Details for: COQ8A

Gene ID: 56997

Symbol: COQ8A

Ensembl ID: ENSG00000163050

Description: coenzyme Q8A

Associated with

Other Information

Genular Protein ID: 1850792916

Symbol: COQ8A_HUMAN

Name: N/A

UniProtKB Accession Codes:

Database IDs:

Citations:

PubMed ID: 11888884

Title: Isolation of a novel gene, CABC1, encoding a mitochondrial protein that is highly homologous to yeast activity of bc1 complex.

PubMed ID: 11888884

PubMed ID: 15498874

Title: Large-scale cDNA transfection screening for genes related to cancer development and progression.

PubMed ID: 15498874

DOI: 10.1073/pnas.0404089101

PubMed ID: 14702039

Title: Complete sequencing and characterization of 21,243 full-length human cDNAs.

PubMed ID: 14702039

DOI: 10.1038/ng1285

PubMed ID: 17974005

Title: The full-ORF clone resource of the German cDNA consortium.

PubMed ID: 17974005

DOI: 10.1186/1471-2164-8-399

PubMed ID: 16710414

Title: The DNA sequence and biological annotation of human chromosome 1.

PubMed ID: 16710414

DOI: 10.1038/nature04727

PubMed ID: 15489334

Title: The status, quality, and expansion of the NIH full-length cDNA project: the Mammalian Gene Collection (MGC).

PubMed ID: 15489334

DOI: 10.1101/gr.2596504

PubMed ID: 25498144

Title: Mitochondrial ADCK3 employs an atypical protein kinase-like fold to enable coenzyme Q biosynthesis.

PubMed ID: 25498144

DOI: 10.1016/j.molcel.2014.11.002

PubMed ID: 20580948

Title: Nonsense mutations in CABC1/ADCK3 cause progressive cerebellar ataxia and atrophy.

PubMed ID: 20580948

DOI: 10.1016/j.mito.2010.05.008

PubMed ID: 21269460

Title: Initial characterization of the human central proteome.

PubMed ID: 21269460

DOI: 10.1186/1752-0509-5-17

PubMed ID: 21296186

Title: Expression of the human atypical kinase ADCK3 rescues coenzyme Q biosynthesis and phosphorylation of Coq polypeptides in yeast coq8 mutants.

PubMed ID: 21296186

DOI: 10.1016/j.bbalip.2011.01.009

PubMed ID: 24270420

Title: ADCK4 mutations promote steroid-resistant nephrotic syndrome through CoQ10 biosynthesis disruption.

PubMed ID: 24270420

DOI: 10.1172/jci69000

PubMed ID: 25216398

Title: A Gly-zipper motif mediates homodimerization of the transmembrane domain of the mitochondrial kinase ADCK3.

PubMed ID: 25216398

DOI: 10.1021/ja505017f

PubMed ID: 24218524

Title: Autosomal-recessive cerebellar ataxia caused by a novel ADCK3 mutation that elongates the protein: clinical, genetic and biochemical characterisation.

PubMed ID: 24218524

DOI: 10.1136/jnnp-2013-306483

PubMed ID: 25540914

Title: Preparation and characterization of human ADCK3, a putative atypical kinase.

PubMed ID: 25540914

DOI: 10.1016/j.pep.2014.12.008

PubMed ID: 25944712

Title: N-terminome analysis of the human mitochondrial proteome.

PubMed ID: 25944712

DOI: 10.1002/pmic.201400617

PubMed ID: 27499294

Title: Cerebellar ataxia and coenzyme Q deficiency through loss of unorthodox kinase activity.

PubMed ID: 27499294

DOI: 10.1016/j.molcel.2016.06.030

PubMed ID: 27499296

Title: Mitochondrial protein interaction mapping identifies regulators of respiratory chain function.

PubMed ID: 27499296

DOI: 10.1016/j.molcel.2016.06.033

PubMed ID: 33988507

Title: A subcellular map of the human kinome.

PubMed ID: 33988507

DOI: 10.7554/elife.64943

PubMed ID: 17344846

Title: Patterns of somatic mutation in human cancer genomes.

PubMed ID: 17344846

DOI: 10.1038/nature05610

PubMed ID: 18319072

Title: CABC1 gene mutations cause ubiquinone deficiency with cerebellar ataxia and seizures.

PubMed ID: 18319072

DOI: 10.1016/j.ajhg.2007.12.022

PubMed ID: 18319074

Title: ADCK3, an ancestral kinase, is mutated in a form of recessive ataxia associated with coenzyme Q10 deficiency.

PubMed ID: 18319074

DOI: 10.1016/j.ajhg.2007.12.024

PubMed ID: 22036850

Title: Adult-onset cerebellar ataxia due to mutations in CABC1/ADCK3.

PubMed ID: 22036850

DOI: 10.1136/jnnp-2011-301258

PubMed ID: 24048965

Title: Heterozygous mutations in the ADCK3 gene in siblings with cerebellar atrophy and extreme phenotypic variability.

PubMed ID: 24048965

DOI: 10.1007/8904_2013_251

PubMed ID: 26818466

Title: Cerebellar ataxia and severe muscle CoQ10 deficiency in a patient with a novel mutation in ADCK3.

PubMed ID: 26818466

DOI: 10.1111/cge.12742

PubMed ID: 27106809

Title: ADCK3 mutations with epilepsy, stroke-like episodes and ataxia: a POLG mimic?

PubMed ID: 27106809

DOI: 10.1111/ene.13003

Sequence Information:

  • Length: 647
  • Mass: 71950
  • Checksum: DEF8F022027BF6CC
  • Sequence:
  • MAAILGDTIM VAKGLVKLTQ AAVETHLQHL GIGGELIMAA RALQSTAVEQ IGMFLGKVQG 
    QDKHEEYFAE NFGGPEGEFH FSVPHAAGAS TDFSSASAPD QSAPPSLGHA HSEGPAPAYV 
    ASGPFREAGF PGQASSPLGR ANGRLFANPR DSFSAMGFQR RFFHQDQSPV GGLTAEDIEK 
    ARQAKARPEN KQHKQTLSEH ARERKVPVTR IGRLANFGGL AVGLGFGALA EVAKKSLRSE 
    DPSGKKAVLG SSPFLSEANA ERIVRTLCKV RGAALKLGQM LSIQDDAFIN PHLAKIFERV 
    RQSADFMPLK QMMKTLNNDL GPNWRDKLEY FEERPFAAAS IGQVHLARMK GGREVAMKIQ 
    YPGVAQSINS DVNNLMAVLN MSNMLPEGLF PEHLIDVLRR ELALECDYQR EAACARKFRD 
    LLKGHPFFYV PEIVDELCSP HVLTTELVSG FPLDQAEGLS QEIRNEICYN ILVLCLRELF 
    EFHFMQTDPN WSNFFYDPQQ HKVALLDFGA TREYDRSFTD LYIQIIRAAA DRDRETVRAK 
    SIEMKFLTGY EVKVMEDAHL DAILILGEAF ASDEPFDFGT QSTTEKIHNL IPVMLRHRLV 
    PPPEETYSLH RKMGGSFLIC SKLKARFPCK AMFEEAYSNY CKRQAQQ

Database document:

This is a preview of the gene's schema. Only a few entries are kept for 'singleCellExpressions,' 'mRNAExpressions,' and other large data arrays for visualization purposes. You can zoom in with the mouse wheel for a closer view, and the text will adjust automatically if necessary. For the full schema, download it here.