16777843

Title: Nucleolar localization of aprataxin is dependent on interaction with nucleolin and on active ribosomal DNA transcription.

PubMed ID: 16777843

DOI: 10.1093/hmg/ddl149

PubMed ID: 16547001

Title: Aprataxin forms a discrete branch in the HIT (histidine triad) superfamily of proteins with both DNA/RNA binding and nucleotide hydrolase activities.

PubMed ID: 16547001

DOI: 10.1074/jbc.m507946200

PubMed ID: 16964241

Title: The neurodegenerative disease protein aprataxin resolves abortive DNA ligation intermediates.

PubMed ID: 16964241

DOI: 10.1038/nature05164

PubMed ID: 17276982

Title: Actions of aprataxin in multiple DNA repair pathways.

PubMed ID: 17276982

DOI: 10.1074/jbc.m611489200

PubMed ID: 21406692

Title: System-wide temporal characterization of the proteome and phosphoproteome of human embryonic stem cell differentiation.

PubMed ID: 21406692

DOI: 10.1126/scisignal.2001570

PubMed ID: 24275569

Title: An enzyme assisted RP-RPLC approach for in-depth analysis of human liver phosphoproteome.

PubMed ID: 24275569

DOI: 10.1016/j.jprot.2013.11.014

PubMed ID: 20008512

Title: CK2 phosphorylation-dependent interaction between aprataxin and MDC1 in the DNA damage response.

PubMed ID: 20008512

DOI: 10.1093/nar/gkp1149

PubMed ID: 24362567

Title: Aprataxin resolves adenylated RNA-DNA junctions to maintain genome integrity.

PubMed ID: 24362567

DOI: 10.1038/nature12824

PubMed ID: 12196655

Title: Early-onset ataxia with ocular motor apraxia and hypoalbuminemia: the aprataxin gene mutations.

PubMed ID: 12196655

DOI: 10.1212/wnl.59.4.590

PubMed ID: 12629250

Title: Phenotypic variability of aprataxin gene mutations.

PubMed ID: 12629250

DOI: 10.1212/01.wnl.0000048562.88536.a4

PubMed ID: 14506070

Title: Cerebellar ataxia with oculomotor apRAxia type 1: clinical and genetic studies.

PubMed ID: 14506070

DOI: 10.1093/brain/awg283

PubMed ID: 15852392

Title: Very late onset in ataxia oculomotor apraxia type I.

PubMed ID: 15852392

DOI: 10.1002/ana.20463

PubMed ID: 15699391

Title: Coenzyme Q deficiency and cerebellar ataxia associated with an aprataxin mutation.

PubMed ID: 15699391

DOI: 10.1212/01.wnl.0000150588.75281.58

Sequence Information:

  • Length: 356
  • Mass: 40740
  • Checksum: 5B338490E35EC8E4
  • Sequence:
  • MSNVNLSVSD FWRVMMRVCW LVRQDSRHQR IRLPHLEAVV IGRGPETKIT DKKCSRQQVQ 
    LKAECNKGYV KVKQVGVNPT SIDSVVIGKD QEVKLQPGQV LHMVNELYPY IVEFEEEAKN 
    PGLETHRKRK RSGNSDSIER DAAQEAEAGT GLEPGSNSGQ CSVPLKKGKD APIKKESLGH 
    WSQGLKISMQ DPKMQVYKDE QVVVIKDKYP KARYHWLVLP WTSISSLKAV AREHLELLKH 
    MHTVGEKVIV DFAGSSKLRF RLGYHAIPSM SHVHLHVISQ DFDSPCLKNK KHWNSFNTEY 
    FLESQAVIEM VQEAGRVTVR DGMPELLKLP LRCHECQQLL PSIPQLKEHL RKHWTQ

Database document:

This is a preview of the gene's schema. Only a few entries are kept for 'singleCellExpressions,' 'mRNAExpressions,' and other large data arrays for visualization purposes. You can zoom in with the mouse wheel for a closer view, and the text will adjust automatically if necessary. For the full schema, download it here.