Details for: IFIH1

Gene ID: 64135

Symbol: IFIH1

Ensembl ID: ENSG00000115267

Description: interferon induced with helicase C domain 1

Associated with

Other Information

Genular Protein ID: 1885550912

Symbol: IFIH1_HUMAN

Name: Clinically amyopathic dermatomyositis autoantigen 140 kDa

UniProtKB Accession Codes:

Database IDs:

Citations:

PubMed ID: 11805321

Title: mda-5: an interferon-inducible putative RNA helicase with double-stranded RNA-dependent ATPase activity and melanoma growth-suppressive properties.

PubMed ID: 11805321

DOI: 10.1073/pnas.022637199

PubMed ID: 14645903

Title: A novel cellular RNA helicase, RH116, differentially regulates cell growth, programmed cell death and human immunodeficiency virus type 1 replication.

PubMed ID: 14645903

DOI: 10.1099/vir.0.19300-0

PubMed ID: 15489334

Title: The status, quality, and expansion of the NIH full-length cDNA project: the Mammalian Gene Collection (MGC).

PubMed ID: 15489334

DOI: 10.1101/gr.2596504

PubMed ID: 14702039

Title: Complete sequencing and characterization of 21,243 full-length human cDNAs.

PubMed ID: 14702039

DOI: 10.1038/ng1285

PubMed ID: 12015121

Title: Overexpression of Helicard, a CARD-containing helicase cleaved during apoptosis, accelerates DNA degradation.

PubMed ID: 12015121

DOI: 10.1016/s0960-9822(02)00842-4

PubMed ID: 15563593

Title: The V proteins of paramyxoviruses bind the IFN-inducible RNA helicase, mda-5, and inhibit its activation of the IFN-beta promoter.

PubMed ID: 15563593

DOI: 10.1073/pnas.0407639101

PubMed ID: 16127453

Title: IPS-1, an adaptor triggering RIG-I- and Mda5-mediated type I interferon induction.

PubMed ID: 16127453

DOI: 10.1038/ni1243

PubMed ID: 16177806

Title: Cardif is an adaptor protein in the RIG-I antiviral pathway and is targeted by hepatitis C virus.

PubMed ID: 16177806

DOI: 10.1038/nature04193

PubMed ID: 17460044

Title: Negative regulation of the RIG-I signaling by the ubiquitin ligase RNF125.

PubMed ID: 17460044

DOI: 10.1073/pnas.0611551104

PubMed ID: 17600090

Title: Negative regulation of MDA5- but not RIG-I-mediated innate antiviral signaling by the dihydroxyacetone kinase.

PubMed ID: 17600090

DOI: 10.1073/pnas.0700544104

PubMed ID: 17709747

Title: The Atg5-Atg12 conjugate associates with innate antiviral immune responses.

PubMed ID: 17709747

DOI: 10.1073/pnas.0704014104

PubMed ID: 19565506

Title: RNA helicase encoded by melanoma differentiation-associated gene 5 is a major autoantigen in patients with clinically amyopathic dermatomyositis: Association with rapidly progressive interstitial lung disease.

PubMed ID: 19565506

DOI: 10.1002/art.24621

PubMed ID: 19211564

Title: Regulation of signal transduction by enzymatically inactive antiviral RNA helicase proteins MDA5, RIG-I, and LGP2.

PubMed ID: 19211564

DOI: 10.1074/jbc.m807365200

PubMed ID: 19656871

Title: Activation of MDA5 requires higher-order RNA structures generated during virus infection.

PubMed ID: 19656871

DOI: 10.1128/jvi.00770-09

PubMed ID: 19881509

Title: PCBP2 mediates degradation of the adaptor MAVS via the HECT ubiquitin ligase AIP4.

PubMed ID: 19881509

DOI: 10.1038/ni.1815

PubMed ID: 20434986

Title: NLRC5 negatively regulates the NF-kappaB and type I interferon signaling pathways.

