Details for: ARSA

Gene ID: 410

Symbol: ARSA

Ensembl ID: ENSG00000100299

Description: arylsulfatase A

Associated with

Cells (max top 100)

(Cell Significance Index and respective Thresholds are uniquely calculated using our advanced thresholding algorithms to reveal cell-specific gene markers)

  • Cell Name: polychromatophilic erythroblast (CL0000550)
    Fold Change: 101.5782
    Cell Significance Index: -15.8000
  • Cell Name: hematopoietic oligopotent progenitor cell (CL0002032)
    Fold Change: 62.1739
    Cell Significance Index: -15.7700
  • Cell Name: mucosal type mast cell (CL0000485)
    Fold Change: 37.9316
    Cell Significance Index: -15.4100
  • Cell Name: smooth muscle fiber of ileum (CL1000278)
    Fold Change: 35.1180
    Cell Significance Index: -16.5800
  • Cell Name: peripheral blood mononuclear cell (CL2000001)
    Fold Change: 33.0978
    Cell Significance Index: -17.0300
  • Cell Name: ileal goblet cell (CL1000326)
    Fold Change: 24.7235
    Cell Significance Index: -16.5900
  • Cell Name: ciliated cell of the bronchus (CL0002332)
    Fold Change: 16.1614
    Cell Significance Index: -15.4300
  • Cell Name: orthochromatic erythroblast (CL0000552)
    Fold Change: 13.2527
    Cell Significance Index: -16.3400
  • Cell Name: CD8-alpha-beta-positive, alpha-beta intraepithelial T cell (CL0000796)
    Fold Change: 5.6591
    Cell Significance Index: -15.1600
  • Cell Name: stromal cell of bone marrow (CL0010001)
    Fold Change: 4.1915
    Cell Significance Index: -16.5400
  • Cell Name: epidermal Langerhans cell (CL0002457)
    Fold Change: 2.8192
    Cell Significance Index: -6.1700
  • Cell Name: epithelial cell of small intestine (CL0002254)
    Fold Change: 1.5757
    Cell Significance Index: 256.2800
  • Cell Name: epithelial cell of stomach (CL0002178)
    Fold Change: 1.3314
    Cell Significance Index: 155.1700
  • Cell Name: acinar cell of salivary gland (CL0002623)
    Fold Change: 1.2663
    Cell Significance Index: 59.0400
  • Cell Name: intestinal crypt stem cell of colon (CL0009043)
    Fold Change: 1.0314
    Cell Significance Index: 112.1800
  • Cell Name: gut absorptive cell (CL0000677)
    Fold Change: 0.9674
    Cell Significance Index: 58.0800
  • Cell Name: conjunctival epithelial cell (CL1000432)
    Fold Change: 0.9645
    Cell Significance Index: 13.1600
  • Cell Name: bladder urothelial cell (CL1001428)
    Fold Change: 0.9342
    Cell Significance Index: 48.5300
  • Cell Name: paneth cell of epithelium of small intestine (CL1000343)
    Fold Change: 0.8807
    Cell Significance Index: 19.0800
  • Cell Name: microfold cell of epithelium of small intestine (CL1000353)
    Fold Change: 0.5902
    Cell Significance Index: 40.8200
  • Cell Name: basal cell of prostate epithelium (CL0002341)
    Fold Change: 0.5832
    Cell Significance Index: 15.8800
  • Cell Name: enteroendocrine cell of colon (CL0009042)
    Fold Change: 0.5403
    Cell Significance Index: 102.8300
  • Cell Name: colon goblet cell (CL0009039)
    Fold Change: 0.5349
    Cell Significance Index: 52.9100
  • Cell Name: umbrella cell of urothelium (CL4030056)
    Fold Change: 0.5337
    Cell Significance Index: 4.9200
  • Cell Name: CD4-positive, alpha-beta memory T cell, CD45RO-positive (CL0001204)
    Fold Change: 0.5213
    Cell Significance Index: 15.3100
  • Cell Name: peg cell (CL4033014)
    Fold Change: 0.5008
    Cell Significance Index: 11.5700
  • Cell Name: progenitor cell of mammary luminal epithelium (CL0009116)
    Fold Change: 0.4679
    Cell Significance Index: 34.8700
  • Cell Name: enterocyte of epithelium of large intestine (CL0002071)
    Fold Change: 0.4185
    Cell Significance Index: 18.9700
  • Cell Name: odontoblast (CL0000060)
    Fold Change: 0.4027
    Cell Significance Index: 51.6300
  • Cell Name: basal epithelial cell of tracheobronchial tree (CL0002329)
    Fold Change: 0.3947
    Cell Significance Index: 11.0300
  • Cell Name: paneth cell of colon (CL0009009)
    Fold Change: 0.3761
    Cell Significance Index: 5.6400
  • Cell Name: basal cell of urothelium (CL1000486)
