Details for: SERPING1

Gene ID: 710

Symbol: SERPING1

Ensembl ID: ENSG00000149131

Description: serpin family G member 1

Associated with

Other Information

Genular Protein ID: 2444783558

Symbol: IC1_HUMAN

Name: Plasma protease C1 inhibitor

UniProtKB Accession Codes:

Database IDs:

Citations:

PubMed ID: 3488058

Title: Isolation and analysis of a cDNA coding for human C1 inhibitor.

PubMed ID: 3488058

DOI: 10.1016/0006-291x(86)91123-x

PubMed ID: 3756141

Title: Human C1 inhibitor: primary structure, cDNA cloning, and chromosomal localization.

PubMed ID: 3756141

DOI: 10.1021/bi00363a018

PubMed ID: 3267220

Title: Genomic and cDNA cloning of the human C1 inhibitor. Intron-exon junctions and comparison with other serpins.

PubMed ID: 3267220

DOI: 10.1111/j.1432-1033.1988.tb13980.x

PubMed ID: 2026152

Title: Complete nucleotide sequence of the gene for human C1 inhibitor with an unusually high density of Alu elements.

PubMed ID: 2026152

DOI: 10.1111/j.1432-1033.1991.tb15911.x

PubMed ID: 14702039

Title: Complete sequencing and characterization of 21,243 full-length human cDNAs.

PubMed ID: 14702039

DOI: 10.1038/ng1285

PubMed ID: 16554811

Title: Human chromosome 11 DNA sequence and analysis including novel gene identification.

PubMed ID: 16554811

DOI: 10.1038/nature04632

PubMed ID: 15489334

Title: The status, quality, and expansion of the NIH full-length cDNA project: the Mammalian Gene Collection (MGC).

PubMed ID: 15489334

DOI: 10.1101/gr.2596504

PubMed ID: 3393514

Title: Molecular cloning of the cDNA coding for human C1 inhibitor.

PubMed ID: 3393514

PubMed ID: 12773530

Title: The functional integrity of the serpin domain of C1-inhibitor depends on the unique N-terminal domain, as revealed by a pathological mutant.

PubMed ID: 12773530

DOI: 10.1074/jbc.m302977200

PubMed ID: 6416294

Title: Human C1 inhibitor: improved isolation and preliminary structural characterization.

PubMed ID: 6416294

DOI: 10.1021/bi00290a019

PubMed ID: 2154751

Title: Clusters of intragenic Alu repeats predispose the human C1 inhibitor locus to deleterious rearrangements.

PubMed ID: 2154751

DOI: 10.1073/pnas.87.4.1551

PubMed ID: 3089875

Title: Molecular cloning of human C1 inhibitor: sequence homologies with alpha 1-antitrypsin and other members of the serpins superfamily.

PubMed ID: 3089875

DOI: 10.1016/0378-1119(86)90230-1

PubMed ID: 8618290

Title: Molecular weights and isoelectric points of sperm antigens relevant to autoimmune infertility in men.

PubMed ID: 8618290

DOI: 10.1097/00005392-199606000-00030

PubMed ID: 3458172

Title: Human inhibitor of the first component of complement, C1: characterization of cDNA clones and localization of the gene to chromosome 11.

PubMed ID: 3458172

DOI: 10.1073/pnas.83.10.3161

PubMed ID: 7814636

Title: Crucial residues in the carboxy-terminal end of C1 inhibitor revealed by pathogenic mutants impaired in secretion or function.

PubMed ID: 7814636

DOI: 10.1172/jci117663

PubMed ID: 8495195

Title: Chymotrypsin inhibitory activity of normal C1-inhibitor and a P1 Arg to His mutant: evidence for the presence of overlapping reactive centers.

PubMed ID: 8495195

DOI: 10.1002/pro.5560020504

PubMed ID: 10946292

Title: Proteolytic activities of two types of mannose-binding lectin-associated serine protease.

