Details for: GBA2

Gene ID: 57704

Symbol: GBA2

Ensembl ID: ENSG00000070610

Description: glucosylceramidase beta 2

Associated with

Other Information

Genular Protein ID: 2982581176

Symbol: GBA2_HUMAN

Name: Beta-glucocerebrosidase 2

UniProtKB Accession Codes:

Database IDs:

Citations:

PubMed ID: 11489889

Title: Molecular cloning and expression of human bile acid beta -glucosidase.

PubMed ID: 11489889

DOI: 10.1074/jbc.m104290200

PubMed ID: 10997877

Title: Prediction of the coding sequences of unidentified human genes. XVIII. The complete sequences of 100 new cDNA clones from brain which code for large proteins in vitro.

PubMed ID: 10997877

DOI: 10.1093/dnares/7.4.271

PubMed ID: 14702039

Title: Complete sequencing and characterization of 21,243 full-length human cDNAs.

PubMed ID: 14702039

DOI: 10.1038/ng1285

PubMed ID: 17974005

Title: The full-ORF clone resource of the German cDNA consortium.

PubMed ID: 17974005

DOI: 10.1186/1471-2164-8-399

PubMed ID: 15164053

Title: DNA sequence and analysis of human chromosome 9.

PubMed ID: 15164053

DOI: 10.1038/nature02465

PubMed ID: 15489334

Title: The status, quality, and expansion of the NIH full-length cDNA project: the Mammalian Gene Collection (MGC).

PubMed ID: 15489334

DOI: 10.1101/gr.2596504

PubMed ID: 9111029

Title: Purification and characterization of a microsomal bile acid beta-glucosidase from human liver.

PubMed ID: 9111029

DOI: 10.1074/jbc.272.17.11261

PubMed ID: 17080196

Title: Mutation of beta-glucosidase 2 causes glycolipid storage disease and impaired male fertility.

PubMed ID: 17080196

DOI: 10.1172/jci29224

PubMed ID: 17105727

Title: Identification of the non-lysosomal glucosylceramidase as beta-glucosidase 2.

PubMed ID: 17105727

DOI: 10.1074/jbc.m610544200

PubMed ID: 32144204

Title: Glucocerebrosidases catalyze a transgalactosylation reaction that yields a newly-identified brain sterol metabolite, galactosylated cholesterol.

PubMed ID: 32144204

DOI: 10.1074/jbc.ra119.012502

PubMed ID: 23332916

Title: Loss of function of glucocerebrosidase GBA2 is responsible for motor neuron defects in hereditary spastic paraplegia.

PubMed ID: 23332916

DOI: 10.1016/j.ajhg.2012.11.021

PubMed ID: 26220345

Title: Lack of enzyme activity in GBA2 mutants associated with hereditary spastic paraplegia/cerebellar ataxia (SPG46).

PubMed ID: 26220345

DOI: 10.1016/j.bbrc.2015.07.112

PubMed ID: 23332917

Title: Mutations in GBA2 cause autosomal-recessive cerebellar ataxia with spasticity.

PubMed ID: 23332917

DOI: 10.1016/j.ajhg.2012.12.012

PubMed ID: 24252062

Title: A novel GBA2 gene missense mutation in spastic ataxia.

PubMed ID: 24252062

DOI: 10.1111/ahg.12045

PubMed ID: 30308956

Title: Biochemical Characterization of the GBA2 c.1780G>C Missense Mutation in Lymphoblastoid Cells from Patients with Spastic Ataxia.

PubMed ID: 30308956

DOI: 10.3390/ijms19103099

Sequence Information:

  • Length: 927
  • Mass: 104649
  • Checksum: 1F6879D6E20A2B1D
  • Sequence:
  • MGTQDPGNMG TGVPASEQIS CAKEDPQVYC PEETGGTKDV QVTDCKSPED SRPPKETDCC 
    NPEDSGQLMV SYEGKAMGYQ VPPFGWRICL AHEFTEKRKP FQANNVSLSN MIKHIGMGLR 
    YLQWWYRKTH VEKKTPFIDM INSVPLRQIY GCPLGGIGGG TITRGWRGQF CRWQLNPGMY 
    QHRTVIADQF TVCLRREGQT VYQQVLSLER PSVLRSWNWG LCGYFAFYHA LYPRAWTVYQ 
    LPGQNVTLTC RQITPILPHD YQDSSLPVGV FVWDVENEGD EALDVSIMFS MRNGLGGGDD 
    APGGLWNEPF CLERSGETVR GLLLHHPTLP NPYTMAVAAR VTAATTVTHI TAFDPDSTGQ 
    QVWQDLLQDG QLDSPTGQST PTQKGVGIAG AVCVSSKLRP RGQCRLEFSL AWDMPRIMFG 
    AKGQVHYRRY TRFFGQDGDA APALSHYALC RYAEWEERIS AWQSPVLDDR SLPAWYKSAL 
    FNELYFLADG GTVWLEVLED SLPEELGRNM CHLRPTLRDY GRFGYLEGQE YRMYNTYDVH 
    FYASFALIML WPKLELSLQY DMALATLRED LTRRRYLMSG VMAPVKRRNV IPHDIGDPDD 
    EPWLRVNAYL IHDTADWKDL NLKFVLQVYR DYYLTGDQNF LKDMWPVCLA VMESEMKFDK 
    DHDGLIENGG YADQTYDGWV TTGPSAYCGG LWLAAVAVMV QMAALCGAQD IQDKFSSILS 
    RGQEAYERLL WNGRYYNYDS SSRPQSRSVM SDQCAGQWFL KACGLGEGDT EVFPTQHVVR 
    ALQTIFELNV QAFAGGAMGA VNGMQPHGVP DKSSVQSDEV WVGVVYGLAA TMIQEGLTWE 
    GFQTAEGCYR TVWERLGLAF QTPEAYCQQR VFRSLAYMRP LSIWAMQLAL QQQQHKKASW 
    PKVKQGTGLR TGPMFGPKEA MANLSPE

Database document:

This is a preview of the gene's schema. Only a few entries are kept for 'singleCellExpressions,' 'mRNAExpressions,' and other large data arrays for visualization purposes. You can zoom in with the mouse wheel for a closer view, and the text will adjust automatically if necessary. For the full schema, download it here.