    Fold Change: 0.2717
    Cell Significance Index: 33.4100
  • Cell Name: intermediate cell of urothelium (CL4030055)
    Fold Change: 0.2633
    Cell Significance Index: 47.4600
  • Cell Name: L2/3-6 intratelencephalic projecting glutamatergic neuron (CL4023040)
    Fold Change: 0.2544
    Cell Significance Index: 51.0400
  • Cell Name: cell in vitro (CL0001034)
    Fold Change: 0.2248
    Cell Significance Index: 122.7900
  • Cell Name: cortical cell of adrenal gland (CL0002097)
    Fold Change: 0.1834
    Cell Significance Index: 4.9200
  • Cell Name: enterocyte of epithelium of small intestine (CL1000334)
    Fold Change: 0.1524
    Cell Significance Index: 4.3900
  • Cell Name: CD14-positive, CD16-negative classical monocyte (CL0002057)
    Fold Change: 0.1510
    Cell Significance Index: 2.7900
  • Cell Name: small intestine goblet cell (CL1000495)
    Fold Change: 0.1417
    Cell Significance Index: 4.9800
  • Cell Name: neutrophil progenitor cell (CL0000834)
    Fold Change: 0.0965
    Cell Significance Index: 2.5800
  • Cell Name: early pro-B cell (CL0002046)
    Fold Change: 0.0916
    Cell Significance Index: 5.9100
  • Cell Name: neoplastic cell (CL0001063)
    Fold Change: 0.0797
    Cell Significance Index: 15.8200
  • Cell Name: luminal adaptive secretory precursor cell of mammary gland (CL4033057)
    Fold Change: 0.0740
    Cell Significance Index: 3.4800
  • Cell Name: hair follicular keratinocyte (CL2000092)
    Fold Change: 0.0453
    Cell Significance Index: 20.0500
  • Cell Name: pancreatic acinar cell (CL0002064)
    Fold Change: 0.0414
    Cell Significance Index: 7.0700
  • Cell Name: obsolete caudal ganglionic eminence derived GABAergic cortical interneuron (CL4023070)
    Fold Change: 0.0382
    Cell Significance Index: 13.7100
  • Cell Name: tonsil germinal center B cell (CL2000006)
    Fold Change: 0.0196
    Cell Significance Index: 2.3100
  • Cell Name: lactocyte (CL0002325)
    Fold Change: 0.0195
    Cell Significance Index: 2.5200
  • Cell Name: stromal cell of ovary (CL0002132)
    Fold Change: 0.0160
    Cell Significance Index: 2.2000
  • Cell Name: pigmented epithelial cell (CL0000529)
    Fold Change: 0.0023
    Cell Significance Index: 4.2400
  • Cell Name: intestinal crypt stem cell of small intestine (CL0009017)
    Fold Change: 0.0019
    Cell Significance Index: 0.0400
  • Cell Name: pulmonary alveolar epithelial cell (CL0000322)
    Fold Change: -0.0026
    Cell Significance Index: -1.9800
  • Cell Name: anterior lens cell (CL0002223)
    Fold Change: -0.0058
    Cell Significance Index: -10.7300
  • Cell Name: lens epithelial cell (CL0002224)
    Fold Change: -0.0086
    Cell Significance Index: -13.1800
  • Cell Name: secondary lens fiber (CL0002225)
    Fold Change: -0.0122
    Cell Significance Index: -16.5600
  • Cell Name: abnormal cell (CL0001061)
    Fold Change: -0.0130
    Cell Significance Index: -1.3300
  • Cell Name: pancreatic A cell (CL0000171)
    Fold Change: -0.0141
    Cell Significance Index: -10.4300
  • Cell Name: non-pigmented ciliary epithelial cell (CL0002304)
    Fold Change: -0.0145
    Cell Significance Index: -9.1900
  • Cell Name: kidney loop of Henle cortical thick ascending limb epithelial cell (CL1001109)
    Fold Change: -0.0153
    Cell Significance Index: -11.2100
  • Cell Name: sebum secreting cell (CL0000317)
    Fold Change: -0.0226
    Cell Significance Index: -1.6000
  • Cell Name: type B pancreatic cell (CL0000169)
    Fold Change: -0.0249
    Cell Significance Index: -14.0200
  • Cell Name: ciliary muscle cell (CL1000443)
    Fold Change: -0.0281
    Cell Significance Index: -12.7400
  • Cell Name: pancreatic PP cell (CL0002275)
    Fold Change: -0.0307
    Cell Significance Index: -19.1400
  • Cell Name: dopaminergic neuron (CL0000700)
    Fold Change: -0.0434
    Cell Significance Index: -12.4900
  • Cell Name: cardiac muscle myoblast (CL0000513)
    Fold Change: -0.0461
    Cell Significance Index: -3.5400
  • Cell Name: lung endothelial cell (CL1001567)
    Fold Change: -0.0541