PubMed ID: 10946292

DOI: 10.4049/jimmunol.165.5.2637

PubMed ID: 12123444

Title: StcE, a metalloprotease secreted by Escherichia coli O157:H7, specifically cleaves C1 esterase inhibitor.

PubMed ID: 12123444

DOI: 10.1046/j.1365-2958.2002.02997.x

PubMed ID: 12754519

Title: Identification and quantification of N-linked glycoproteins using hydrazide chemistry, stable isotope labeling and mass spectrometry.

PubMed ID: 12754519

DOI: 10.1038/nbt827

PubMed ID: 15096536

Title: Potentiation of C1 esterase inhibitor by StcE, a metalloprotease secreted by Escherichia coli O157:H7.

PubMed ID: 15096536

DOI: 10.1084/jem.20030255

PubMed ID: 14760718

Title: Screening for N-glycosylated proteins by liquid chromatography mass spectrometry.

PubMed ID: 14760718

DOI: 10.1002/pmic.200300556

PubMed ID: 16040958

Title: N-linked glycosylation at Asn3 and the positively charged residues within the amino-terminal domain of the c1 inhibitor are required for interaction of the C1 Inhibitor with Salmonella enterica serovar typhimurium lipopolysaccharide and lipid A.

PubMed ID: 16040958

DOI: 10.1128/iai.73.8.4478-4487.2005

PubMed ID: 16335952

Title: Human plasma N-glycoproteome analysis by immunoaffinity subtraction, hydrazide chemistry, and mass spectrometry.

PubMed ID: 16335952

DOI: 10.1021/pr0502065

PubMed ID: 19159218

Title: Glycoproteomics analysis of human liver tissue by combination of multiple enzyme digestion and hydrazide chemistry.

PubMed ID: 19159218

DOI: 10.1021/pr8008012

PubMed ID: 19139490

Title: A strategy for precise and large scale identification of core fucosylated glycoproteins.

PubMed ID: 19139490

DOI: 10.1074/mcp.m800504-mcp200

PubMed ID: 19838169

Title: Enrichment of glycopeptides for glycan structure and attachment site identification.

PubMed ID: 19838169

DOI: 10.1038/nmeth.1392

PubMed ID: 22171320

Title: Human urinary glycoproteomics; attachment site specific analysis of N- and O-linked glycosylations by CID and ECD.

PubMed ID: 22171320

DOI: 10.1074/mcp.m111.013649

PubMed ID: 23234360

Title: LC-MS/MS characterization of O-glycosylation sites and glycan structures of human cerebrospinal fluid glycoproteins.

PubMed ID: 23234360

DOI: 10.1021/pr300963h

PubMed ID: 24275569

Title: An enzyme assisted RP-RPLC approach for in-depth analysis of human liver phosphoproteome.

PubMed ID: 24275569

DOI: 10.1016/j.jprot.2013.11.014

PubMed ID: 17488724

Title: C1 inhibitor serpin domain structure reveals the likely mechanism of heparin potentiation and conformational disease.

PubMed ID: 17488724

DOI: 10.1074/jbc.m700841200

PubMed ID: 7749926

Title: What do dysfunctional serpins tell us about molecular mobility and disease?

PubMed ID: 7749926

DOI: 10.1038/nsb0295-96

PubMed ID: 3178731

Title: Dysfunctional C1-inhibitor(At), isolated from a type II hereditary-angio-oedema plasma, contains a P1 'reactive centre' (Arg444-->His) mutation.

PubMed ID: 3178731

DOI: 10.1042/bj2530615

PubMed ID: 2365061

Title: Identification of a new P1 residue mutation (444Arg-->Ser) in a dysfunctional C1 inhibitor protein contained in a type II hereditary angioedema plasma.

PubMed ID: 2365061

DOI: 10.1016/0014-5793(90)81494-9

PubMed ID: 2296585

Title: Type II hereditary angioneurotic edema that may result from a single nucleotide change in the codon for alanine-436 in the C1 inhibitor gene.

PubMed ID: 2296585

DOI: 10.1073/pnas.87.1.265

PubMed ID: 2118657

Title: Dysfunctional C1 inhibitor Ta: deletion of Lys-251 results in acquisition of an N-glycosylation site.

