No CSI details found for gene ID: 5161

Other Information

This section provides additional information about the gene, including a description generated by an AI language model and details about associated proteins.

Genular Protein ID: 1546917137

Symbol: ODPAT_HUMAN

Name: Pyruvate dehydrogenase E1 component subunit alpha, testis-specific form, mitochondrial

UniProtKB Accession Codes:

Database IDs:

Citations:

PubMed ID: 2249846

Title: A testis-specific form of the human pyruvate dehydrogenase E1 alpha subunit is coded for by an intronless gene on chromosome 4.

PubMed ID: 2249846

DOI: 10.1016/0888-7543(90)90275-y

PubMed ID: 14702039

Title: Complete sequencing and characterization of 21,243 full-length human cDNAs.

PubMed ID: 14702039

DOI: 10.1038/ng1285

PubMed ID: 15489334

Title: The status, quality, and expansion of the NIH full-length cDNA project: the Mammalian Gene Collection (MGC).

PubMed ID: 15489334

DOI: 10.1101/gr.2596504

PubMed ID: 14638692

Title: Organization of the cores of the mammalian pyruvate dehydrogenase complex formed by E2 and E2 plus the E3-binding protein and their capacities to bind the E1 and E3 components.

PubMed ID: 14638692

DOI: 10.1074/jbc.m308172200

PubMed ID: 16436377

Title: Characterization of testis-specific isoenzyme of human pyruvate dehydrogenase.

PubMed ID: 16436377

DOI: 10.1074/jbc.m511481200

PubMed ID: 21406692

Title: System-wide temporal characterization of the proteome and phosphoproteome of human embryonic stem cell differentiation.

PubMed ID: 21406692

DOI: 10.1126/scisignal.2001570

PubMed ID: 22750801

Title: Pyruvate dehydrogenase complex: mRNA and protein expression patterns of E1alpha subunit genes in human spermatogenesis.

PubMed ID: 22750801

DOI: 10.1016/j.gene.2012.06.068

PubMed ID: 29581481

Title: Linked homozygous BMPR1B and PDHA2 variants in a consanguineous family with complex digit malformation and male infertility.

PubMed ID: 29581481

DOI: 10.1038/s41431-018-0121-7

PubMed ID: 31536960

Title: Rewiring of the Human Mitochondrial Interactome during Neuronal Reprogramming Reveals Regulators of the Respirasome and Neurogenesis.

PubMed ID: 31536960

DOI: 10.1016/j.isci.2019.08.057

PubMed ID: 35172124

Title: Whole-exome sequencing improves the diagnosis and care of men with non-obstructive azoospermia.

PubMed ID: 35172124

DOI: 10.1016/j.ajhg.2022.01.011

Sequence Information:

  • Length: 388
  • Mass: 42933
  • Checksum: 075B6CFF6DC73CC5
  • Sequence:
  • MLAAFISRVL RRVAQKSARR VLVASRNSSN DATFEIKKCD LYLLEEGPPV TTVLTRAEGL 
    KYYRMMLTVR RMELKADQLY KQKFIRGFCH LCDGQEACCV GLEAGINPSD HVITSYRAHG 
    VCYTRGLSVR SILAELTGRR GGCAKGKGGS MHMYTKNFYG GNGIVGAQGP LGAGIALACK 
    YKGNDEICLT LYGDGAANQG QIAEAFNMAA LWKLPCVFIC ENNLYGMGTS TERAAASPDY 
    YKRGNFIPGL KVDGMDVLCV REATKFAANY CRSGKGPILM ELQTYRYHGH SMSDPGVSYR 
    TREEIQEVRS KRDPIIILQD RMVNSKLATV EELKEIGAEV RKEIDDAAQF ATTDPEPHLE 
    ELGHHIYSSD SSFEVRGANP WIKFKSVS
 