    Cell Significance Index: -2.8200
  • Cell Name: placental villous trophoblast (CL2000060)
    Fold Change: -0.0637
    Cell Significance Index: -1.7000
  • Cell Name: transit amplifying cell of colon (CL0009011)
    Fold Change: -0.0743
    Cell Significance Index: -2.3800
  • Cell Name: pancreatic ductal cell (CL0002079)
    Fold Change: -0.0743
    Cell Significance Index: -8.5100
  • Cell Name: pigmented ciliary epithelial cell (CL0002303)
    Fold Change: -0.0843
    Cell Significance Index: -12.2600
  • Cell Name: pancreatic D cell (CL0000173)
    Fold Change: -0.0845
    Cell Significance Index: -17.7900
  • Cell Name: intestinal epithelial cell (CL0002563)
    Fold Change: -0.1029
    Cell Significance Index: -1.0700
  • Cell Name: transit amplifying cell of small intestine (CL0009012)
    Fold Change: -0.1111
    Cell Significance Index: -2.3100
  • Cell Name: eye photoreceptor cell (CL0000287)
    Fold Change: -0.1114
    Cell Significance Index: -7.0200
  • Cell Name: smooth muscle cell of sphincter of pupil (CL0002243)
    Fold Change: -0.1504
    Cell Significance Index: -15.6600
  • Cell Name: glycinergic neuron (CL1001509)
    Fold Change: -0.1588
    Cell Significance Index: -8.3400
  • Cell Name: hippocampal granule cell (CL0001033)
    Fold Change: -0.1594
    Cell Significance Index: -10.7200
  • Cell Name: kidney loop of Henle descending limb epithelial cell (CL1001021)
    Fold Change: -0.2032
    Cell Significance Index: -16.0900
  • Cell Name: forebrain neuroblast (CL1000042)
    Fold Change: -0.2239
    Cell Significance Index: -13.7600
  • Cell Name: retinal progenitor cell (CL0002672)
    Fold Change: -0.2249
    Cell Significance Index: -12.6200
  • Cell Name: granulosa cell (CL0000501)
    Fold Change: -0.2324
    Cell Significance Index: -6.1100
  • Cell Name: intestinal tuft cell (CL0019032)
    Fold Change: -0.2371
    Cell Significance Index: -14.5400
  • Cell Name: keratocyte (CL0002363)
    Fold Change: -0.2433
    Cell Significance Index: -3.8600
  • Cell Name: hippocampal pyramidal neuron (CL1001571)
    Fold Change: -0.2821
    Cell Significance Index: -8.0500
  • Cell Name: indirect pathway medium spiny neuron (CL4023029)
    Fold Change: -0.2842
    Cell Significance Index: -12.5700
  • Cell Name: Purkinje cell (CL0000121)
    Fold Change: -0.2996
    Cell Significance Index: -6.5600
  • Cell Name: fibroblast of mammary gland (CL0002555)
    Fold Change: -0.3094
    Cell Significance Index: -8.8700
  • Cell Name: enteroendocrine cell of small intestine (CL0009006)
    Fold Change: -0.3112
    Cell Significance Index: -7.7800
  • Cell Name: foveolar cell of stomach (CL0002179)
    Fold Change: -0.3213
    Cell Significance Index: -2.1000
  • Cell Name: direct pathway medium spiny neuron (CL4023026)
    Fold Change: -0.3346
    Cell Significance Index: -12.6700
  • Cell Name: mesenchymal cell (CL0008019)
    Fold Change: -0.3358
    Cell Significance Index: -5.6200
  • Cell Name: L5 extratelencephalic projecting glutamatergic cortical neuron (CL4023041)
    Fold Change: -0.3440
    Cell Significance Index: -12.0500
  • Cell Name: kidney epithelial cell (CL0002518)
    Fold Change: -0.3544
    Cell Significance Index: -10.4400
  • Cell Name: fibroblast of dermis (CL0002551)
    Fold Change: -0.3593
    Cell Significance Index: -7.5200
  • Cell Name: leptomeningeal cell (CL0000708)
    Fold Change: -0.3694
    Cell Significance Index: -7.9000
  • Cell Name: corticothalamic-projecting glutamatergic cortical neuron (CL4023013)
    Fold Change: -0.3696
    Cell Significance Index: -11.7700
  • Cell Name: L6b glutamatergic cortical neuron (CL4023038)
    Fold Change: -0.3778
    Cell Significance Index: -12.3700
  • Cell Name: mesonephric nephron tubule epithelial cell (CL1000022)
    Fold Change: -0.3842
    Cell Significance Index: -13.3500
  • Cell Name: stratified epithelial cell (CL0000079)
    Fold Change: -0.3909
    Cell Significance Index: -14.3500
  • Cell Name: fibro/adipogenic progenitor cell (CL0009099)
    Fold Change: -0.3934
    Cell Significance Index: -19.8800