PubMed ID: 2118657

DOI: 10.1073/pnas.87.17.6786

PubMed ID: 1451784

Title: A dysfunctional C1 inhibitor protein with a new reactive center mutation (Arg-444-->Leu).

PubMed ID: 1451784

DOI: 10.1016/0014-5793(92)80204-t

PubMed ID: 1363816

Title: C1 inhibitor hinge region mutations produce dysfunction by different mechanisms.

PubMed ID: 1363816

DOI: 10.1038/ng0892-354

PubMed ID: 8172583

Title: Mutations in the C1 inhibitor gene that result in hereditary angioneurotic edema.

PubMed ID: 8172583

PubMed ID: 7883978

Title: Unique C1 inhibitor dysfunction in a kindred without angioedema. II. Identification of an Ala443-->Val substitution and functional analysis of the recombinant mutant protein.

PubMed ID: 7883978

DOI: 10.1172/jci117780

PubMed ID: 8529136

Title: A mutation unique in serine protease inhibitors (serpins) identified in a family with type II hereditary angioneurotic edema.

PubMed ID: 8529136

DOI: 10.1007/bf03401610

PubMed ID: 8755917

Title: Exhaustive mutation scanning by fluorescence-assisted mismatch analysis discloses new genotype-phenotype correlations in angiodema.

PubMed ID: 8755917

PubMed ID: 14635117

Title: Mutation screening of the C1 inhibitor gene among Hungarian patients with hereditary angioedema.

PubMed ID: 14635117

DOI: 10.1002/humu.9202

PubMed ID: 16409206

Title: Normal C1 inhibitor mRNA expression level in type I hereditary angioedema patients: newly found C1 inhibitor gene mutations.

PubMed ID: 16409206

DOI: 10.1111/j.1398-9995.2006.01010.x

PubMed ID: 22994404

Title: Mutational spectrum and geno-phenotype correlation in Chinese families with Hereditary Angioedema.

PubMed ID: 22994404

DOI: 10.1111/all.12024

PubMed ID: 24456027

Title: Mutational spectrum of the c1 inhibitor gene in a cohort of Italian patients with hereditary angioedema: description of nine novel mutations.

PubMed ID: 24456027

DOI: 10.1111/ahg.12052

Sequence Information:

  • Length: 500
  • Mass: 55154
  • Checksum: 8B5E874833EA6C05
  • Sequence:
  • MASRLTLLTL LLLLLAGDRA SSNPNATSSS SQDPESLQDR GEGKVATTVI SKMLFVEPIL 
    EVSSLPTTNS TTNSATKITA NTTDEPTTQP TTEPTTQPTI QPTQPTTQLP TDSPTQPTTG 
    SFCPGPVTLC SDLESHSTEA VLGDALVDFS LKLYHAFSAM KKVETNMAFS PFSIASLLTQ 
    VLLGAGENTK TNLESILSYP KDFTCVHQAL KGFTTKGVTS VSQIFHSPDL AIRDTFVNAS 
    RTLYSSSPRV LSNNSDANLE LINTWVAKNT NNKISRLLDS LPSDTRLVLL NAIYLSAKWK 
    TTFDPKKTRM EPFHFKNSVI KVPMMNSKKY PVAHFIDQTL KAKVGQLQLS HNLSLVILVP 
    QNLKHRLEDM EQALSPSVFK AIMEKLEMSK FQPTLLTLPR IKVTTSQDML SIMEKLEFFD 
    FSYDLNLCGL TEDPDLQVSA MQHQTVLELT ETGVEAAAAS AISVARTLLV FEVQQPFLFV 
    LWDQQHKFPV FMGRVYDPRA

Database document:

This is a preview of the gene's schema. Only a few entries are kept for 'singleCellExpressions,' 'mRNAExpressions,' and other large data arrays for visualization purposes. You can zoom in with the mouse wheel for a closer view, and the text will adjust automatically if necessary. For the full schema, download it here.