Details for: NGLY1

Gene ID: 55768

Symbol: NGLY1

Ensembl ID: ENSG00000151092

Description: N-glycanase 1

Associated with

Other Information

Genular Protein ID: 2113716294

Symbol: NGLY1_HUMAN

Name: Peptide-N(4)-(N-acetyl-beta-glucosaminyl)asparagine amidase

UniProtKB Accession Codes:

Database IDs:

Citations:

PubMed ID: 10831608

Title: PNG1, a yeast gene encoding a highly conserved peptide:N-glycanase.

PubMed ID: 10831608

DOI: 10.1083/jcb.149.5.1039

PubMed ID: 14702039

Title: Complete sequencing and characterization of 21,243 full-length human cDNAs.

PubMed ID: 14702039

DOI: 10.1038/ng1285

PubMed ID: 16641997

Title: The DNA sequence, annotation and analysis of human chromosome 3.

PubMed ID: 16641997

DOI: 10.1038/nature04728

PubMed ID: 15489334

Title: The status, quality, and expansion of the NIH full-length cDNA project: the Mammalian Gene Collection (MGC).

PubMed ID: 15489334

DOI: 10.1101/gr.2596504

PubMed ID: 15362974

Title: A novel UBA and UBX domain protein that binds polyubiquitin and VCP and is a substrate for SAPKs.

PubMed ID: 15362974

DOI: 10.1042/bj20041498

PubMed ID: 14749736

Title: A glycosylated type I membrane protein becomes cytosolic when peptide: N-glycanase is compromised.

PubMed ID: 14749736

DOI: 10.1038/sj.emboj.7600090

PubMed ID: 15358861

Title: A complex between peptide:N-glycanase and two proteasome-linked proteins suggests a mechanism for the degradation of misfolded glycoproteins.

PubMed ID: 15358861

DOI: 10.1073/pnas.0405663101

PubMed ID: 15610852

Title: Using a small molecule inhibitor of peptide: N-glycanase to probe its role in glycoprotein turnover.

PubMed ID: 15610852

DOI: 10.1016/j.chembiol.2004.11.010

PubMed ID: 16055502

Title: The retrotranslocation protein derlin-1 binds peptide:N-glycanase to the endoplasmic reticulum.

PubMed ID: 16055502

DOI: 10.1091/mbc.e05-04-0345

PubMed ID: 19413330

Title: Lys-N and trypsin cover complementary parts of the phosphoproteome in a refined SCX-based approach.

PubMed ID: 19413330

DOI: 10.1021/ac9004309

PubMed ID: 22581936

Title: Clinical application of exome sequencing in undiagnosed genetic conditions.

PubMed ID: 22581936

DOI: 10.1136/jmedgenet-2012-100819

PubMed ID: 23186163

Title: Toward a comprehensive characterization of a human cancer cell phosphoproteome.

PubMed ID: 23186163

DOI: 10.1021/pr300630k

PubMed ID: 24651605

Title: Mutations in NGLY1 cause an inherited disorder of the endoplasmic reticulum-associated degradation pathway.

PubMed ID: 24651605

DOI: 10.1038/gim.2014.22

PubMed ID: 16807242

Title: The PUB domain functions as a p97 binding module in human peptide N-glycanase.

PubMed ID: 16807242

DOI: 10.1074/jbc.m601173200

Sequence Information:

  • Length: 654
  • Mass: 74390
  • Checksum: 94BD44316EA66AF6
  • Sequence:
  • MAAAALGSSS GSASPAVAEL CQNTPETFLE ASKLLLTYAD NILRNPNDEK YRSIRIGNTA 
    FSTRLLPVRG AVECLFEMGF EEGETHLIFP KKASVEQLQK IRDLIAIERS SRLDGSNKSH 
    KVKSSQQPAA STQLPTTPSS NPSGLNQHTR NRQGQSSDPP SASTVAADSA ILEVLQSNIQ 
    HVLVYENPAL QEKALACIPV QELKRKSQEK LSRARKLDKG INISDEDFLL LELLHWFKEE 
    FFHWVNNVLC SKCGGQTRSR DRSLLPSDDE LKWGAKEVED HYCDACQFSN RFPRYNNPEK 
    LLETRCGRCG EWANCFTLCC RAVGFEARYV WDYTDHVWTE VYSPSQQRWL HCDACEDVCD 
    KPLLYEIGWG KKLSYVIAFS KDEVVDVTWR YSCKHEEVIA RRTKVKEALL RDTINGLNKQ 
    RQLFLSENRR KELLQRIIVE LVEFISPKTP KPGELGGRIS GSVAWRVARG EMGLQRKETL 
    FIPCENEKIS KQLHLCYNIV KDRYVRVSNN NQTISGWENG VWKMESIFRK VETDWHMVYL 
    ARKEGSSFAY ISWKFECGSV GLKVDSISIR TSSQTFQTGT VEWKLRSDTA QVELTGDNSL 
    HSYADFSGAT EVILEAELSR GDGDVAWQHT QLFRQSLNDH EENCLEIIIK FSDL

Database document:

This is a preview of the gene's schema. Only a few entries are kept for 'singleCellExpressions,' 'mRNAExpressions,' and other large data arrays for visualization purposes. You can zoom in with the mouse wheel for a closer view, and the text will adjust automatically if necessary. For the full schema, download it here.