Cell ID: Standard Cell Ontology term used for mapping and comparing cells across experiments. Ensures consistency in analyzing cellular functions across tissues.
Fold Change: Represents the ratio of the current Cell Significance Index to the Cell Significance Index Threshold, indicating how much the gene expression has changed compared to a baseline.
Cell Significance Index: Reflects how strongly a gene is expressed in this specific cell.

Cell ID: Standard Cell Ontology term used for mapping and comparing cells across experiments. Ensures consistency in analyzing cellular functions across tissues.
Fold Change: Represents the ratio of the current Cell Significance Index to the Cell Significance Index Threshold, indicating how much the gene expression has changed compared to a baseline.
Cell Significance Index: Reflects how strongly a gene is expressed in this cell type. Calculated using techniques like effect size estimation and bootstrapping for reliability.

Cell ID: Standard Cell Ontology term used for mapping and comparing cells across experiments. Ensures consistency in analyzing cellular functions across tissues.
Fold Change: Represents the ratio of the current Cell Significance Index to the Cell Significance Index Threshold, indicating how much the gene expression has changed compared to a baseline.
Cell Significance Index: Reflects how strongly a gene is expressed in this cell type. Calculated using techniques like effect size estimation and bootstrapping for reliability.

Other Information

**Key Characteristics:** 1. **Enzyme Activity:** ARSA catalyzes the hydrolysis of alpha-N-acetylglucosamine residues from glycosphingolipids, leading to the breakdown of these complex lipids into simpler components. 2. **Subcellular Localization:** ARSA is primarily localized to the lysosomal lumen, where it plays a critical role in lipid metabolism and degradation. 3. **Cellular Expression:** ARSA is expressed in a variety of cell types, including salivary gland acinar cells, plasma cells, enterocytes, and neural cells, highlighting its broad functional significance. 4. **Protein Structure:** The ARSA protein consists of a single polypeptide chain with a molecular weight of approximately 80 kDa. **Pathways and Functions:** ARSA plays a pivotal role in various cellular processes, including: 1. **Glycosphingolipid Metabolism:** ARSA is essential for the degradation of glycosphingolipids, which are critical components of cellular membranes. 2. **Lysosomal Function:** ARSA's activity is closely linked to lysosomal function, as it helps maintain the integrity of lysosomal membranes and regulates the degradation of cellular waste. 3. **Immune System Regulation:** ARSA has been implicated in the regulation of immune responses, particularly in the context of neutrophil degranulation and the activation of arylsulfatases. 4. **Neurological Function:** ARSA's expression in neural cells and its role in lipid metabolism suggest a potential involvement in neurological processes, such as synapse formation and maintenance. **Clinical Significance:** Dysregulation of ARSA has been linked to various diseases, including: 1. **Metachromatic Lymphohistiocytosis (MLH):** A rare genetic disorder characterized by the accumulation of sulfated lipids in cells and tissues. 2. **I-cell Disease:** A lysosomal storage disorder caused by mutations in the ARSA gene, leading to the accumulation of glycosphingolipids in cells and tissues. 3. **Immune System Dysfunction:** ARSA's role in regulating immune responses suggests that its dysregulation may contribute to immune system dysfunction and autoimmune diseases. 4. **Neurological Disorders:** The potential involvement of ARSA in neurological processes highlights the importance of this enzyme in maintaining proper neuronal function and development. In conclusion, ARSA is a crucial enzyme involved in lipid metabolism, lysosomal function, and immune regulation. Its dysregulation has been linked to various diseases, emphasizing the importance of understanding the molecular mechanisms underlying ARSA's function and its role in human health and disease.

Genular Protein ID: 2484454210

Symbol: ARSA_HUMAN

Name: Arylsulfatase A

UniProtKB Accession Codes:

Database IDs:

Citations:

PubMed ID: 2562955

Title: Cloning and expression of human arylsulfatase A.

PubMed ID: 2562955

DOI: 10.1016/s0021-9258(19)85079-2

PubMed ID: 1975241

Title: Structure of the arylsulfatase A gene.

PubMed ID: 1975241

DOI: 10.1111/j.1432-1033.1990.tb19167.x

PubMed ID: 19262745

Title: Characterization of the arylsulfatase I (ARSI) gene preferentially expressed in the human retinal pigment epithelium cell line ARPE-19.