PubMed ID: 20434986

DOI: 10.1016/j.cell.2010.03.040

PubMed ID: 20368735

Title: The ubiquitin-specific protease 17 is involved in virus-triggered type I IFN signaling.

PubMed ID: 20368735

DOI: 10.1038/cr.2010.41

PubMed ID: 20127681

Title: DEAD/H BOX 3 (DDX3) helicase binds the RIG-I adaptor IPS-1 to up-regulate IFN-beta-inducing potential.

PubMed ID: 20127681

DOI: 10.1002/eji.200940203

PubMed ID: 20015976

Title: The RIG-I-like receptor IFIH1/MDA5 is a dermatomyositis-specific autoantigen identified by the anti-CADM-140 antibody.

PubMed ID: 20015976

DOI: 10.1093/rheumatology/kep375

PubMed ID: 20068231

Title: Quantitative phosphoproteomics reveals widespread full phosphorylation site occupancy during mitosis.

PubMed ID: 20068231

DOI: 10.1126/scisignal.2000475

PubMed ID: 21269460

Title: Initial characterization of the human central proteome.

PubMed ID: 21269460

DOI: 10.1186/1752-0509-5-17

PubMed ID: 21616437

Title: Immune signaling by RIG-I-like receptors.

PubMed ID: 21616437

DOI: 10.1016/j.immuni.2011.05.003

PubMed ID: 21884169

Title: RIG-I-like receptors: cytoplasmic sensors for non-self RNA.

PubMed ID: 21884169

DOI: 10.1111/j.1600-065x.2011.01052.x

PubMed ID: 21742966

Title: Innate immune responses in human monocyte-derived dendritic cells are highly dependent on the size and the 5' phosphorylation of RNA molecules.

PubMed ID: 21742966

DOI: 10.4049/jimmunol.1100361

PubMed ID: 20950133

Title: Retinoic acid-inducible gene-I-like receptors.

PubMed ID: 20950133

DOI: 10.1089/jir.2010.0057

PubMed ID: 21791617

Title: DDX60, a DEXD/H box helicase, is a novel antiviral factor promoting RIG-I-like receptor-mediated signaling.

PubMed ID: 21791617

DOI: 10.1128/mcb.01368-10

PubMed ID: 21156324

Title: MDA5 is SUMOylated by PIAS2? in the upregulation of type I interferon signaling.

PubMed ID: 21156324

DOI: 10.1016/j.molimm.2010.09.003

PubMed ID: 21245900

Title: 2 methylate or not 2 methylate: viral evasion of the type I interferon response.

PubMed ID: 21245900

DOI: 10.1038/ni0211-114

PubMed ID: 21217758

Title: Ribose 2'-O-methylation provides a molecular signature for the distinction of self and non-self mRNA dependent on the RNA sensor Mda5.

PubMed ID: 21217758

DOI: 10.1038/ni.1979

PubMed ID: 22160685

Title: Cooperative assembly and dynamic disassembly of MDA5 filaments for viral dsRNA recognition.

PubMed ID: 22160685

DOI: 10.1073/pnas.1113651108

PubMed ID: 22301138

Title: Herpes simplex virus 1 tegument protein US11 downmodulates the RLR signaling pathway via direct interaction with RIG-I and MDA-5.

PubMed ID: 22301138

DOI: 10.1128/jvi.06713-11

PubMed ID: 23711367

Title: A role for the Ankyrin repeat containing protein Ankrd17 in Nod1- and Nod2-mediated inflammatory responses.

PubMed ID: 23711367

DOI: 10.1016/j.febslet.2013.05.037

PubMed ID: 24275569

Title: An enzyme assisted RP-RPLC approach for in-depth analysis of human liver phosphoproteome.

PubMed ID: 24275569

DOI: 10.1016/j.jprot.2013.11.014

PubMed ID: 24390337

Title: Enterovirus 2Apro targets MDA5 and MAVS in infected cells.

