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Array

Raw Database JSON for Gene ID: 5161

{
    "geneID": 5161,
    "tax": {
        "id": 9606,
        "name": [
            {
                "name": "Homo sapiens Linnaeus 1758"
            },
            {
                "name": "Homo sapiens",
                "type": 0
            },
            {
                "name": "human",
                "type": 4
            }
        ]
    },
    "accession": {
        "gene": [
            "AC093828.3"
        ]
    },
    "genePos": {
        "start": 95840093,
        "end": 95841464
    },
    "orientation": true,
    "symbol": "PDHA2",
    "created": {
        "$date": {
            "$numberLong": "1738333349058"
        }
    },
    "crossReference": {
        "enseGeneID": "ENSG00000163114",
        "enseRnaID": [
            "ENST00000295266.6"
        ],
        "enseProtID": [
            "ENSP00000295266.4"
        ]
    },
    "chrom": {
        "pos": "4",
        "type": 1,
        "loc": "4q22.3"
    },
    "desc": "pyruvate dehydrogenase E1 subunit alpha 2",
    "geneType": 5,
    "mim": [
        {
            "id": 179061,
            "relation": 0
        }
    ],
    "ontology": [
        {
            "id": "R-HSA-1430728",
            "term": "Metabolism",
            "cat": 10
        },
        {
            "id": "R-HSA-162582",
            "term": "Signal Transduction",
            "cat": 10
        },
        {
            "id": "R-HSA-1428517",
            "term": "Aerobic respiration and respiratory electron transport",
            "cat": 11
        },
        {
            "id": "R-HSA-9006931",
            "term": "Signaling by Nuclear Receptors",
            "cat": 11
        },
        {
            "id": "R-HSA-5362517",
            "term": "Signaling by Retinoic Acid",
            "cat": 12
        },
        {
            "id": "R-HSA-70268",
            "term": "Pyruvate metabolism",
            "cat": 12
        },
        {
            "id": "R-HSA-9861559",
            "term": "PDH complex synthesizes acetyl-CoA from PYR",
            "cat": 13
        },
        {
            "id": "R-HSA-9861718",
            "term": "Regulation of pyruvate metabolism",
            "cat": 13
        },
        {
            "id": "R-HSA-204174",
            "term": "Regulation of pyruvate dehydrogenase (PDH) complex",
            "cat": 14
        },
        {
            "id": "GO:0004739",
            "term": "pyruvate dehydrogenase (acetyl-transferring) activity",
            "cat": 0
        },
        {
            "id": "GO:0004739",
            "term": "pyruvate dehydrogenase (acetyl-transferring) activity",
            "pubMed": [
                16436377
            ],
            "cat": 0
        },
        {
            "id": "GO:0005515",
            "term": "protein binding",
            "pubMed": [
                32296183
            ],
            "cat": 0
        },
        {
            "id": "GO:0034604",
            "term": "pyruvate dehydrogenase (NAD+) activity",
            "pubMed": [
                16436377
            ],
            "cat": 0
        },
        {
            "id": "GO:0046872",
            "term": "metal ion binding",
            "cat": 0
        },
        {
            "id": "GO:0006006",
            "term": "glucose metabolic process",
            "cat": 1
        },
        {
            "id": "GO:0006086",
            "term": "acetyl-CoA biosynthetic process from pyruvate",
            "cat": 1
        },
        {
            "id": "GO:0006086",
            "term": "acetyl-CoA biosynthetic process from pyruvate",
            "pubMed": [
                16436377
            ],
            "cat": 1
        },
        {
            "id": "GO:0006090",
            "term": "pyruvate metabolic process",
            "pubMed": [
                16436377
            ],
            "cat": 1
        },
        {
            "id": "GO:0006099",
            "term": "tricarboxylic acid cycle",
            "cat": 1
        },
        {
            "id": "GO:0005634",
            "term": "nucleus",
            "pubMed": [
                21630459
            ],
            "cat": 2
        },
        {
            "id": "GO:0005730",
            "term": "nucleolus",
            "cat": 2
        },
        {
            "id": "GO:0005739",
            "term": "mitochondrion",
            "pubMed": [
                34800366
            ],
            "cat": 2
        },
        {
            "id": "GO:0005739",
            "term": "mitochondrion",
            "cat": 2
        },
        {
            "id": "GO:0005739",
            "term": "mitochondrion",
            "pubMed": [
                24534072
            ],
            "cat": 2
        },
        {
            "id": "GO:0005759",
            "term": "mitochondrial matrix",
            "cat": 2
        },
        {
            "id": "GO:0045254",
            "term": "pyruvate dehydrogenase complex",
            "cat": 2
        }
    ],
    "protein": [
        {
            "symbol": "ODPAT_HUMAN",
            "name": "Pyruvate dehydrogenase E1 component subunit alpha, testis-specific form, mitochondrial",
            "accession": [
                "P29803",
                "B2R9Q3",
                "Q0VDI5",
                "Q4VC02",
                "Q6NXQ1"
            ],
            "databaseIDs": {
                "NCBI Taxonomy": [
                    "9606"
                ],
                "Rhea": [
                    "RHEA:19189",
                    "RHEA-COMP:10480",
                    "RHEA-COMP:10481"