PubMed ID: 19262745

PubMed ID: 15461802

Title: A genome annotation-driven approach to cloning the human ORFeome.

PubMed ID: 15461802

DOI: 10.1186/gb-2004-5-10-r84

PubMed ID: 14702039

Title: Complete sequencing and characterization of 21,243 full-length human cDNAs.

PubMed ID: 14702039

DOI: 10.1038/ng1285

PubMed ID: 10591208

Title: The DNA sequence of human chromosome 22.

PubMed ID: 10591208

DOI: 10.1038/990031

PubMed ID: 15489334

Title: The status, quality, and expansion of the NIH full-length cDNA project: the Mammalian Gene Collection (MGC).

PubMed ID: 15489334

DOI: 10.1101/gr.2596504

PubMed ID: 1352993

Title: Proteolytic processing of human lysosomal arylsulfatase A.

PubMed ID: 1352993

DOI: 10.1016/0167-4838(92)90132-w

PubMed ID: 7628016

Title: A novel amino acid modification in sulfatases that is defective in multiple sulfatase deficiency.

PubMed ID: 7628016

DOI: 10.1016/0092-8674(95)90314-3

PubMed ID: 9342345

Title: Conversion of cysteine to formylglycine: a protein modification in the endoplasmic reticulum.

PubMed ID: 9342345

DOI: 10.1073/pnas.94.22.11963

PubMed ID: 15146462

Title: Molecular and functional analysis of SUMF1 mutations in multiple sulfatase deficiency.

PubMed ID: 15146462

DOI: 10.1002/humu.20040

PubMed ID: 19159218

Title: Glycoproteomics analysis of human liver tissue by combination of multiple enzyme digestion and hydrazide chemistry.

PubMed ID: 19159218

DOI: 10.1021/pr8008012

PubMed ID: 24294900

Title: A new analytical bench assay for the determination of arylsulfatase a activity toward galactosyl-3-sulfate ceramide: implication for metachromatic leukodystrophy diagnosis.

PubMed ID: 24294900

DOI: 10.1021/ac4023555

PubMed ID: 9521684

Title: Crystal structure of human arylsulfatase A: the aldehyde function and the metal ion at the active site suggest a novel mechanism for sulfate ester hydrolysis.

PubMed ID: 9521684

DOI: 10.1021/bi9714924

PubMed ID: 11124905

Title: Crystal structure of an enzyme-substrate complex provides insight into the interaction between human arylsulfatase A and its substrates during catalysis.

PubMed ID: 11124905

DOI: 10.1006/jmbi.2000.4297

PubMed ID: 12888274

Title: Crystal structure of a covalent intermediate of endogenous human arylsulfatase A.

PubMed ID: 12888274

DOI: 10.1016/s0162-0134(03)00176-4

PubMed ID: 16368756

Title: A general binding mechanism for all human sulfatases by the formylglycine-generating enzyme.

PubMed ID: 16368756

DOI: 10.1073/pnas.0507592102

PubMed ID: 7866401

Title: Molecular genetics of metachromatic leukodystrophy.

PubMed ID: 7866401

DOI: 10.1002/humu.1380040402

PubMed ID: 2574462

Title: Arylsulfatase A pseudodeficiency: loss of a polyadenylylation signal and N-glycosylation site.

PubMed ID: 2574462

DOI: 10.1073/pnas.86.23.9436

PubMed ID: 1673291

Title: Identification of a mutation in the arylsulfatase A gene of a patient with adult-type metachromatic leukodystrophy.

PubMed ID: 1673291

PubMed ID: 1678251

Title: Mutations in the arylsulfatase A pseudodeficiency allele causing metachromatic leukodystrophy.

PubMed ID: 1678251

PubMed ID: 1670590

Title: Molecular basis of different forms of metachromatic leukodystrophy.

PubMed ID: 1670590

DOI: 10.1056/nejm199101033240104

PubMed ID: 1353340

Title: Late-onset metachromatic leukodystrophy: molecular pathology in two siblings.

PubMed ID: 1353340

DOI: 10.1002/ana.410310305

PubMed ID: 8101038

Title: High residual arylsulfatase A (ARSA) activity in a patient with late-infantile metachromatic leukodystrophy.

PubMed ID: 8101038

PubMed ID: 8101083

Title: Mutations in the arylsulfatase A gene of Japanese patients with metachromatic leukodystrophy.

PubMed ID: 8101083

DOI: 10.1089/dna.1993.12.493

PubMed ID: 8095918

Title: Prevalence of common mutations in the arylsulphatase A gene in metachromatic leukodystrophy patients diagnosed in Britain.