PubMed ID: 24390337

DOI: 10.1128/jvi.02712-13

PubMed ID: 25865883

Title: RIOK3-mediated phosphorylation of MDA5 interferes with its assembly and attenuates the innate immune response.

PubMed ID: 25865883

DOI: 10.1016/j.celrep.2015.03.027

PubMed ID: 25228397

Title: ECSIT bridges RIG-I-like receptors to VISA in signaling events of innate antiviral responses.

PubMed ID: 25228397

DOI: 10.1159/000365971

PubMed ID: 27312109

Title: RNF123 has an E3 ligase-independent function in RIG-I-like receptor-mediated antiviral signaling.

PubMed ID: 27312109

DOI: 10.15252/embr.201541703

PubMed ID: 28424289

Title: Disruption of MDA5-Mediated Innate Immune Responses by the 3C Proteins of Coxsackievirus A16, Coxsackievirus A6, and Enterovirus D68.

PubMed ID: 28424289

DOI: 10.1128/jvi.00546-17

PubMed ID: 29117565

Title: The E3 Ubiquitin Ligase TRIM40 Attenuates Antiviral Immune Responses by Targeting MDA5 and RIG-I.

PubMed ID: 29117565

DOI: 10.1016/j.celrep.2017.10.020

PubMed ID: 28594402

Title: ARRDC4 regulates enterovirus 71-induced innate immune response by promoting K63 polyubiquitination of MDA5 through TRIM65.

PubMed ID: 28594402

DOI: 10.1038/cddis.2017.257

PubMed ID: 30312637

Title: Encephalomyocarditis virus 2C protein antagonizes interferon-beta signaling pathway through interaction with MDA5.

PubMed ID: 30312637

DOI: 10.1016/j.antiviral.2018.10.010

PubMed ID: 30193849

Title: The zinc-finger protein ZCCHC3 binds RNA and facilitates viral RNA sensing and activation of the RIG-I-like receptors.

PubMed ID: 30193849

DOI: 10.1016/j.immuni.2018.08.014

PubMed ID: 32169843

Title: NOD1 Promotes Antiviral Signaling by Binding Viral RNA and Regulating the Interaction of MDA5 and MAVS.

PubMed ID: 32169843

DOI: 10.4049/jimmunol.1900667

PubMed ID: 33440148

Title: MDA5 Governs the Innate Immune Response to SARS-CoV-2 in Lung Epithelial Cells.

PubMed ID: 33440148

DOI: 10.1016/j.celrep.2020.108628

PubMed ID: 33514628

Title: SARS-CoV-2 triggers an MDA-5-dependent interferon response which is unable to control replication in lung epithelial cells.

PubMed ID: 33514628

DOI: 10.1128/jvi.02415-20

PubMed ID: 33727702

Title: ISG15-dependent activation of the sensor MDA5 is antagonized by the SARS-CoV-2 papain-like protease to evade host innate immunity.

PubMed ID: 33727702

DOI: 10.1038/s41564-021-00884-1

PubMed ID: 19531363

Title: Structural basis of double-stranded RNA recognition by the RIG-I like receptor MDA5.

PubMed ID: 19531363

DOI: 10.1016/j.abb.2009.06.008

PubMed ID: 19380577

Title: Solution structures of cytosolic RNA sensor MDA5 and LGP2 C-terminal domains: identification of the RNA recognition loop in RIG-I-like receptors.

PubMed ID: 19380577

DOI: 10.1074/jbc.m109.007179

PubMed ID: 16699517

Title: A genome-wide association study of nonsynonymous SNPs identifies a type 1 diabetes locus in the interferon-induced helicase (IFIH1) region.

PubMed ID: 16699517

DOI: 10.1038/ng1800

PubMed ID: 24995871

Title: Aicardi-Goutieres syndrome is caused by IFIH1 mutations.