                
                    {
    "geneID": 5161,
    "tax": {
        "id": 9606,
        "name": [
            {
                "name": "Homo sapiens Linnaeus 1758"
            },
            {
                "name": "Homo sapiens",
                "type": 0
            },
            {
                "name": "human",
                "type": 4
            }
        ]
    },
    "accession": {
        "gene": [
            "AC093828.3"
        ]
    },
    "genePos": {
        "start": 95840093,
        "end": 95841464
    },
    "orientation": true,
    "symbol": "PDHA2",
    "created": {
        "$date": {
            "$numberLong": "1738333349058"
        }
    },
    "crossReference": {
        "enseGeneID": "ENSG00000163114",
        "enseRnaID": [
            "ENST00000295266.6"
        ],
        "enseProtID": [
            "ENSP00000295266.4"
        ]
    },
    "chrom": {
        "pos": "4",
        "type": 1,
        "loc": "4q22.3"
    },
    "desc": "pyruvate dehydrogenase E1 subunit alpha 2",
    "geneType": 5,
    "mim": [
        {
            "id": 179061,
            "relation": 0
        }
    ],
    "ontology": [
        {
            "id": "R-HSA-1430728",
            "term": "Metabolism",
            "cat": 10
        },
        {
            "id": "R-HSA-162582",
            "term": "Signal Transduction",
            "cat": 10
        },
        {
            "id": "R-HSA-1428517",
            "term": "Aerobic respiration and respiratory electron transport",
            "cat": 11
        },
        {
            "id": "R-HSA-9006931",
            "term": "Signaling by Nuclear Receptors",
            "cat": 11
        },
        {
            "id": "R-HSA-5362517",
            "term": "Signaling by Retinoic Acid",
            "cat": 12
        },
        {
            "id": "R-HSA-70268",
            "term": "Pyruvate metabolism",
            "cat": 12
        },
        {
            "id": "R-HSA-9861559",
            "term": "PDH complex synthesizes acetyl-CoA from PYR",
            "cat": 13
        },
        {
            "id": "R-HSA-9861718",
            "term": "Regulation of pyruvate metabolism",
            "cat": 13
        },
        {
            "id": "R-HSA-204174",
            "term": "Regulation of pyruvate dehydrogenase (PDH) complex",
            "cat": 14
        },
        {
            "id": "GO:0004739",
            "term": "pyruvate dehydrogenase (acetyl-transferring) activity",
            "cat": 0
        },
        {
            "id": "GO:0004739",
            "term": "pyruvate dehydrogenase (acetyl-transferring) activity",
            "pubMed": [
                16436377
            ],
            "cat": 0
        },
        {
            "id": "GO:0005515",
            "term": "protein binding",
            "pubMed": [
                32296183
            ],
            "cat": 0
        },
        {
            "id": "GO:0034604",
            "term": "pyruvate dehydrogenase (NAD+) activity",
            "pubMed": [
                16436377
            ],
            "cat": 0
        },
        {
            "id": "GO:0046872",
            "term": "metal ion binding",
            "cat": 0
        },
        {
            "id": "GO:0006006",
            "term": "glucose metabolic process",
            "cat": 1
        },
        {
            "id": "GO:0006086",
            "term": "acetyl-CoA biosynthetic process from pyruvate",
            "cat": 1
        },
        {
            "id": "GO:0006086",
            "term": "acetyl-CoA biosynthetic process from pyruvate",
            "pubMed": [
                16436377
            ],
            "cat": 1
        },
        {
            "id": "GO:0006090",
            "term": "pyruvate metabolic process",
            "pubMed": [
                16436377
            ],
            "cat": 1
        },
        {
            "id": "GO:0006099",
            "term": "tricarboxylic acid cycle",
            "cat": 1
        },
        {
            "id": "GO:0005634",
            "term": "nucleus",
            "pubMed": [
                21630459
            ],
            "cat": 2
        },
        {
            "id": "GO:0005730",
            "term": "nucleolus",
            "cat": 2
        },
        {
            "id": "GO:0005739",
            "term": "mitochondrion",
            "pubMed": [
                34800366
            ],
            "cat": 2
        },
        {
            "id": "GO:0005739",
            "term": "mitochondrion",
            "cat": 2
        },
        {
            "id": "GO:0005739",
            "term": "mitochondrion",
            "pubMed": [
                24534072
            ],
            "cat": 2
        },
        {
            "id": "GO:0005759",
            "term": "mitochondrial matrix",
            "cat": 2
        },
        {
            "id": "GO:0045254",
            "term": "pyruvate dehydrogenase complex",
            "cat": 2
        }
    ],
    "protein": [
        {
            "symbol": "ODPAT_HUMAN",
            "name": "Pyruvate dehydrogenase E1 component subunit alpha, testis-specific form, mitochondrial",
            "accession": [
                "P29803",
                "B2R9Q3",
                "Q0VDI5",
                "Q4VC02",
                "Q6NXQ1"
            ],
            "databaseIDs": {
                "NCBI Taxonomy": [
                    "9606"
                ],
                "Rhea": [
                    "RHEA:19189",
                    "RHEA-COMP:10480",
                    "RHEA-COMP:10481"
                ],
                "ChEBI": [