PubMed ID: 8095918

DOI: 10.1007/bf00230227

PubMed ID: 7902317

Title: An adult-type metachromatic leukodystrophy caused by substitution of serine for glycine-122 in arylsulfatase A.

PubMed ID: 7902317

DOI: 10.1007/bf00216449

PubMed ID: 7906588

Title: Missense mutations in the arylsulphatase A genes of metachromatic leukodystrophy patients.

PubMed ID: 7906588

DOI: 10.1093/hmg/2.12.2117

PubMed ID: 8104633

Title: An arylsulfatase A (ARSA) missense mutation (T274M) causing late-infantile metachromatic leukodystrophy.

PubMed ID: 8104633

DOI: 10.1002/humu.1380020405

PubMed ID: 7909527

Title: Single exon mutation in arylsulfatase A gene has two effects: loss of enzyme activity and aberrant splicing.

PubMed ID: 7909527

DOI: 10.1007/bf00201666

PubMed ID: 7825603

Title: Multiple mutations are responsible for the high frequency of metachromatic leukodystrophy in a small geographic area.

PubMed ID: 7825603

PubMed ID: 7860068

Title: A missense mutation P136L in the arylsulfatase A gene causes instability and loss of activity of the mutant enzyme.

PubMed ID: 7860068

DOI: 10.1007/bf00209402

PubMed ID: 7581401

Title: Identification of seven novel mutations associated with metachromatic leukodystrophy.

PubMed ID: 7581401

DOI: 10.1002/humu.1380060210

PubMed ID: 8891236

Title: Two novel mutations in a Japanese patient with the late-infantile form of metachromatic leukodystrophy.

PubMed ID: 8891236

DOI: 10.1016/0387-7604(96)00041-1

PubMed ID: 8723680

Title: Characterization of two arylsulfatase A missense mutations D335V and T274M causing late infantile metachromatic leukodystrophy.

PubMed ID: 8723680

DOI: 10.1002/(sici)1098-1004(1996)7:4<311::aid-humu4>3.0.co;2-b

PubMed ID: 9272717

Title: A T > C transition causing a Leu > Pro substitution in a conserved region of the arylsulfatase A gene in a late infantile metachromatic leukodystrophy patient.

PubMed ID: 9272717

DOI: 10.1111/j.1399-0004.1997.tb02518.x

PubMed ID: 9090526

Title: Metachromatic leukodystrophy: identification of the first deletion in exon 1 and of nine novel point mutations in the arylsulfatase A gene.

PubMed ID: 9090526

DOI: 10.1002/(sici)1098-1004(1997)9:3<234::aid-humu4>3.0.co;2-7

PubMed ID: 9490297

Title: A 9-bp deletion (2320del9) on the background of the arylsulfatase A pseudodeficiency allele in a metachromatic leukodystrophy patient and in a patient with nonprogressive neurological symptoms.

PubMed ID: 9490297

DOI: 10.1007/s004390050652

PubMed ID: 9600244

Title: Molecular genetic characterization of two metachromatic leukodystrophy patients who carry the T799G mutation and show different phenotypes; description of a novel null-type mutation.

PubMed ID: 9600244

DOI: 10.1007/s004390050721

PubMed ID: 9744473

Title: The R496H mutation of arylsulfatase A does not cause metachromatic leukodystrophy.

PubMed ID: 9744473

DOI: 10.1002/(sici)1098-1004(1998)12:4<238::aid-humu3>3.0.co;2-b

PubMed ID: 9452102

Title: Two novel mutations in the arylsulfatase A gene associated with juvenile (R390Q) and adult onset (H397Y) metachromatic leukodystrophy.

PubMed ID: 9452102

DOI: 10.1002/humu.1380110181

PubMed ID: 9819708

Title: Prevalence of arylsulphatase A mutations in 11 Japanese patients with metachromatic leukodystrophy: identification of two novel mutations.

PubMed ID: 9819708

DOI: 10.1023/a:1005405418215

PubMed ID: 9888390

Title: Coincidence of two novel arylsulfatase A alleles and mutation 459+1G>A within a family with metachromatic leukodystrophy: molecular basis of phenotypic heterogeneity.

PubMed ID: 9888390

DOI: 10.1002/(sici)1098-1004(1999)13:1<61::aid-humu7>3.0.co;2-h

PubMed ID: 10220151

Title: Metachromatic leucodystrophy in Portugal-finding of four new molecular lesions: C300F, P425T, g.1190-1191insC, and g.2408delC.

PubMed ID: 10220151

DOI: 10.1002/(sici)1098-1004(1999)13:4<337::aid-humu14>3.0.co;2-9

PubMed ID: 10477432

Title: Identification of 12 novel mutations and two new polymorphisms in the arylsulfatase A gene: haplotype and genotype-phenotype correlation studies in Spanish metachromatic leukodystrophy patients.