PubMed ID: 24995871

DOI: 10.1016/j.ajhg.2014.06.007

PubMed ID: 24686847

Title: Gain-of-function mutations in IFIH1 cause a spectrum of human disease phenotypes associated with upregulated type I interferon signaling.

PubMed ID: 24686847

DOI: 10.1038/ng.2933

PubMed ID: 25620204

Title: A specific IFIH1 gain-of-function mutation causes Singleton-Merten syndrome.

PubMed ID: 25620204

DOI: 10.1016/j.ajhg.2014.12.014

PubMed ID: 28606988

Title: Recurrent rhinovirus infections in a child with inherited MDA5 deficiency.

PubMed ID: 28606988

DOI: 10.1084/jem.20161759

PubMed ID: 29018476

Title: Recurrent and prolonged infections in a child with a homozygous IFIH1 nonsense mutation.

PubMed ID: 29018476

DOI: 10.3389/fgene.2017.00130

Sequence Information:

  • Length: 1025
  • Mass: 116689
  • Checksum: 789CFB4824B92DC9
  • Sequence:
  • MSNGYSTDEN FRYLISCFRA RVKMYIQVEP VLDYLTFLPA EVKEQIQRTV ATSGNMQAVE 
    LLLSTLEKGV WHLGWTREFV EALRRTGSPL AARYMNPELT DLPSPSFENA HDEYLQLLNL 
    LQPTLVDKLL VRDVLDKCME EELLTIEDRN RIAAAENNGN ESGVRELLKR IVQKENWFSA 
    FLNVLRQTGN NELVQELTGS DCSESNAEIE NLSQVDGPQV EEQLLSTTVQ PNLEKEVWGM 
    ENNSSESSFA DSSVVSESDT SLAEGSVSCL DESLGHNSNM GSDSGTMGSD SDEENVAARA 
    SPEPELQLRP YQMEVAQPAL EGKNIIICLP TGSGKTRVAV YIAKDHLDKK KKASEPGKVI 
    VLVNKVLLVE QLFRKEFQPF LKKWYRVIGL SGDTQLKISF PEVVKSCDII ISTAQILENS 
    LLNLENGEDA GVQLSDFSLI IIDECHHTNK EAVYNNIMRH YLMQKLKNNR LKKENKPVIP 
    LPQILGLTAS PGVGGATKQA KAEEHILKLC ANLDAFTIKT VKENLDQLKN QIQEPCKKFA 
    IADATREDPF KEKLLEIMTR IQTYCQMSPM SDFGTQPYEQ WAIQMEKKAA KEGNRKERVC 
    AEHLRKYNEA LQINDTIRMI DAYTHLETFY NEEKDKKFAV IEDDSDEGGD DEYCDGDEDE 
    DDLKKPLKLD ETDRFLMTLF FENNKMLKRL AENPEYENEK LTKLRNTIME QYTRTEESAR 
    GIIFTKTRQS AYALSQWITE NEKFAEVGVK AHHLIGAGHS SEFKPMTQNE QKEVISKFRT 
    GKINLLIATT VAEEGLDIKE CNIVIRYGLV TNEIAMVQAR GRARADESTY VLVAHSGSGV 
    IEHETVNDFR EKMMYKAIHC VQNMKPEEYA HKILELQMQS IMEKKMKTKR NIAKHYKNNP 
    SLITFLCKNC SVLACSGEDI HVIEKMHHVN MTPEFKELYI VRENKALQKK CADYQINGEI 
    ICKCGQAWGT MMVHKGLDLP CLKIRNFVVV FKNNSTKKQY KKWVELPITF PNLDYSECCL 
    FSDED

Database document:

This is a preview of the gene's schema. Only a few entries are kept for 'singleCellExpressions,' 'mRNAExpressions,' and other large data arrays for visualization purposes. You can zoom in with the mouse wheel for a closer view, and the text will adjust automatically if necessary. For the full schema, download it here.