Details for: UBA1

Gene ID: 7317

Gene Type:  Protein-coding  - A gene that serves as a template for producing a messenger RNA (mRNA) molecule, which is then translated into a functional protein.

Symbol: UBA1

Ensembl ID: ENSG00000130985

Description: ubiquitin like modifier activating enzyme 1

Selected Context(s):  Overall

Cell Significance Landscape

Contexts:

Associated with

Significant Cells

Cell Significance Index (CSI) scores for the chosen context(s)

  • fallopian tube secretory epithelial cell CL4030006
    CSI 30.05
    rCSI 28.93%
    PRS 27.55
  • caudal ganglionic eminence derived cortical interneuron CL4023064
    CSI 11.79
    rCSI 20.83%
    PRS 15.93
  • kidney loop of Henle thin descending limb epithelial cell CL1001111
    CSI 10.57
    rCSI 14.99%
    PRS 24.77
  • CD4-positive, CD25-positive, alpha-beta regulatory T cell CL0000792
    CSI 9.72
    rCSI 9.55%
    PRS 40.23
  • intestinal epithelial cell CL0002563
    CSI 8.58
    rCSI 8.96%
    PRS 27.44
  • megakaryocyte-erythroid progenitor cell CL0000050
    CSI 8.1
    rCSI 7.32%
    PRS 24.31
  • lung pericyte CL0009089
    CSI 7.76
    rCSI 20.48%
    PRS 31.8
  • retinal pigment epithelial cell CL0002586
    CSI 7.18
    rCSI 14.26%
    PRS 27.62
  • alveolar type 1 fibroblast cell CL4028004
    CSI 6.85
    rCSI 7.5%
    PRS 29.79
  • mesenchymal cell CL0008019
    CSI 6.66
    rCSI 16.92%
    PRS 26.03
  • duct epithelial cell CL0000068
    CSI 5.88
    rCSI 8.6%
    PRS 28.38
  • granulocyte monocyte progenitor cell CL0000557
    CSI 5.75
    rCSI 4.98%
    PRS 29.83
  • ciliated epithelial cell CL0000067
    CSI 5.62
    rCSI 4.94%
    PRS 19.57
  • cardiac muscle cell CL0000746
    CSI 5.57
    rCSI 8%
    PRS 20.97
  • multi-ciliated epithelial cell CL0005012
    CSI 5.19
    rCSI 5.18%
    PRS 22.84
  • activated CD4-positive, alpha-beta T cell CL0000896
    CSI 4.56
    rCSI 4.22%
    PRS 45.71
  • CD1c-positive myeloid dendritic cell CL0002399
    CSI 4.51
    rCSI 5.45%
    PRS 32.07
  • regular ventricular cardiac myocyte CL0002131
    CSI 4.2
    rCSI 26.21%
    PRS 21.36
  • pvalb GABAergic cortical interneuron CL4023018
    CSI 3.98
    rCSI 4.95%
    PRS 15.32
  • skin fibroblast CL0002620
    CSI 3.8
    rCSI 3.28%
    PRS 38.19
  • effector memory CD8-positive, alpha-beta T cell, terminally differentiated CL0001062
    CSI 3.77
    rCSI 18.92%
    PRS 35.01
  • cerebellar granule cell CL0001031
    CSI 3.7
    rCSI 5.44%
    PRS 24.6
  • kidney distal convoluted tubule epithelial cell CL1000849
    CSI 3.7
    rCSI 39.18%
    PRS 31.97
  • ON-bipolar cell CL0000749
    CSI 3.58
    rCSI 5.32%
    PRS 30.29
  • CD4-positive, alpha-beta thymocyte CL0000810
    CSI 3.14
    rCSI 2.52%
    PRS 45.45
  • foveolar cell of stomach CL0002179
    CSI 3.05
    rCSI 6.48%
    PRS 40.74
  • effector CD8-positive, alpha-beta T cell CL0001050
    CSI 2.84
    rCSI 2.16%
    PRS 35.14
  • secretory cell CL0000151
    CSI 2.8
    rCSI 2.92%
    PRS 27.39
  • immature B cell CL0000816
    CSI 2.74
    rCSI 2.03%
    PRS 38.18
  • mesenchymal stem cell CL0000134
    CSI 2.69
    rCSI 29.47%
    PRS 44.6
  • melanocyte CL0000148
    CSI 2.66
    rCSI 1.97%
    PRS 22.87
  • naive T cell CL0000898
    CSI 2.66
    rCSI 1.85%
    PRS 36.93
  • enteroendocrine cell CL0000164
    CSI 2.64
    rCSI 3.61%
    PRS 29.42
  • double negative thymocyte CL0002489
    CSI 2.62
    rCSI 1.82%
    PRS 32.18
  • bronchus fibroblast of lung CL2000093
    CSI 2.62
    rCSI 2.13%
    PRS 27.76
  • central memory CD8-positive, alpha-beta T cell CL0000907
    CSI 2.61
    rCSI 1.76%
    PRS 33.13
  • Kupffer cell CL0000091
    CSI 2.61
    rCSI 5.98%
    PRS 26.09
  • pancreatic acinar cell CL0002064
    CSI 2.59
    rCSI 3.45%
    PRS 29.37
  • forebrain radial glial cell CL0013000
    CSI 2.59
    rCSI 8.31%
    PRS 35.65
  • myeloid lineage restricted progenitor cell CL0000839
    CSI 2.57
    rCSI 13.29%
    PRS 49.03
  • precursor B cell CL0000817
    CSI 2.51
    rCSI 2.2%
    PRS 34.8
  • intestine goblet cell CL0019031
    CSI 2.5
    rCSI 2.22%
    PRS 26.84
  • mesodermal cell CL0000222
    CSI 2.49
    rCSI 2.99%
    PRS 25.82
  • epithelial cell of lower respiratory tract CL0002632