PubMed ID: 10477432

DOI: 10.1002/(sici)1098-1004(1999)14:3<240::aid-humu7>3.0.co;2-l

PubMed ID: 10533072

Title: Metachromatic leucodystrophy: a newly identified mutation in arylsulphatase A, D281Y, found as a compound heterozygote with I179L in an adult onset case.

PubMed ID: 10533072

DOI: 10.1002/(sici)1098-1004(199911)14:5<447::aid-humu12>3.0.co;2-1

PubMed ID: 10381328

Title: Metachromatic leukodystrophy: subtype genotype/phenotype correlations and identification of novel missense mutations (P148L and P191T) causing the juvenile-onset disease.

PubMed ID: 10381328

DOI: 10.1006/mgme.1999.2865

PubMed ID: 10751093

Title: Characterization of four arylsulfatase A missense mutations G86D, Y201C, D255H, and E312D causing metachromatic leukodystrophy.

PubMed ID: 10751093

DOI: 10.1002/(sici)1096-8628(20000306)91:1<68::aid-ajmg13>3.0.co;2-g

PubMed ID: 11061266

Title: Adult-onset MLD: a gene mutation with isolated polyneuropathy.

PubMed ID: 11061266

DOI: 10.1212/wnl.55.7.1036

PubMed ID: 11020646

Title: Variable onset of metachromatic leukodystrophy in a Vietnamese family.

PubMed ID: 11020646

DOI: 10.1016/s0887-8994(00)00164-8

PubMed ID: 11456299

Title: Late-onset metachromatic leukodystrophy clinically presenting as isolated peripheral neuropathy: compound heterozygosity for the IVS2+1G-->A mutation and a newly identified missense mutation (Thr408Ile) in a Spanish family.

PubMed ID: 11456299

DOI: 10.1002/ana.1076

PubMed ID: 11941485

Title: Contribution of arylsulfatase A mutations located on the same allele to enzyme activity reduction and metachromatic leukodystrophy severity.

PubMed ID: 11941485

DOI: 10.1007/s00439-002-0701-y

PubMed ID: 12503099

Title: Biochemical characterization of two (C300F, P425T) arylsulfatase A missense mutations.

PubMed ID: 12503099

DOI: 10.1002/ajmg.a.10822

PubMed ID: 12788103

Title: Oligomerization capacity of two arylsulfatase A mutants: C300F and P425T.

PubMed ID: 12788103

DOI: 10.1016/s0006-291x(03)00969-0

PubMed ID: 14517960

Title: Identification of nine novel arylsulfatase A (ARSA) gene mutations in patients with metachromatic leukodystrophy (MLD).

PubMed ID: 14517960

DOI: 10.1002/humu.9190

PubMed ID: 14680985

Title: Novel mutations in arylsulfatase A gene in three Ukrainian families with metachromatic leukodystrophy.

PubMed ID: 14680985

DOI: 10.1016/j.ymgme.2003.08.004

PubMed ID: 15326627

Title: Novel mutations associated with metachromatic leukodystrophy: phenotype and expression studies in nine Czech and Slovak patients.

PubMed ID: 15326627

DOI: 10.1002/ajmg.a.30118

PubMed ID: 15026521

Title: Late onset MLD with normal nerve conduction associated with two novel missense mutations in the ASA gene.

PubMed ID: 15026521

DOI: 10.1136/jnnp.2003.017400

PubMed ID: 15710861

Title: Adult onset metachromatic leukodystrophy without electroclinical peripheral nervous system involvement: a new mutation in the ARSA gene.

PubMed ID: 15710861

DOI: 10.1001/archneur.62.2.309

PubMed ID: 18693274

Title: Molecular analysis of ARSA and PSAP genes in twenty-one Italian patients with metachromatic leukodystrophy: identification and functional characterization of 11 novel ARSA alleles.

PubMed ID: 18693274

DOI: 10.1002/humu.20851

PubMed ID: 19606494

Title: Characterization of new arylsulfatase A gene mutations reinforces genotype-phenotype correlation in metachromatic leukodystrophy.

PubMed ID: 19606494

DOI: 10.1002/humu.21093

PubMed ID: 20339381

Title: Molecular bases of metachromatic leukodystrophy in Polish patients.

PubMed ID: 20339381

DOI: 10.1038/jhg.2010.25

PubMed ID: 21265945

Title: Adult-type metachromatic leukodystrophy with compound heterozygous ARSA mutations: a case report and phenotypic comparison with a previously reported case.