                    "CHEBI:15361",
                    "CHEBI:15378",
                    "CHEBI:16526",
                    "CHEBI:83099",
                    "CHEBI:83111",
                    "CHEBI:58937",
                    "CHEBI:18420",
                    "CHEBI:15361",
                    "CHEBI:15361",
                    "CHEBI:58937",
                    "CHEBI:15361",
                    "CHEBI:58937",
                    "CHEBI:15361",
                    "CHEBI:58937",
                    "CHEBI:15361",
                    "CHEBI:58937",
                    "CHEBI:18420",
                    "CHEBI:15361",
                    "CHEBI:58937",
                    "CHEBI:15361",
                    "CHEBI:58937",
                    "CHEBI:15361",
                    "CHEBI:58937",
                    "CHEBI:18420",
                    "CHEBI:15361",
                    "CHEBI:58937",
                    "CHEBI:18420",
                    "CHEBI:15361",
                    "CHEBI:58937"
                ],
                "EC": [
                    "1.2.4.1",
                    "1.2.4.1"
                ],
                "MIM": [
                    "619828",
                    "179061",
                    "619828"
                ],
                "EMBL": [
                    "M86808",
                    "AK313872",
                    "BC030697",
                    "BC066953",
                    "BC094760",
                    "BC119656",
                    "BC119657",
                    "BC127637",
                    "BC127638"
                ],
                "CCDS": [
                    "CCDS3644.1"
                ],
                "PIR": [
                    "A37104"
                ],
                "RefSeq": [
                    "NP_005381.1"
                ],
                "AlphaFoldDB": [
                    "P29803"
                ],
                "SMR": [
                    "P29803"
                ],
                "BioGRID": [
                    "111187"
                ],
                "ComplexPortal": [
                    "CPX-6242"
                ],
                "IntAct": [
                    "P29803"
                ],
                "MINT": [
                    "P29803"
                ],
                "STRING": [
                    "9606.ENSP00000295266"
                ],
                "DrugBank": [
                    "DB00157"
                ],
                "iPTMnet": [
                    "P29803"
                ],
                "PhosphoSitePlus": [
                    "P29803"
                ],
                "BioMuta": [
                    "PDHA2"
                ],
                "jPOST": [
                    "P29803"
                ],
                "MassIVE": [
                    "P29803"
                ],
                "PaxDb": [
                    "9606-ENSP00000295266"
                ],
                "PeptideAtlas": [
                    "P29803"
                ],
                "ProteomicsDB": [
                    "54610"
                ],
                "Antibodypedia": [
                    "25781"
                ],
                "DNASU": [
                    "5161"
                ],
                "Ensembl": [
                    "ENST00000295266.6"
                ],
                "KEGG": [
                    "hsa:5161"
                ],
                "MANE-Select": [
                    "ENST00000295266.6"
                ],
                "UCSC": [
                    "uc003htr.5"
                ],
                "AGR": [
                    "HGNC:8807"
                ],
                "CTD": [
                    "5161"
                ],
                "DisGeNET": [
                    "5161"
                ],
                "GeneCards": [
                    "PDHA2"
                ],
                "HGNC": [
                    "HGNC:8807"
                ],
                "HPA": [
                    "ENSG00000163114"
                ],
                "MalaCards": [
                    "PDHA2"
                ],
                "neXtProt": [
                    "NX_P29803"
                ],
                "OpenTargets": [
                    "ENSG00000163114"
                ],
                "Orphanet": [
                    "399805"
                ],
                "PharmGKB": [
                    "PA33151"
                ],
                "VEuPathDB": [
                    "HostDB:ENSG00000163114"
                ],
                "eggNOG": [
                    "KOG0225"
                ],
                "GeneTree": [
                    "ENSGT00530000063174"
                ],
                "HOGENOM": [
                    "CLU_029393_5_2_1"
                ],
                "InParanoid": [
                    "P29803"
                ],
                "OMA": [
                    "SKRDPIM"
                ],
                "OrthoDB": [
                    "166915at2759"
                ],
                "PhylomeDB": [
                    "P29803"
                ],
                "TreeFam": [
                    "TF300742"
                ],
                "PathwayCommons": [
                    "P29803"
                ],
                "Reactome": [
                    "R-HSA-204174",
                    "R-HSA-5362517",
                    "R-HSA-9861559"
                ],
                "SignaLink": [
                    "P29803"
                ],
                "SIGNOR": [
                    "P29803"
                ],
                "BioGRID-ORCS": [