    CSI 2.46
    rCSI 1.91%
    PRS 26.01
  • early lymphoid progenitor CL0000936
    CSI 2.4
    rCSI 2.11%
    PRS 30.46
  • acinar cell CL0000622
    CSI 2.36
    rCSI 3.46%
    PRS 34.77
  • respiratory suprabasal cell CL4033048
    CSI 2.36
    rCSI 3.03%
    PRS 30.67
  • myofibroblast cell CL0000186
    CSI 2.36
    rCSI 3.26%
    PRS 34.87
  • interstitial cell of Cajal CL0002088
    CSI 2.35
    rCSI 2.99%
    PRS 30.62
  • peripheral nervous system neuron CL2000032
    CSI 2.34
    rCSI 3.18%
    PRS 23.18
  • paneth cell CL0000510
    CSI 2.33
    rCSI 3.44%
    PRS 40.73
  • serotonergic neuron CL0000850
    CSI 2.33
    rCSI 10.39%
    PRS 18.45
  • perivascular cell CL4033054
    CSI 2.3
    rCSI 3.15%
    PRS 30.1
  • myeloid dendritic cell CL0000782
    CSI 2.28
    rCSI 3.3%
    PRS 39.76
  • glandular epithelial cell CL0000150
    CSI 2.26
    rCSI 5.95%
    PRS 48.72
  • lung macrophage CL1001603
    CSI 2.26
    rCSI 5.04%
    PRS 31.23
  • lung secretory cell CL1000272
    CSI 2.23
    rCSI 5.53%
    PRS 24.88
  • hematopoietic stem cell CL0000037
    CSI 2.2
    rCSI 1.47%
    PRS 31.13
  • inflammatory macrophage CL0000863
    CSI 2.16
    rCSI 3.69%
    PRS 50.98
  • endothelial cell of periportal hepatic sinusoid CL0019021
    CSI 2.15
    rCSI 9.87%
    PRS 52.42
  • interneuron CL0000099
    CSI 2.15
    rCSI 4.31%
    PRS 19.86
  • fibroblast of lung CL0002553
    CSI 2.14
    rCSI 1.99%
    PRS 26.66
  • midzonal region hepatocyte CL0019028
    CSI 2.14
    rCSI 5.02%
    PRS 36.78
  • epithelial cell CL0000066
    CSI 2.13
    rCSI 3.27%
    PRS 33.66
  • pro-B cell CL0000826
    CSI 2.11
    rCSI 1.74%
    PRS 27.09
  • central memory CD4-positive, alpha-beta T cell CL0000904
    CSI 2.08
    rCSI 1.23%
    PRS 37.29
  • alpha-beta T cell CL0000789
    CSI 2.07
    rCSI 2.43%
    PRS 37.39
  • T-helper 17 cell CL0000899
    CSI 2.05
    rCSI 1.63%
    PRS 45.68
  • plasmablast CL0000980
    CSI 2.05
    rCSI 1.61%
    PRS 31.99
  • goblet cell CL0000160
    CSI 1.97
    rCSI 1.86%
    PRS 27.92
  • mucous neck cell CL0000651
    CSI 1.95
    rCSI 2.81%
    PRS 40.34
  • conjunctival epithelial cell CL1000432
    CSI 1.92
    rCSI 2.94%
    PRS 26.86
  • transit amplifying cell of colon CL0009011
    CSI 1.9
    rCSI 2.24%
    PRS 30.37
  • renal alpha-intercalated cell CL0005011
    CSI 1.9
    rCSI 2.54%
    PRS 33.72
  • pancreatic D cell CL0000173
    CSI 1.9
    rCSI 1.86%
    PRS 28.59
  • CD14-positive, CD16-positive monocyte CL0002397
    CSI 1.89
    rCSI 2.47%
    PRS 37.37
  • cerebral cortex GABAergic interneuron CL0010011
    CSI 1.87
    rCSI 5.51%
    PRS 30.94
  • kidney connecting tubule epithelial cell CL1000768
    CSI 1.83
    rCSI 4.64%
    PRS 20.48
  • neural crest cell CL0011012
    CSI 1.82
    rCSI 1.44%
    PRS 18.44
  • effector CD4-positive, alpha-beta T cell CL0001044
    CSI 1.78
    rCSI 5.11%
    PRS 39.55
  • rod bipolar cell CL0000751
    CSI 1.77
    rCSI 3.19%
    PRS 22.2
  • vascular leptomeningeal cell CL4023051
    CSI 1.77
    rCSI 3.11%
    PRS 20.87
  • kidney interstitial alternatively activated macrophage CL1000695
    CSI 1.77
    rCSI 4.61%
    PRS 25.34
  • retinal blood vessel endothelial cell CL0002585
    CSI 1.74
    rCSI 2.77%
    PRS 29.23
  • brush cell of tracheobronchial tree CL0002075
    CSI 1.72
    rCSI 5.11%
    PRS 36.15
  • CD4-positive, alpha-beta memory T cell CL0000897
    CSI 1.72
    rCSI 1.23%
    PRS 36.35
  • retinal bipolar neuron CL0000748
    CSI 1.72
    rCSI 3.22%
    PRS 19.63
  • group 3 innate lymphoid cell CL0001071
    CSI 1.72
    rCSI 1.29%
    PRS 28.61
  • enterocyte CL0000584
    CSI 1.72
    rCSI 2.77%
    PRS 38.19
  • blood vessel endothelial cell CL0000071
    CSI 1.71
    rCSI 3.55%
    PRS 26.36
  • activated type II NK T cell CL0000931
    CSI 1.7
    rCSI 1.92%
    PRS 41.28
  • corneal epithelial cell CL0000575
    CSI 1.7
    rCSI 4.86%
    PRS 44.16
  • intrahepatic cholangiocyte CL0002538
    CSI 1.7
    rCSI 4.07%
    PRS 44.16
  • keratinocyte CL0000312
    CSI 1.69
    rCSI 1.42%
    PRS 31.26
  • M cell of gut CL0000682
    CSI 1.68
    rCSI 1.78%
    PRS 42.79
  • pulmonary ionocyte CL0017000
    CSI 1.68