PubMed ID: 21265945

DOI: 10.1111/j.1440-1819.2010.02169.x

Sequence Information:

  • Length: 507
  • Mass: 53588
  • Checksum: 3DDBE1378B4176A6
  • Sequence:
  • MGAPRSLLLA LAAGLAVARP PNIVLIFADD LGYGDLGCYG HPSSTTPNLD QLAAGGLRFT 
    DFYVPVSLCT PSRAALLTGR LPVRMGMYPG VLVPSSRGGL PLEEVTVAEV LAARGYLTGM 
    AGKWHLGVGP EGAFLPPHQG FHRFLGIPYS HDQGPCQNLT CFPPATPCDG GCDQGLVPIP 
    LLANLSVEAQ PPWLPGLEAR YMAFAHDLMA DAQRQDRPFF LYYASHHTHY PQFSGQSFAE 
    RSGRGPFGDS LMELDAAVGT LMTAIGDLGL LEETLVIFTA DNGPETMRMS RGGCSGLLRC 
    GKGTTYEGGV REPALAFWPG HIAPGVTHEL ASSLDLLPTL AALAGAPLPN VTLDGFDLSP 
    LLLGTGKSPR QSLFFYPSYP DEVRGVFAVR TGKYKAHFFT QGSAHSDTTA DPACHASSSL 
    TAHEPPLLYD LSKDPGENYN LLGGVAGATP EVLQALKQLQ LLKAQLDAAV TFGPSQVARG 
    EDPALQICCH PGCTPRPACC HCPDPHA

Genular Protein ID: 3430676058

Symbol: B4DVI5_HUMAN

Name: N/A

UniProtKB Accession Codes:

Database IDs:

Sequence Information:

  • Length: 196
  • Mass: 20260
  • Checksum: 5999180718B27638
  • Sequence:
  • MGAPRSLLLA LAAGLAVARP PNIVLIFADD LGYGDLGCYG HPSSTTPNLD QLAAGGLRFT 
    DFYVPVSLCT PSRAALLTGR LPVRMGMYPG VLVPSSRGGL PLEEVTVAEV LAARGYLTGM 
    AGKWHLGVGP EGAFLPPHQG FHRFLGIPYS HDQVGTTRAL SHPPTSQSPP ALDAPAAPPA 
    SPALTAAARL RAPART

Genular Protein ID: 1229088727

Symbol: A0A0C4DFZ2_HUMAN

Name: N/A

UniProtKB Accession Codes:

Database IDs:

Citations:

PubMed ID: 10591208

Title: The DNA sequence of human chromosome 22.

PubMed ID: 10591208

DOI: 10.1038/990031

PubMed ID: 11237011

Title: Initial sequencing and analysis of the human genome.

PubMed ID: 11237011

DOI: 10.1038/35057062

PubMed ID: 15496913

Title: Finishing the euchromatic sequence of the human genome.

PubMed ID: 15496913

DOI: 10.1038/nature03001

PubMed ID: 18477386

Title: Finishing the finished human chromosome 22 sequence.

PubMed ID: 18477386

DOI: 10.1186/gb-2008-9-5-r78

Sequence Information:

  • Length: 509
  • Mass: 53806
  • Checksum: 3DDBE12E7427DBA6
  • Sequence:
  • MSMGAPRSLL LALAAGLAVA RPPNIVLIFA DDLGYGDLGC YGHPSSTTPN LDQLAAGGLR 
    FTDFYVPVSL CTPSRAALLT GRLPVRMGMY PGVLVPSSRG GLPLEEVTVA EVLAARGYLT 
    GMAGKWHLGV GPEGAFLPPH QGFHRFLGIP YSHDQGPCQN LTCFPPATPC DGGCDQGLVP 
    IPLLANLSVE AQPPWLPGLE ARYMAFAHDL MADAQRQDRP FFLYYASHHT HYPQFSGQSF 
    AERSGRGPFG DSLMELDAAV GTLMTAIGDL GLLEETLVIF TADNGPETMR MSRGGCSGLL 
    RCGKGTTYEG GVREPALAFW PGHIAPGVTH ELASSLDLLP TLAALAGAPL PNVTLDGFDL 
    SPLLLGTGKS PRQSLFFYPS YPDEVRGVFA VRTGKYKAHF FTQGSAHSDT TADPACHASS 
    SLTAHEPPLL YDLSKDPGEN YNLLGGVAGA TPEVLQALKQ LQLLKAQLDA AVTFGPSQVA 
    RGEDPALQIC CHPGCTPRPA CCHCPDPHA

Database document:

This is a preview of the gene's schema. Only a few entries are kept for 'singleCellExpressions,' 'mRNAExpressions,' and other large data arrays for visualization purposes. You can zoom in with the mouse wheel for a closer view, and the text will adjust automatically if necessary. For the full schema, download it here.