                ],
                "ChEBI": [
                    "CHEBI:15361",
                    "CHEBI:15378",
                    "CHEBI:16526",
                    "CHEBI:83099",
                    "CHEBI:83111",
                    "CHEBI:58937",
                    "CHEBI:18420",
                    "CHEBI:15361",
                    "CHEBI:15361",
                    "CHEBI:58937",
                    "CHEBI:15361",
                    "CHEBI:58937",
                    "CHEBI:15361",
                    "CHEBI:58937",
                    "CHEBI:15361",
                    "CHEBI:58937",
                    "CHEBI:18420",
                    "CHEBI:15361",
                    "CHEBI:58937",
                    "CHEBI:15361",
                    "CHEBI:58937",
                    "CHEBI:15361",
                    "CHEBI:58937",
                    "CHEBI:18420",
                    "CHEBI:15361",
                    "CHEBI:58937",
                    "CHEBI:18420",
                    "CHEBI:15361",
                    "CHEBI:58937"
                ],
                "EC": [
                    "1.2.4.1",
                    "1.2.4.1"
                ],
                "MIM": [
                    "619828",
                    "179061",
                    "619828"
                ],
                "EMBL": [
                    "M86808",
                    "AK313872",
                    "BC030697",
                    "BC066953",
                    "BC094760",
                    "BC119656",
                    "BC119657",
                    "BC127637",
                    "BC127638"
                ],
                "CCDS": [
                    "CCDS3644.1"
                ],
                "PIR": [
                    "A37104"
                ],
                "RefSeq": [
                    "NP_005381.1"
                ],
                "AlphaFoldDB": [
                    "P29803"
                ],
                "SMR": [
                    "P29803"
                ],
                "BioGRID": [
                    "111187"
                ],
                "ComplexPortal": [
                    "CPX-6242"
                ],
                "IntAct": [
                    "P29803"
                ],
                "MINT": [
                    "P29803"
                ],
                "STRING": [
                    "9606.ENSP00000295266"
                ],
                "DrugBank": [
                    "DB00157"
                ],
                "iPTMnet": [
                    "P29803"
                ],
                "PhosphoSitePlus": [
                    "P29803"
                ],
                "BioMuta": [
                    "PDHA2"
                ],
                "jPOST": [
                    "P29803"
                ],
                "MassIVE": [
                    "P29803"
                ],
                "PaxDb": [
                    "9606-ENSP00000295266"
                ],
                "PeptideAtlas": [
                    "P29803"
                ],
                "ProteomicsDB": [
                    "54610"
                ],
                "Antibodypedia": [
                    "25781"
                ],
                "DNASU": [
                    "5161"
                ],
                "Ensembl": [
                    "ENST00000295266.6"
                ],
                "KEGG": [
                    "hsa:5161"
                ],
                "MANE-Select": [
                    "ENST00000295266.6"
                ],
                "UCSC": [
                    "uc003htr.5"
                ],
                "AGR": [
                    "HGNC:8807"
                ],
                "CTD": [
                    "5161"
                ],
                "DisGeNET": [
                    "5161"
                ],
                "GeneCards": [
                    "PDHA2"
                ],
                "HGNC": [
                    "HGNC:8807"
                ],
                "HPA": [
                    "ENSG00000163114"
                ],
                "MalaCards": [
                    "PDHA2"
                ],
                "neXtProt": [
                    "NX_P29803"
                ],
                "OpenTargets": [
                    "ENSG00000163114"
                ],
                "Orphanet": [
                    "399805"
                ],
                "PharmGKB": [
                    "PA33151"
                ],
                "VEuPathDB": [
                    "HostDB:ENSG00000163114"
                ],
                "eggNOG": [
                    "KOG0225"
                ],
                "GeneTree": [
                    "ENSGT00530000063174"
                ],
                "HOGENOM": [
                    "CLU_029393_5_2_1"
                ],
                "InParanoid": [
                    "P29803"
                ],
                "OMA": [
                    "SKRDPIM"
                ],
                "OrthoDB": [
                    "166915at2759"
                ],
                "PhylomeDB": [
                    "P29803"
                ],
                "TreeFam": [
                    "TF300742"
                ],
                "PathwayCommons": [
                    "P29803"
                ],
                "Reactome": [
                    "R-HSA-204174",
                    "R-HSA-5362517",
                    "R-HSA-9861559"
                ],
                "SignaLink": [
                    "P29803"
                ],
                "SIGNOR": [
                    "P29803"
                ],