    rCSI 2.04%
    PRS 32.96
  • myoepithelial cell CL0000185
    CSI 1.67
    rCSI 4.23%
    PRS 32.7
  • tracheal goblet cell CL1000329
    CSI 1.66
    rCSI 3.62%
    PRS 47.76
  • lung neuroendocrine cell CL1000223
    CSI 1.64
    rCSI 2.43%
    PRS 30.32
  • T follicular helper cell CL0002038
    CSI 1.63
    rCSI 1.22%
    PRS 40.45
  • megakaryocyte progenitor cell CL0000553
    CSI 0.1
    rCSI 2.1%
    PRS 65.0%
  • stromal cell of ovary CL0002132
    CSI 0.2
    rCSI 0.4%
    PRS 42.1%
  • acinar cell of salivary gland CL0002623
    CSI 0.2
    rCSI 5.2%
    PRS 47.7%
  • kidney loop of Henle epithelial cell CL1000909
    CSI 0.3
    rCSI 6.5%
    PRS 82.2%
  • primitive red blood cell CL0002355
    CSI 0.4
    rCSI 2.1%
    PRS 42.1%
  • basal cell of epithelium of trachea CL1000348
    CSI 0.4
    rCSI 2.8%
    PRS 59.6%
  • eosinophil CL0000771
    CSI 0.4
    rCSI 2.8%
    PRS 59.7%
  • basophil mast progenitor cell CL0002028
    CSI 0.5
    rCSI 2.4%
    PRS 71.1%
  • differentiation-committed oligodendrocyte precursor CL4023059
    CSI 0.5
    rCSI 0.8%
    PRS 22.9%
  • pancreatic stellate cell CL0002410
    CSI 0.5
    rCSI 2.7%
    PRS 38.0%
  • CD14-positive, CD16-negative classical monocyte CL0002057
    CSI 0.5
    rCSI 2.9%
    PRS 53.4%
  • type EC enteroendocrine cell CL0000577
    CSI 0.5
    rCSI 1.7%
    PRS 41.2%
  • near-projecting glutamatergic cortical neuron CL4023012
    CSI 0.5
    rCSI 1.8%
    PRS 17.0%
  • Bergmann glial cell CL0000644
    CSI 0.5
    rCSI 0.7%
    PRS 26.0%
  • lymphoid lineage restricted progenitor cell CL0000838
    CSI 0.5
    rCSI 2.0%
    PRS 42.9%
  • enterocyte of epithelium of large intestine CL0002071
    CSI 0.6
    rCSI 2.9%
    PRS 42.8%
  • small intestine goblet cell CL1000495
    CSI 0.6
    rCSI 1.2%
    PRS 35.1%
  • lamp5 GABAergic cortical interneuron CL4023011
    CSI 0.6
    rCSI 1.0%
    PRS 16.3%
  • kidney epithelial cell CL0002518
    CSI 0.6
    rCSI 1.1%
    PRS 51.4%
  • fraction A pre-pro B cell CL0002045
    CSI 0.6
    rCSI 0.7%
    PRS 49.6%
  • pancreatic PP cell CL0002275
    CSI 0.7
    rCSI 2.6%
    PRS 42.9%
  • tracheobronchial serous cell CL0019001
    CSI 0.7
    rCSI 2.8%
    PRS 45.0%
  • ciliated columnar cell of tracheobronchial tree CL0002145
    CSI 0.7
    rCSI 1.5%
    PRS 26.9%
  • large pre-B-II cell CL0000957
    CSI 0.7
    rCSI 1.9%
    PRS 41.9%
  • transit amplifying cell CL0009010
    CSI 0.7
    rCSI 1.0%
    PRS 41.7%
  • dopaminergic neuron CL0000700
    CSI 0.7
    rCSI 3.9%
    PRS 16.5%
  • L6b glutamatergic cortical neuron CL4023038
    CSI 0.7
    rCSI 2.2%
    PRS 17.1%
  • Cajal-Retzius cell CL0000695
    CSI 0.7
    rCSI 5.5%
    PRS 46.9%
  • L2/3-6 intratelencephalic projecting glutamatergic neuron CL4023040
    CSI 0.7
    rCSI 1.7%
    PRS 15.9%
  • elicited macrophage CL0000861
    CSI 0.7
    rCSI 0.7%
    PRS 31.8%
  • hepatocyte CL0000182
    CSI 0.7
    rCSI 1.3%
    PRS 24.9%
  • cardiac neuron CL0010022
    CSI 0.7
    rCSI 2.3%
    PRS 22.9%
  • L5 extratelencephalic projecting glutamatergic cortical neuron CL4023041
    CSI 0.7
    rCSI 2.6%
    PRS 15.5%
  • mammary gland epithelial cell CL0002327
    CSI 0.7
    rCSI 2.6%
    PRS 43.4%
  • parietal epithelial cell CL1000452
    CSI 0.8
    rCSI 2.0%
    PRS 22.3%
  • late pro-B cell CL0002048
    CSI 0.8
    rCSI 2.0%
    PRS 60.9%
  • respiratory basal cell CL0002633
    CSI 0.8
    rCSI 0.8%
    PRS 31.4%
  • paneth cell of epithelium of small intestine CL1000343
    CSI 0.8
    rCSI 2.2%
    PRS 40.4%
  • endothelial cell of placenta CL0009092
    CSI 0.8
    rCSI 4.1%
    PRS 35.6%
  • retinal cone cell CL0000573
    CSI 0.8
    rCSI 1.3%
    PRS 20.5%
  • retina horizontal cell CL0000745
    CSI 0.8
    rCSI 1.3%
    PRS 24.6%
  • chandelier pvalb GABAergic cortical interneuron CL4023036
    CSI 0.8
    rCSI 2.6%
    PRS 18.6%
  • endothelial cell of pericentral hepatic sinusoid CL0019022
    CSI 0.9
    rCSI 2.6%
    PRS 38.3%
  • CD8-positive, CD28-negative, alpha-beta regulatory T cell CL0000920
    CSI 0.9
    rCSI 1.8%
    PRS 42.9%
  • deuterosomal cell CL4033044
    CSI 0.9
    rCSI 3.1%
    PRS 39.5%
  • bronchial goblet cell CL1000312
    CSI 0.9
    rCSI 3.7%