                    "5161"
                ],
                "ChiTaRS": [
                    "PDHA2"
                ],
                "GeneWiki": [
                    "Pyruvate_dehydrogenase_(lipoamide)_alpha_2"
                ],
                "GenomeRNAi": [
                    "5161"
                ],
                "Pharos": [
                    "P29803"
                ],
                "PRO": [
                    "PR:P29803"
                ],
                "Proteomes": [
                    "UP000005640"
                ],
                "RNAct": [
                    "P29803"
                ],
                "Bgee": [
                    "ENSG00000163114"
                ],
                "GO": [
                    "GO:0005759",
                    "GO:0005739",
                    "GO:0005730",
                    "GO:0005634",
                    "GO:0045254",
                    "GO:0004739",
                    "GO:0034604",
                    "GO:0006086",
                    "GO:0006006",
                    "GO:0006090",
                    "GO:0006099"
                ],
                "CDD": [
                    "cd02000"
                ],
                "Gene3D": [
                    "3.40.50.970"
                ],
                "InterPro": [
                    "IPR001017",
                    "IPR050642",
                    "IPR017597",
                    "IPR029061"
                ],
                "NCBIfam": [
                    "TIGR03182"
                ],
                "PANTHER": [
                    "PTHR11516:SF27",
                    "PTHR11516"
                ],
                "Pfam": [
                    "PF00676"
                ],
                "SUPFAM": [
                    "SSF52518"
                ]
            },
            "citations": [
                {
                    "title": "A testis-specific form of the human pyruvate dehydrogenase E1 alpha subunit is coded for by an intronless gene on chromosome 4.",
                    "pubmedID": "2249846",
                    "doi": "10.1016\/0888-7543(90)90275-y"
                },
                {
                    "title": "Complete sequencing and characterization of 21,243 full-length human cDNAs.",
                    "pubmedID": "14702039",
                    "doi": "10.1038\/ng1285"
                },
                {
                    "title": "The status, quality, and expansion of the NIH full-length cDNA project: the Mammalian Gene Collection (MGC).",
                    "pubmedID": "15489334",
                    "doi": "10.1101\/gr.2596504"
                },
                {
                    "title": "Organization of the cores of the mammalian pyruvate dehydrogenase complex formed by E2 and E2 plus the E3-binding protein and their capacities to bind the E1 and E3 components.",
                    "pubmedID": "14638692",
                    "doi": "10.1074\/jbc.m308172200"
                },
                {
                    "title": "Characterization of testis-specific isoenzyme of human pyruvate dehydrogenase.",
                    "pubmedID": "16436377",
                    "doi": "10.1074\/jbc.m511481200"
                },
                {
                    "title": "System-wide temporal characterization of the proteome and phosphoproteome of human embryonic stem cell differentiation.",
                    "pubmedID": "21406692",
                    "doi": "10.1126\/scisignal.2001570"
                },
                {
                    "title": "Pyruvate dehydrogenase complex: mRNA and protein expression patterns of E1alpha subunit genes in human spermatogenesis.",
                    "pubmedID": "22750801",
                    "doi": "10.1016\/j.gene.2012.06.068"
                },
                {
                    "title": "Linked homozygous BMPR1B and PDHA2 variants in a consanguineous family with complex digit malformation and male infertility.",
                    "pubmedID": "29581481",
                    "doi": "10.1038\/s41431-018-0121-7"
                },
                {
                    "title": "Rewiring of the Human Mitochondrial Interactome during Neuronal Reprogramming Reveals Regulators of the Respirasome and Neurogenesis.",
                    "pubmedID": "31536960",
                    "doi": "10.1016\/j.isci.2019.08.057"
                },
                {
                    "title": "Whole-exome sequencing improves the diagnosis and care of men with non-obstructive azoospermia.",
                    "pubmedID": "35172124",
                    "doi": "10.1016\/j.ajhg.2022.01.011"
                }
            ],
            "sequence": {
                "length": 388,
                "mass": 42933,
                "checksum": "075B6CFF6DC73CC5",
                "modified": {
                    "$date": {
                        "$numberLong": "733622400000"
                    }
                },
                "version": 1,
                "sequence": "MLAAFISRVLRRVAQKSARRVLVASRNSSNDATFEIKKCDLYLLEEGPPVTTVLTRAEGLKYYRMMLTVRRMELKADQLYKQKFIRGFCHLCDGQEACCVGLEAGINPSDHVITSYRAHGVCYTRGLSVRSILAELTGRRGGCAKGKGGSMHMYTKNFYGGNGIVGAQGPLGAGIALACKYKGNDEICLTLYGDGAANQGQIAEAFNMAALWKLPCVFICENNLYGMGTSTERAAASPDYYKRGNFIPGLKVDGMDVLCVREATKFAANYCRSGKGPILMELQTYRYHGHSMSDPGVSYRTREEIQEVRSKRDPIIILQDRMVNSKLATVEELKEIGAEVRKEIDDAAQFATTDPEPHLEELGHHIYSSDSSFEVRGANPWIKFKSVS"
            },
            "existence": 0,
            "relevance": 1,
            "proteinID": 1546917137
        }
    ],
    "singleCellExpressions": {
        "cellSignificanceIndex": []
    }
}