                "BioGRID-ORCS": [
                    "5161"
                ],
                "ChiTaRS": [
                    "PDHA2"
                ],
                "GeneWiki": [
                    "Pyruvate_dehydrogenase_(lipoamide)_alpha_2"
                ],
                "GenomeRNAi": [
                    "5161"
                ],
                "Pharos": [
                    "P29803"
                ],
                "PRO": [
                    "PR:P29803"
                ],
                "Proteomes": [
                    "UP000005640"
                ],
                "RNAct": [
                    "P29803"
                ],
                "Bgee": [
                    "ENSG00000163114"
                ],
                "GO": [
                    "GO:0005759",
                    "GO:0005739",
                    "GO:0005730",
                    "GO:0005634",
                    "GO:0045254",
                    "GO:0004739",
                    "GO:0034604",
                    "GO:0006086",
                    "GO:0006006",
                    "GO:0006090",
                    "GO:0006099"
                ],
                "CDD": [
                    "cd02000"
                ],
                "Gene3D": [
                    "3.40.50.970"
                ],
                "InterPro": [
                    "IPR001017",
                    "IPR050642",
                    "IPR017597",
                    "IPR029061"
                ],
                "NCBIfam": [
                    "TIGR03182"
                ],
                "PANTHER": [
                    "PTHR11516:SF27",
                    "PTHR11516"
                ],
                "Pfam": [
                    "PF00676"
                ],
                "SUPFAM": [
                    "SSF52518"
                ]
            },
            "citations": [
                {
                    "title": "A testis-specific form of the human pyruvate dehydrogenase E1 alpha subunit is coded for by an intronless gene on chromosome 4.",
                    "pubmedID": "2249846",
                    "doi": "10.1016/0888-7543(90)90275-y"
                },
                {
                    "title": "Complete sequencing and characterization of 21,243 full-length human cDNAs.",
                    "pubmedID": "14702039",
                    "doi": "10.1038/ng1285"
                },
                {
                    "title": "The status, quality, and expansion of the NIH full-length cDNA project: the Mammalian Gene Collection (MGC).",
                    "pubmedID": "15489334",
                    "doi": "10.1101/gr.2596504"
                },
                {
                    "title": "Organization of the cores of the mammalian pyruvate dehydrogenase complex formed by E2 and E2 plus the E3-binding protein and their capacities to bind the E1 and E3 components.",
                    "pubmedID": "14638692",
                    "doi": "10.1074/jbc.m308172200"
                },
                {
                    "title": "Characterization of testis-specific isoenzyme of human pyruvate dehydrogenase.",
                    "pubmedID": "16436377",
                    "doi": "10.1074/jbc.m511481200"
                },
                {
                    "title": "System-wide temporal characterization of the proteome and phosphoproteome of human embryonic stem cell differentiation.",
                    "pubmedID": "21406692",
                    "doi": "10.1126/scisignal.2001570"
                },
                {
                    "title": "Pyruvate dehydrogenase complex: mRNA and protein expression patterns of E1alpha subunit genes in human spermatogenesis.",
                    "pubmedID": "22750801",
                    "doi": "10.1016/j.gene.2012.06.068"
                },
                {
                    "title": "Linked homozygous BMPR1B and PDHA2 variants in a consanguineous family with complex digit malformation and male infertility.",
                    "pubmedID": "29581481",
                    "doi": "10.1038/s41431-018-0121-7"
                },
                {
                    "title": "Rewiring of the Human Mitochondrial Interactome during Neuronal Reprogramming Reveals Regulators of the Respirasome and Neurogenesis.",
                    "pubmedID": "31536960",
                    "doi": "10.1016/j.isci.2019.08.057"
                },
                {
                    "title": "Whole-exome sequencing improves the diagnosis and care of men with non-obstructive azoospermia.",
                    "pubmedID": "35172124",
                    "doi": "10.1016/j.ajhg.2022.01.011"
                }
            ],
            "sequence": {
                "length": 388,
                "mass": 42933,
                "checksum": "075B6CFF6DC73CC5",
                "modified": {
                    "$date": {
                        "$numberLong": "733622400000"
                    }
                },
                "version": 1,
                "sequence": "MLAAFISRVLRRVAQKSARRVLVASRNSSNDATFEIKKCDLYLLEEGPPVTTVLTRAEGLKYYRMMLTVRRMELKADQLYKQKFIRGFCHLCDGQEACCVGLEAGINPSDHVITSYRAHGVCYTRGLSVRSILAELTGRRGGCAKGKGGSMHMYTKNFYGGNGIVGAQGPLGAGIALACKYKGNDEICLTLYGDGAANQGQIAEAFNMAALWKLPCVFICENNLYGMGTSTERAAASPDYYKRGNFIPGLKVDGMDVLCVREATKFAANYCRSGKGPILMELQTYRYHGHSMSDPGVSYRTREEIQEVRSKRDPIIILQDRMVNSKLATVEELKEIGAEVRKEIDDAAQFATTDPEPHLEELGHHIYSSDSSFEVRGANPWIKFKSVS"
            },
            "existence": 0,
            "relevance": 1,
            "proteinID": 1546917137
        }
    ],
    "singleCellExpressions": {
        "cellSignificanceIndex": []
    }
}