    PRS 50.6%
  • pluripotent stem cell CL0002248
    CSI 0.9
    rCSI 27.5%
    PRS 52.0%
  • kidney loop of Henle thin ascending limb epithelial cell CL1001107
    CSI 0.9
    rCSI 2.4%
    PRS 24.6%
  • retinal ganglion cell CL0000740
    CSI 0.9
    rCSI 2.1%
    PRS 19.2%
  • lung ciliated cell CL1000271
    CSI 0.9
    rCSI 1.1%
    PRS 19.9%
  • IgG plasma cell CL0000985
    CSI 0.9
    rCSI 1.1%
    PRS 44.2%
  • small pre-B-II cell CL0000954
    CSI 1.0
    rCSI 0.9%
    PRS 50.0%
  • respiratory epithelial cell CL0002368
    CSI 1.0
    rCSI 6.2%
    PRS 66.6%
  • BEST4+ enteroycte CL4030026
    CSI 1.0
    rCSI 1.3%
    PRS 28.6%
  • common myeloid progenitor CL0000049
    CSI 1.0
    rCSI 0.8%
    PRS 26.8%
  • erythroid progenitor cell CL0000038
    CSI 1.0
    rCSI 5.9%
    PRS 37.6%
  • sncg GABAergic cortical interneuron CL4023015
    CSI 1.0
    rCSI 1.7%
    PRS 17.7%
  • enteroendocrine cell of small intestine CL0009006
    CSI 1.1
    rCSI 2.3%
    PRS 39.3%
  • colon goblet cell CL0009039
    CSI 1.1
    rCSI 2.5%
    PRS 38.4%
  • club cell CL0000158
    CSI 1.1
    rCSI 1.6%
    PRS 29.5%
  • squamous epithelial cell CL0000076
    CSI 1.1
    rCSI 2.6%
    PRS 32.2%
  • promyelocyte CL0000836
    CSI 1.1
    rCSI 1.6%
    PRS 36.1%
  • ionocyte CL0005006
    CSI 1.1
    rCSI 1.2%
    PRS 24.7%
  • promonocyte CL0000559
    CSI 1.1
    rCSI 2.0%
    PRS 35.3%
  • placental villous trophoblast CL2000060
    CSI 1.2
    rCSI 1.8%
    PRS 25.1%
  • chondrocyte CL0000138
    CSI 1.2
    rCSI 1.8%
    PRS 22.5%
  • extravillous trophoblast CL0008036
    CSI 1.2
    rCSI 1.5%
    PRS 23.5%
  • lung endothelial cell CL1001567
    CSI 1.2
    rCSI 2.8%
    PRS 55.3%
  • luminal epithelial cell of mammary gland CL0002326
    CSI 1.2
    rCSI 2.2%
    PRS 40.1%
  • pancreatic ductal cell CL0002079
    CSI 1.2
    rCSI 2.3%
    PRS 27.5%
  • pancreatic epsilon cell CL0005019
    CSI 1.2
    rCSI 5.5%
    PRS 52.3%
  • common lymphoid progenitor CL0000051
    CSI 1.2
    rCSI 1.6%
    PRS 47.5%
  • common dendritic progenitor CL0001029
    CSI 1.2
    rCSI 1.5%
    PRS 34.2%
  • periportal region hepatocyte CL0019026
    CSI 1.2
    rCSI 4.8%
    PRS 35.6%
  • glioblast CL0000030
    CSI 1.3
    rCSI 2.0%
    PRS 22.8%
  • choroid plexus epithelial cell CL0000706
    CSI 1.3
    rCSI 2.0%
    PRS 20.7%
  • enteric smooth muscle cell CL0002504
    CSI 1.3
    rCSI 1.8%
    PRS 29.5%
  • germinal center B cell CL0000844
    CSI 1.3
    rCSI 3.8%
    PRS 53.0%
  • epithelial cell of lung CL0000082
    CSI 1.3
    rCSI 1.1%
    PRS 25.4%
  • Hofbauer cell CL3000001
    CSI 1.3
    rCSI 2.4%
    PRS 33.8%
  • cerebral cortex endothelial cell CL1001602
    CSI 1.3
    rCSI 2.2%
    PRS 20.5%
  • basal cell CL0000646
    CSI 1.3
    rCSI 1.7%
    PRS 28.8%
  • respiratory hillock cell CL4030023
    CSI 1.3
    rCSI 2.3%
    PRS 41.9%
  • radial glial cell CL0000681
    CSI 1.3
    rCSI 1.8%
    PRS 26.9%
  • granulocyte CL0000094
    CSI 1.3
    rCSI 2.0%
    PRS 34.1%
  • luminal cell of prostate epithelium CL0002340
    CSI 1.3
    rCSI 7.2%
    PRS 43.4%
  • neuroblast (sensu Vertebrata) CL0000031
    CSI 1.3
    rCSI 1.7%
    PRS 25.5%
  • endocrine cell CL0000163
    CSI 1.4
    rCSI 7.0%
    PRS 69.1%
  • mononuclear phagocyte CL0000113
    CSI 1.4
    rCSI 3.0%
    PRS 30.3%
  • VIP GABAergic cortical interneuron CL4023016
    CSI 1.4
    rCSI 1.6%
    PRS 16.1%
  • dendritic cell, human CL0001056
    CSI 1.4
    rCSI 2.1%
    PRS 31.9%
  • nasal mucosa goblet cell CL0002480
    CSI 1.4
    rCSI 1.6%
    PRS 37.4%
  • colonocyte CL1000347
    CSI 1.4
    rCSI 2.0%
    PRS 34.9%
  • alveolar adventitial fibroblast CL4028006
    CSI 1.4
    rCSI 2.2%
    PRS 26.9%
  • neuroblast (sensu Nematoda and Protostomia) CL0000338
    CSI 1.4
    rCSI 1.6%
    PRS 23.1%
  • colon epithelial cell CL0011108
    CSI 1.4
    rCSI 1.5%
    PRS 24.9%
  • type B pancreatic cell CL0000169
    CSI 1.4
    rCSI 3.1%
    PRS 24.6%
  • alveolar macrophage CL0000583
    CSI 1.4
    rCSI 2.3%
    PRS 31.1%
  • stem cell CL0000034
    CSI 1.4
    rCSI 1.4%
    PRS 19.9%
  • pulmonary capillary endothelial cell CL4028001
    CSI 1.4
    rCSI 2.7%
    PRS 41.3%

Cell ID: Standard Cell Ontology term used for mapping and comparing cells across experiments. Ensures consistency in analyzing cellular functions across tissues.
Fold Change: Represents the ratio of the current Cell Significance Index to the Cell Significance Index Threshold, indicating how much the gene expression has changed compared to a baseline.
Cell Significance Index: Reflects how strongly a gene is expressed in this specific cell.

Cell ID: Standard Cell Ontology term used for mapping and comparing cells across experiments. Ensures consistency in analyzing cellular functions across tissues.
Fold Change: Represents the ratio of the current Cell Significance Index to the Cell Significance Index Threshold, indicating how much the gene expression has changed compared to a baseline.
Cell Significance Index: Reflects how strongly a gene is expressed in this cell type. Calculated using techniques like effect size estimation and bootstrapping for reliability.

Cell ID: Standard Cell Ontology term used for mapping and comparing cells across experiments. Ensures consistency in analyzing cellular functions across tissues.
Fold Change: Represents the ratio of the current Cell Significance Index to the Cell Significance Index Threshold, indicating how much the gene expression has changed compared to a baseline.
Cell Significance Index: Reflects how strongly a gene is expressed in this cell type. Calculated using techniques like effect size estimation and bootstrapping for reliability.
Network Configuration

Explore relationships of the current gene. Select an Interaction Source: 'ONTOLOGY' for shared pathways (GO/Reactome) or 'STRING' for protein-protein interactions. Further refine by selecting context genes and comparing Cell Significance Index (CSI) scores between baseline and target cell types and their specific contexts.

Comma-separated if multiple.
Comma-separated if multiple.

Legend:
  • Query Gene
  • Node Color (Target Cell CSI, relative to current network):
    • Very High
    • High
    • Medium
    • Low
    • Very Low
    • CSI N/A
  • Node Size: Proportional to Target Cell CSI magnitude
  • STRING PPI Edge
  • Shared Pathway Edge (ONTOLOGY)

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Other Information

This section provides additional information about the gene, including a description generated by an AI language model and details about associated proteins.

## Summary Ubiquitin like modifier activating enzyme 1, [UBA1](/details-gene/7317), is a protein-coding gene located on the X chromosome that encodes the primary E1 activating enzyme essential for the ubiquitination pathway. This enzyme initiates the covalent attachment of ubiquitin to substrate proteins, a process critical for protein degradation, DNA damage response, signal transduction, and cell cycle control. Consistent with its fundamental role in protein homeostasis, [UBA1](/details-gene/7317) shows significant expression across a wide array of cell types, with particularly high activity noted in metabolically active cells such as [fallopian tube secretory epithelial cell](/details-cell/CL4030006). Mutations and dysregulation of [UBA1](/details-gene/7317) are associated with several X-linked genetic disorders, including spinal muscular atrophy ([314370](https://omim.org/entry/314370)) and VEXAS syndrome ([301054](https://omim.org/entry/301054)), highlighting its critical importance in human health. ## Cellular Roles and Expression Landscape The expression profile of [UBA1](/details-gene/7317) underscores its role as a ubiquitous and essential "housekeeping" enzyme rather than a specific cell lineage marker. Its significance is widespread across diverse functional categories, indicating a fundamental requirement for its activity in maintaining cellular function. **Overall**, the gene exhibits its highest significance in cells with high metabolic or secretory activity. For instance, it is a top marker in [fallopian tube secretory epithelial cell](/details-cell/CL4030006) (CSI: 30.05), suggesting a critical role in managing the high protein turnover associated with secretion. Significant expression is also observed in other epithelial lineages, including [kidney loop of Henle thin descending limb epithelial cell](/details-cell/CL1001111) and [intestinal epithelial cell](/details-cell/CL0002563), as well as progenitor cells like [megakaryocyte-erythroid progenitor cell](/details-cell/CL0000050) and [granulocyte monocyte progenitor cell](/details-cell/CL0000557). Furthermore, its activity is prominent in the immune system, exemplified by its high CSI in [CD4-positive, CD25-positive, alpha-beta regulatory T cell](/details-cell/CL0000792), which is consistent with the role of the ubiquitin-proteasome system in antigen presentation and immune regulation. The broad expression pattern, extending to neuronal ([caudal ganglionic eminence derived cortical interneuron](/details-cell/CL4023064)), structural ([lung pericyte](/details-cell/CL0009089)), and muscle ([cardiac muscle cell](/details-cell/CL0000746)) lineages, confirms that [UBA1](/details-gene/7317)-mediated ubiquitination is a cornerstone of cellular biology across the human body. Early research confirmed its localization to both the cytoplasm and nucleus, supporting its involvement in a wide range of cellular processes [Link](https://doi.org/10.1016/s0021-9258(20)30113-7). ## Pathways and Molecular Function The functional annotations for [UBA1](/details-gene/7317) confirm its central role as the initiator of the protein ubiquitination cascade. Its primary molecular function is **ubiquitin activating enzyme activity** ([GO:0004839](https://www.ebi.ac.uk/QuickGO/term/GO:0004839)), which requires **ATP binding** ([GO:0005524](https://www.ebi.ac.uk/QuickGO/term/GO:0005524)) to adenylate ubiquitin before transferring it to an E2 conjugating enzyme. This single enzymatic function drives a multitude of downstream biological processes. Key biological processes involving [UBA1](/details-gene/7317) include **protein ubiquitination** ([GO:0016567](https://www.ebi.ac.uk/QuickGO/term/GO:0016567)) and the subsequent **ubiquitin-dependent protein catabolic process** ([GO:0006511](https://www.ebi.ac.uk/QuickGO/term/GO:0006511)). These are fundamental for cellular protein quality control and are elaborated in Reactome pathways such as **Metabolism of proteins** ([R-HSA-392499](https://reactome.org/content/detail/R-HSA-392499)) and **Post-translational protein modification** ([R-HSA-597592](https://reactome.org/content/detail/R-HSA-597592)). Reflecting its importance in immunity, [UBA1](/details-gene/7317) is integral to the **Immune system** ([R-HSA-168256](https://reactome.org/content/detail/R-HSA-168256)), particularly in **Antigen processing: ubiquitination & proteasome degradation** ([R-HSA-983168](https://reactome.org/content/detail/R-HSA-983168)) and **Class I MHC mediated antigen processing & presentation** ([R-HSA-983169](https://reactome.org/content/detail/R-HSA-983169)). The gene is also annotated to the **Dna damage response** ([GO:0006974](https://www.ebi.ac.uk/QuickGO/term/GO:0006974)), consistent with early studies that identified its essential role in DNA replication [Link](https://doi.org/10.1002/j.1460-2075.1990.tb07483.x). The wide distribution of the UBA1 protein across cellular compartments, including the **cytoplasm** ([GO:0005737](https://www.ebi.ac.uk/QuickGO/term/GO:0005737)), **nucleus** ([GO:0005634](https://www.ebi.ac.uk/QuickGO/term/GO:0005634)), and **mitochondrion** ([GO:0005739](https://www.ebi.ac.uk/QuickGO/term/GO:0005739)), enables its participation in these diverse pathways. ## Research Directions Given that [UBA1](/details-gene/7317) is a central enzyme in a fundamental cellular process, research should focus on understanding how its activity is regulated in a cell-type-specific manner and how its dysregulation contributes to pathology. ### Proposed Hypotheses: 1. **Cell-type specific regulation in hematopoiesis:** The significant expression of [UBA1](/details-gene/7317) in hematopoietic progenitors ([megakaryocyte-erythroid progenitor cell](/details-cell/CL0000050) and [granulocyte monocyte progenitor cell](/details-cell/CL0000557)) suggests that its activity is tightly regulated during blood cell differentiation. We hypothesize that cell-type-specific E2/E3 ligase partners or post-translational modifications of UBA1 itself dictate lineage commitment, and that pathogenic mutations disrupt these interactions, leading to hematopoietic defects seen in conditions like VEXAS syndrome. 2. **Role in secretory stress response:** The exceptionally high CSI score in [fallopian tube secretory epithelial cell](/details-cell/CL4030006) suggests a specialized role beyond basal protein turnover. We hypothesize that [UBA1](/details-gene/7317) is a critical component of the unfolded protein response (UPR) in highly secretory cells, and that its activity is upregulated to clear misfolded proteins from the endoplasmic reticulum, thereby preventing secretory stress and maintaining tissue function. ### Key Experimental Approach: To test the hypothesis regarding the role of [UBA1](/details-gene/7317) in hematopoiesis (Hypothesis 1), one could use a conditional knockout mouse model or a CRISPR-Cas9-based inducible knockdown system in human hematopoietic stem and progenitor cells (HSPCs). Following induced loss of [UBA1](/details-gene/7317) function, HSPCs would be cultured under conditions that promote differentiation towards myeloid and erythroid lineages. The effects on cell survival, proliferation, and differentiation efficiency could be quantified using flow cytometry and colony-forming unit assays. To identify the specific ubiquitination pathways that are disrupted, quantitative ubiquitin proteomics (e.g., di-glycine remnant profiling) could be performed on sorted cell populations to reveal changes in the ubiquitination status of key regulatory proteins involved in hematopoiesis. ### Therapeutic Potential: As the primary E1 enzyme, [UBA1](/details-gene/7317) represents a challenging therapeutic target, as its systemic inhibition would likely lead to severe, widespread toxicity due to the shutdown of essential cellular processes. However, this perspective is changing with the discovery of somatic mutations in [UBA1](/details-gene/7317) that drive inflammatory diseases like VEXAS syndrome. Therapeutic strategies could focus on developing highly specific allosteric inhibitors or molecular glues that selectively target the mutant form of the enzyme or its aberrant protein-protein interactions. Such an approach would represent a targeted inhibition strategy, aiming to eliminate the pathogenic cell population while sparing healthy cells, thereby offering a promising avenue for treating [UBA1](/details-gene/7317)-driven diseases.

Genular Protein ID: 3230077572

Symbol: UBA1_HUMAN

Name: Ubiquitin-like modifier-activating enzyme 1

UniProtKB Accession Codes:

Database IDs:

Citations:

PubMed ID: 1606621

Title: Complementation by a cloned human ubiquitin-activating enzyme E1 of the S-phase-arrested mouse FM3A cell mutant with thermolabile E1.

PubMed ID: 1606621

DOI: 10.1247/csf.17.113

PubMed ID: 1986373

Title: Molecular cloning, sequence, and tissue distribution of the human ubiquitin-activating enzyme E1.

PubMed ID: 1986373

DOI: 10.1073/pnas.88.1.258

PubMed ID: 1871145

Title:

PubMed ID: 1871145

DOI: 10.1073/pnas.88.16.7456c

PubMed ID: 15772651

Title: The DNA sequence of the human X chromosome.

PubMed ID: 15772651

DOI: 10.1038/nature03440

PubMed ID: 15489334

Title: The status, quality, and expansion of the NIH full-length cDNA project: the Mammalian Gene Collection (MGC).

PubMed ID: 15489334

DOI: 10.1101/gr.2596504

PubMed ID: 2390975

Title: Molecular cloning, primary structure and expression of the human X linked A1S9 gene cDNA which complements the ts A1S9 mouse L cell defect in DNA replication.

PubMed ID: 2390975

DOI: 10.1002/j.1460-2075.1990.tb07483.x

PubMed ID: 1447181

Title: Isoforms of mammalian ubiquitin-activating enzyme.

PubMed ID: 1447181

DOI: 10.1016/s0021-9258(18)35767-3

PubMed ID: 1376922

Title: Immunoelectron microscopic localization of the ubiquitin-activating enzyme E1 in HepG2 cells.

PubMed ID: 1376922

DOI: 10.1073/pnas.89.12.5542

PubMed ID: 7528747

Title: Human ubiquitin-activating enzyme, E1. Indication of potential nuclear and cytoplasmic subpopulations using epitope-tagged cDNA constructs.

PubMed ID: 7528747

DOI: 10.1016/s0021-9258(20)30113-7

PubMed ID: 9099746

Title: Identification of a region within the ubiquitin-activating enzyme required for nuclear targeting and phosphorylation.

PubMed ID: 9099746

DOI: 10.1074/jbc.272.16.10895

PubMed ID: 16139798

Title: Proteomic identification of proteins conjugated to ISG15 in mouse and human cells.

PubMed ID: 16139798

DOI: 10.1016/j.bbrc.2005.08.132

PubMed ID: 15592455

Title: Immunoaffinity profiling of tyrosine phosphorylation in cancer cells.

PubMed ID: 15592455

DOI: 10.1038/nbt1046

PubMed ID: 16227972

Title: Gigaxonin-controlled degradation of MAP1B light chain is critical to neuronal survival.

PubMed ID: 16227972

DOI: 10.1038/nature04256

PubMed ID: 18669648

Title: A quantitative atlas of mitotic phosphorylation.

PubMed ID: 18669648

DOI: 10.1073/pnas.0805139105

PubMed ID: 19413330

Title: Lys-N and trypsin cover complementary parts of the phosphoproteome in a refined SCX-based approach.

PubMed ID: 19413330

DOI: 10.1021/ac9004309

PubMed ID: 19690332

Title: Quantitative phosphoproteomic analysis of T cell receptor signaling reveals system-wide modulation of protein-protein interactions.

PubMed ID: 19690332

DOI: 10.1126/scisignal.2000007

PubMed ID: 19608861

Title: Lysine acetylation targets protein complexes and co-regulates major cellular functions.

PubMed ID: 19608861

DOI: 10.1126/science.1175371

PubMed ID: 20068231

Title: Quantitative phosphoproteomics reveals widespread full phosphorylation site occupancy during mitosis.

PubMed ID: 20068231

DOI: 10.1126/scisignal.2000475

PubMed ID: 21269460

Title: Initial characterization of the human central proteome.

PubMed ID: 21269460

DOI: 10.1186/1752-0509-5-17

PubMed ID: 21406692

Title: System-wide temporal characterization of the proteome and phosphoproteome of human embryonic stem cell differentiation.

PubMed ID: 21406692

DOI: 10.1126/scisignal.2001570

PubMed ID: 22456334

Title: Ubiquitin-activating enzyme UBA1 is required for cellular response to DNA damage.

PubMed ID: 22456334

DOI: 10.4161/cc.19978

PubMed ID: 22814378

Title: N-terminal acetylome analyses and functional insights of the N-terminal acetyltransferase NatB.

PubMed ID: 22814378

DOI: 10.1073/pnas.1210303109

PubMed ID: 23186163

Title: Toward a comprehensive characterization of a human cancer cell phosphoproteome.

PubMed ID: 23186163

DOI: 10.1021/pr300630k

PubMed ID: 24275569

Title: An enzyme assisted RP-RPLC approach for in-depth analysis of human liver phosphoproteome.

PubMed ID: 24275569

DOI: 10.1016/j.jprot.2013.11.014

PubMed ID: 25944712

Title: N-terminome analysis of the human mitochondrial proteome.

PubMed ID: 25944712

DOI: 10.1002/pmic.201400617

PubMed ID: 33108101

Title: Somatic Mutations in UBA1 and Severe Adult-Onset Autoinflammatory Disease.

PubMed ID: 33108101

DOI: 10.1056/nejmoa2026834

PubMed ID: 25209502

Title: Expression, purification, and crystal structure of N-terminal domains of human ubiquitin-activating enzyme (E1).

PubMed ID: 25209502

DOI: 10.1080/09168451.2014.923301

PubMed ID: 18179898

Title: Rare missense and synonymous variants in UBE1 are associated with X-linked infantile spinal muscular atrophy.

PubMed ID: 18179898

DOI: 10.1016/j.ajhg.2007.09.009

PubMed ID: 23518311

Title: Clinical and neuropathological features of X-linked spinal muscular atrophy (SMAX2) associated with a novel mutation in the UBA1 gene.

PubMed ID: 23518311

DOI: 10.1016/j.nmd.2013.02.001

Sequence Information:

  • Length: 1058
  • Mass: 117849
  • Checksum: 4B413AAA75FAA562
  • Sequence:
  • MSSSPLSKKR RVSGPDPKPG SNCSPAQSVL SEVPSVPTNG MAKNGSEADI DEGLYSRQLY 
    VLGHEAMKRL QTSSVLVSGL RGLGVEIAKN IILGGVKAVT LHDQGTAQWA DLSSQFYLRE 
    EDIGKNRAEV SQPRLAELNS YVPVTAYTGP LVEDFLSGFQ VVVLTNTPLE DQLRVGEFCH 
    NRGIKLVVAD TRGLFGQLFC DFGEEMILTD SNGEQPLSAM VSMVTKDNPG VVTCLDEARH 
    GFESGDFVSF SEVQGMVELN GNQPMEIKVL GPYTFSICDT SNFSDYIRGG IVSQVKVPKK 
    ISFKSLVASL AEPDFVVTDF AKFSRPAQLH IGFQALHQFC AQHGRPPRPR NEEDAAELVA 
    LAQAVNARAL PAVQQNNLDE DLIRKLAYVA AGDLAPINAF IGGLAAQEVM KACSGKFMPI 
    MQWLYFDALE CLPEDKEVLT EDKCLQRQNR YDGQVAVFGS DLQEKLGKQK YFLVGAGAIG 
    CELLKNFAMI GLGCGEGGEI IVTDMDTIEK SNLNRQFLFR PWDVTKLKSD TAAAAVRQMN 
    PHIRVTSHQN RVGPDTERIY DDDFFQNLDG VANALDNVDA RMYMDRRCVY YRKPLLESGT 
    LGTKGNVQVV IPFLTESYSS SQDPPEKSIP ICTLKNFPNA IEHTLQWARD EFEGLFKQPA 
    ENVNQYLTDP KFVERTLRLA GTQPLEVLEA VQRSLVLQRP QTWADCVTWA CHHWHTQYSN 
    NIRQLLHNFP PDQLTSSGAP FWSGPKRCPH PLTFDVNNPL HLDYVMAAAN LFAQTYGLTG 
    SQDRAAVATF LQSVQVPEFT PKSGVKIHVS DQELQSANAS VDDSRLEELK ATLPSPDKLP 
    GFKMYPIDFE KDDDSNFHMD FIVAASNLRA ENYDIPSADR HKSKLIAGKI IPAIATTTAA 
    VVGLVCLELY KVVQGHRQLD SYKNGFLNLA LPFFGFSEPL AAPRHQYYNQ EWTLWDRFEV 
    QGLQPNGEEM TLKQFLDYFK TEHKLEITML SQGVSMLYSF FMPAAKLKER LDQPMTEIVS 
    RVSKRKLGRH VRALVLELCC NDESGEDVEV PYVRYTIR